A case of isolated uterine relapse of nasal T/NK cell lymphoma is reported. A 47-year old lady developed menstrual symptoms a year after attaining complete remission from her nasal T/NK cell lymphoma. Endometrial tissue showed characteristic zonal necrosis, angiocentricity and infiltration by lymphoma cells that were positive for both the characteristic immunopheotypic profile of T/NK cell (CD2+, surface CD3-, cytoplasmic CD3 [CD3epsilon]+ and CD56+) and EBER.