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Study Description

Ataxias are a group of diseases that result in a lack of coordinated muscle movement. Hereditary ataxias are genetically heterogeneous and it is reported that 40% of suspected genetic ataxias currently have an unknown cause. We used exome sequencing to detect mutations responsible for ataxia. We sequenced, when available, multiple individuals per family to identify family specific mutations and further confirmed segregation of variants using samples from available affected and unaffected family members.

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Publicly Available Data
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Study Inclusion/Exclusion Criteria
  • Probands had a suspected genetic form of ataxia and had tested negative on commercially available tests for common ataxia mutations.
  • Affected and, in most cases, unaffected relatives of proband were recruited.
Molecular Data
TypeSourcePlatformNumber of Oligos/SNPsSNP Batch IdComment
Whole Exome Sequencing Roche NimbleGen SeqCap EZ Human Exome Library v1.0 N/A N/A
Whole Exome Sequencing Roche NimbleGen SeqCap EZ Human Exome Library v2.0 N/A N/A
Whole Exome Sequencing Roche NimbleGen SeqCap EZHuman Exome Library v3.0 N/A N/A
Selected Publications
Diseases/Traits Related to Study (MeSH terms)
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Study Attribution
  • Principal Investigator
    • Margit Burmeister, PhD. University of Michigan, Ann Arbor, MI, USA.
  • Funding Source
    • R01-NS078560. National Institutes of Health, Bethesda, MD, USA.