PMC

Focal facial dermal dysplasia in the proposita. (A and B). White, shiny, atrophic papules measuring 3–10 mm were present on the right cheek (A) and left cheek (B). (C). Intraoral polyps in the proposita that were seen as small, polypoid lesions measuring 2–3 mm protruding 5–8 mm from the left buccal mucosa. (D). Teeth of the proposita, showing minor dental ridges. (E and F). Focal facial dermal dysplasia in the brother of the proposita. White, shiny, atrophic papules similar to those in the proposita are present on the right cheek (E) and the left cheek (F). (G and H). Facial features of the fifth patient with FFDD Type IV. Atrophic skin lesion on the right (G and left H) cheeks.