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Select item 31425411.

Enzymatic defects underlying hereditary glutamate cysteine ligase deficiency are mitigated by association of the catalytic and regulatory subunits

Melanie Neely Willis, Yilin Liu, Ekaterina I. Biterova, Melanie A. Simpson, Heejeong Kim, Jaekwon Lee, Joseph J. Barycki

Biochemistry. Author manuscript; available in PMC 2012 Jul 26.

Published in final edited form as: Biochemistry. 2011 Jul 26; 50(29): 6508–6517. Published online 2011 Jun 29. doi: 10.1021/bi200708w

PMCID:: PMC3142541

Abstract Article PDF–2.5M

Select item 18520942.

Inborn errors in the metabolism of glutathione

Ellinor Ristoff, Agne Larsson

Orphanet J Rare Dis. 2007; 2: 16. Published online 2007 Mar 30. doi: 10.1186/1750-1172-2-16

PMCID:: PMC1852094

Abstract Article PDF–545K

Select item 11714013.

Molecular basis of glutathione synthetase deficiency and a rare gene permutation event.

G Polekhina, P G Board, R R Gali, J Rossjohn, M W Parker

EMBO J. 1999 Jun 15; 18(12): 3204–3213. doi: 10.1093/emboj/18.12.3204

PMCID:: PMC1171401

Summary PDF–442K

Select item 91366804.

Oxidative stress induces inflammation of lens cells and triggers immune surveillance of ocular tissues

Brian Thompson, Emily A. Davidson, Ying Chen, David J. Orlicky, David C. Thompson, Vasilis Vasiliou

Chem Biol Interact. Author manuscript; available in PMC 2023 Mar 1.

Published in final edited form as: Chem Biol Interact. 2022 Mar 1; 355: 109804. Published online 2022 Feb 4. doi: 10.1016/j.cbi.2022.109804

PMCID:: PMC9136680

Abstract Article PDF–2.5M

Select item 66345455.

Redox Dysregulation Affects the Ventral But Not Dorsal Hippocampus: Impairment of Parvalbumin Neurons, Gamma Oscillations, and Related Behaviors

Pascal Steullet, Jan-Harry Cabungcal, Anita Kulak, Rudolf Kraftsik, Ying Chen, Timothy P. Dalton, Michel Cuenod, Kim Q. Do

J Neurosci. 2010 Feb 17; 30(7): 2547–2558. doi: 10.1523/JNEUROSCI.3857-09.2010

PMCID:: PMC6634545

Abstract Article PDF–3.4M

Select item 60750786.

Gclc deficiency in mouse CNS causes mitochondrial damage and neurodegeneration

Weiyi Feng, Mariana Rosca, Yuxuan Fan, Yufen Hu, Pingfu Feng, Hyoung-Gon Lee, Vincent M. Monnier, Xingjun Fan

Hum Mol Genet. 2017 Apr 1; 26(7): 1376–1390. Published online 2017 Jan 31. doi: 10.1093/hmg/ddx040

PMCID:: PMC6075078

Abstract Article PDF–2.0M

Select item 60134107.

Glutathione deficiency sensitizes cultured embryonic mouse ovaries to benzo[a]pyrene-induced germ cell apoptosis

Jinhwan Lim, Ulrike Luderer

Toxicol Appl Pharmacol. Author manuscript; available in PMC 2019 Aug 1.

Published in final edited form as: Toxicol Appl Pharmacol. 2018 Aug 1; 352: 38–45. Published online 2018 May 22. doi: 10.1016/j.taap.2018.05.024

PMCID:: PMC6013410

Abstract Article PDF–1.5M

Select item 50724278.

Metabolic reprogramming during neuronal differentiation

M Agostini, F Romeo, S Inoue, M V Niklison-Chirou, A J Elia, D Dinsdale, N Morone, R A Knight, T W Mak, G Melino

Cell Death Differ. 2016 Sep 1; 23(9): 1502–1514. Published online 2016 Apr 8. doi: 10.1038/cdd.2016.36

PMCID:: PMC5072427

Abstract Article PDF–1.5M

Select item 47265039.

A Glutathione-Nrf2-Thioredoxin Cross-Talk Ensures Keratinocyte Survival and Efficient Wound Repair

Michèle Telorack, Michael Meyer, Irina Ingold, Marcus Conrad, Wilhelm Bloch, Sabine Werner

PLoS Genet. 2016 Jan; 12(1): e1005800. Published online 2016 Jan 25. doi: 10.1371/journal.pgen.1005800

PMCID:: PMC4726503

Abstract Article PDF–11M

Select item 444270910.

The brominated flame retardant BDE-47 causes oxidative stress and apoptotic cell death in vitro and in vivo in mice

Lucio G. Costa, Claudia Pellacani, Khoi Dao, Terrance J. Kavanagh, Pamela J. Roque

Neurotoxicology. Author manuscript; available in PMC 2016 May 1.

Published in final edited form as: Neurotoxicology. 2015 May; 48: 68–76. Published online 2015 Mar 19. doi: 10.1016/j.neuro.2015.03.008

PMCID:: PMC4442709

Abstract Article PDF–682K

Select item 385622411.

In Utero Exposure to Benzo[a]pyrene Increases Adiposity and Causes Hepatic Steatosis in Female Mice, and Glutathione Deficiency Is Protective

Laura Ortiz, Brooke Nakamura, Xia Li., Bruce Blumberg, Ulrike Luderer

Toxicol Lett. Author manuscript; available in PMC 2014 Nov 25.

Published in final edited form as: Toxicol Lett. 2013 Nov 25; 223(2): 10.1016/j.toxlet.2013.09.017. Published online 2013 Oct 6. doi: 10.1016/j.toxlet.2013.09.017

PMCID:: PMC3856224

Abstract Article PDF–819K

Select item 203426512.

Impaired glutathione synthesis in schizophrenia: Convergent genetic and functional evidence

René Gysin, Rudolf Kraftsik, Julie Sandell, Pierre Bovet, Céline Chappuis, Philippe Conus, Patricia Deppen, Martin Preisig, Viviane Ruiz, Pascal Steullet, Mirjana Tosic, Thomas Werge, Michel Cuénod, Kim Q. Do

Proc Natl Acad Sci U S A. 2007 Oct 16; 104(42): 16621–16626. Published online 2007 Oct 5. doi: 10.1073/pnas.0706778104

PMCID:: PMC2034265

Abstract Article PDF–516K

Select item 2578813.

Glutathione synthesis is essential for mouse development but not for cell growth in culture

Zheng-Zheng Shi, Joseph Osei-Frimpong, Geeta Kala, Subbarao V. Kala, Roberto J. Barrios, Geetha M. Habib, Dana J. Lukin, Christopher M. Danney, Martin M. Matzuk, Michael W. Lieberman

Proc Natl Acad Sci U S A. 2000 May 9; 97(10): 5101–5106. doi: 10.1073/pnas.97.10.5101

PMCID:: PMC25788

Abstract Article PDF–365K

Select item 674373014.

Hepatic metabolic adaptation in a murine model of glutathione deficiency

Ying Chen, Srujana Golla, Rolando Garcia-Milian, David C. Thompson, Frank J. Gonzalez, Vasilis Vasiliou

Chem Biol Interact. Author manuscript; available in PMC 2019 Sep 13.

Published in final edited form as: Chem Biol Interact. 2019 Apr 25; 303: 1–6. Published online 2019 Feb 20. doi: 10.1016/j.cbi.2019.02.015

PMCID:: PMC6743730

Abstract Article PDF–773K

Select item 584951415.

Decreased glutathione levels cause overt motor neuron degeneration in hSOD1^WT overexpressing mice

Kelby M. Killoy, Benjamin A. Harlan, Mariana Pehar, Kristi L. Helke, Jeffrey A. Johnson, Marcelo R. Vargas

Exp Neurol. Author manuscript; available in PMC 2019 Apr 1.

Published in final edited form as: Exp Neurol. 2018 Apr; 302: 129–135. Published online 2018 Jan 4. doi: 10.1016/j.expneurol.2018.01.004

PMCID:: PMC5849514

Abstract Article PDF–598K

Select item 559626516.

Role of glutathione biosynthesis in endothelial dysfunction and fibrosis

Cristina Espinosa-Díez, Verónica Miguel, Susana Vallejo, Francisco J. Sánchez, Elena Sandoval, Eva Blanco, Pablo Cannata, Concepción Peiró, Carlos F. Sánchez-Ferrer, Santiago Lamas

Redox Biol. 2018 Apr; 14: 88–99. Published online 2017 Sep 1. doi: 10.1016/j.redox.2017.08.019

PMCID:: PMC5596265

Abstract Article PDF–1.8M

Select item 481547517.

Glutathione Deficit Affects the Integrity and Function of the Fimbria/Fornix and Anterior Commissure in Mice: Relevance for Schizophrenia

Alberto Corcoba, Pascal Steullet, João M. N. Duarte, Yohan Van de Looij, Aline Monin, Michel Cuenod, Rolf Gruetter, Kim Q. Do

Int J Neuropsychopharmacol. 2016 Mar; 19(3): pyv110. Published online 2015 Oct 3. doi: 10.1093/ijnp/pyv110

PMCID:: PMC4815475

Abstract Article PDF–5.6M

Select item 380118818.

GLUTATHIONE DEFENSE MECHANISM IN LIVER INJURY: INSIGHTS FROM ANIMAL MODELS

Y Chen, H Dong, DC Thompson, HG Shertzer, DW Nebert, V Vasiliou

Food Chem Toxicol. Author manuscript; available in PMC 2014 Oct 1.

Published in final edited form as: Food Chem Toxicol. 2013 Oct; 60: 38–44. Published online 2013 Jul 12. doi: 10.1016/j.fct.2013.07.008

PMCID:: PMC3801188

Abstract Article PDF–626K

Select item 351133419.

The LEGSKO Mouse: A Mouse Model of Age-Related Nuclear Cataract Based on Genetic Suppression of Lens Glutathione Synthesis

Xingjun Fan, Xiaoqin Liu, Shuyu Hao, Benlian Wang, Michael L. Robinson, Vincent M. Monnier

PLoS One. 2012; 7(11): e50832. Published online 2012 Nov 30. doi: 10.1371/journal.pone.0050832

PMCID:: PMC3511334

Abstract Article PDF–2.2M

Select item 344848820.

Beneficial Effects of Nrf2 Overexpression in a Mouse Model of Alexander Disease

Christine M. LaPash Daniels, Elizabeth V. Austin, Danica E. Rockney, Elizabeth M. Jacka, Tracy L. Hagemann, Delinda A. Johnson, Jeffrey A. Johnson, Albee Messing

J Neurosci. 2012 Aug 1; 32(31): 10507–10515. doi: 10.1523/JNEUROSCI.1494-12.2012