Hypoplastic left heart syndrome with restrictive atrial septal defect and congenital pulmonary lymphangiectasis

Cardiovasc Pathol. 1999 Jan-Feb;8(1):49-51. doi: 10.1016/s1054-8807(98)00012-x.

Abstract

The presence of a restrictive atrial septal defect in hypoplastic left heart syndrome represents a surgical emergency and may negatively affect survival after operation. A neonate with such a disease association, requiring septectomy upon birth developed intractable respiratory failure due to congenital pulmonary lymphangiectasis. The therapeutic implications of this rare pathologic condition are discussed.

Publication types

  • Case Reports

MeSH terms

  • Fatal Outcome
  • Heart Septal Defects, Atrial / complications*
  • Heart Septal Defects, Atrial / pathology
  • Heart Septal Defects, Atrial / therapy
  • Humans
  • Hypoplastic Left Heart Syndrome / complications*
  • Hypoplastic Left Heart Syndrome / pathology
  • Hypoplastic Left Heart Syndrome / therapy
  • Infant, Newborn
  • Lung / abnormalities*
  • Lung Diseases / complications*
  • Lung Diseases / congenital
  • Lung Diseases / pathology
  • Lung Diseases / therapy
  • Lymphangiectasis / complications*
  • Lymphangiectasis / congenital
  • Lymphangiectasis / pathology
  • Lymphangiectasis / therapy
  • Male