Abstract
The presence of a restrictive atrial septal defect in hypoplastic left heart syndrome represents a surgical emergency and may negatively affect survival after operation. A neonate with such a disease association, requiring septectomy upon birth developed intractable respiratory failure due to congenital pulmonary lymphangiectasis. The therapeutic implications of this rare pathologic condition are discussed.
MeSH terms
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Fatal Outcome
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Heart Septal Defects, Atrial / complications*
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Heart Septal Defects, Atrial / pathology
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Heart Septal Defects, Atrial / therapy
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Humans
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Hypoplastic Left Heart Syndrome / complications*
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Hypoplastic Left Heart Syndrome / pathology
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Hypoplastic Left Heart Syndrome / therapy
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Infant, Newborn
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Lung / abnormalities*
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Lung Diseases / complications*
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Lung Diseases / congenital
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Lung Diseases / pathology
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Lung Diseases / therapy
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Lymphangiectasis / complications*
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Lymphangiectasis / congenital
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Lymphangiectasis / pathology
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Lymphangiectasis / therapy
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Male