Polycystic Kidney Disease Diet: What is Known and What is Safe.
Clin J Am Soc Nephrol.
2024 May 1;19(5):664-682. doi: 10.2215/CJN.0000000000000326. Epub 2023 Sep 20. Review. PubMed PMID:
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Deep learning-based automated kidney and cyst segmentation of autosomal dominant polycystic kidney disease using single vs. multi-institutional data.
Clin Imaging.
2024 Feb;106:110068. doi: 10.1016/j.clinimag.2023.110068. Epub 2023 Dec 12. PubMed PMID:
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Utility of new image-derived biomarkers for autosomal dominant polycystic kidney disease prognosis using automated instance cyst segmentation.
Kidney Int.
2023 Aug;104(2):334-342. doi: 10.1016/j.kint.2023.01.010. Epub 2023 Feb 1. PubMed PMID:
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Prioritized polycystic kidney disease drug targets and repurposing candidates from pre-cystic and cystic mouse Pkd2 model gene expression reversion.
Mol Med.
2023 May 22;29(1):67. doi: 10.1186/s10020-023-00664-z. PubMed PMID:
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Cx3cr1 controls kidney resident macrophage heterogeneity.
Front Immunol.
2023;14:1082078. doi: 10.3389/fimmu.2023.1082078. eCollection 2023. PubMed PMID:
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Venglustat, a Novel Glucosylceramide Synthase Inhibitor, in Patients at Risk of Rapidly Progressing ADPKD: Primary Results of a Double-Blind, Placebo-Controlled, Phase 2/3 Randomized Clinical Trial.
Am J Kidney Dis.
2023 May;81(5):517-527.e1. doi: 10.1053/j.ajkd.2022.10.016. Epub 2022 Dec 17. PubMed PMID:
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Risk Severity Model for Pediatric Autosomal Dominant Polycystic Kidney Disease Using 3D Ultrasound Volumetry.
Clin J Am Soc Nephrol.
2023 May 1;18(5):581-591. doi: 10.2215/CJN.0000000000000122. Epub 2023 Feb 17. PubMed PMID:
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Accuracy and processing time of kidney volume measurement methods in rodents polycystic kidney disease models: superiority of semiautomated kidney segmentation.
Am J Physiol Renal Physiol.
2023 Apr 1;324(4):F423-F430. doi: 10.1152/ajprenal.00295.2022. Epub 2023 Feb 16. PubMed PMID:
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A kidney resident macrophage subset is a candidate biomarker for renal cystic disease in preclinical models.
Dis Model Mech.
2023 Jan 1;16(1). doi: 10.1242/dmm.049810. Epub 2023 Jan 16. PubMed PMID:
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Red blood cell exosome hemoglobin content increases after cardiopulmonary bypass and mediates acute kidney injury in an animal model.
J Thorac Cardiovasc Surg.
2022 Dec;164(6):e289-e308. doi: 10.1016/j.jtcvs.2020.11.102. Epub 2020 Dec 3. PubMed PMID:
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The STAGED-PKD 2-Stage Adaptive Study With a Patient Enrichment Strategy and Treatment Effect Modeling for Improved Study Design Efficiency in Patients With ADPKD.
Kidney Med.
2022 Oct;4(10):100538. doi: 10.1016/j.xkme.2022.100538. eCollection 2022 Oct. PubMed PMID:
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Design and Basic Characteristics of a National Patient-Powered Registry in ADPKD.
Kidney360.
2022 Aug 25;3(8):1350-1358. doi: 10.34067/KID.0002372022. eCollection 2022 Aug 25. PubMed PMID:
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A Comprehensive Immune Cell Atlas of Cystic Kidney Disease Reveals the Involvement of Adaptive Immune Cells in Injury-Mediated Cyst Progression in Mice.
J Am Soc Nephrol.
2022 Apr;33(4):747-768. doi: 10.1681/ASN.2021030278. Epub 2022 Feb 2. PubMed PMID:
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Volume Progression and Imaging Classification of Polycystic Liver in Early Autosomal Dominant Polycystic Kidney Disease.
Clin J Am Soc Nephrol.
2022 Mar;17(3):374-384. doi: 10.2215/CJN.08660621. Epub 2022 Feb 25. PubMed PMID:
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Monoallelic IFT140 pathogenic variants are an important cause of the autosomal dominant polycystic kidney-spectrum phenotype.
Am J Hum Genet.
2022 Jan 6;109(1):136-156. doi: 10.1016/j.ajhg.2021.11.016. Epub 2021 Dec 9. PubMed PMID:
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New Creatinine- and Cystatin C-Based Equations to Estimate GFR without Race.
N Engl J Med.
2021 Nov 4;385(19):1737-1749. doi: 10.1056/NEJMoa2102953. Epub 2021 Sep 23. PubMed PMID:
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Genetic Testing for Chronic Kidney Diseases: Clinical Utility and Barriers Perceived by Nephrologists.
Kidney Med.
2021 Nov-Dec;3(6):1050-1056. doi: 10.1016/j.xkme.2021.08.006. eCollection 2021 Nov-Dec. PubMed PMID:
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Early infiltrating macrophage subtype correlates with late-stage phenotypic outcome in a mouse model of hepatorenal fibrocystic disease.
Lab Invest.
2021 Oct;101(10):1382-1393. doi: 10.1038/s41374-021-00627-0. Epub 2021 Jun 22. PubMed PMID:
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Ly6c(hi) Infiltrating Macrophages Promote Cyst Progression in Injured Conditional Ift88 Mice.
Kidney360.
2021 Jun 24;2(6):989-995. doi: 10.34067/KID.0000882021. PubMed PMID:
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Autosomal Dominant Polycystic Kidney Disease Does Not Significantly Alter Major COVID-19 Outcomes among Veterans.
Kidney360.
2021 Jun 24;2(6):983-988. doi: 10.34067/KID.0007282020. eCollection 2021 Jun 24. PubMed PMID:
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Prognostic Value of Fibroblast Growth Factor 23 in Autosomal Dominant Polycystic Kidney Disease.
Kidney Int Rep.
2021 Apr;6(4):953-961. doi: 10.1016/j.ekir.2021.01.004. eCollection 2021 Apr. PubMed PMID:
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Establishing a Core Outcome Set for Autosomal Dominant Polycystic Kidney Disease: Report of the Standardized Outcomes in Nephrology-Polycystic Kidney Disease (SONG-PKD) Consensus Workshop.
Am J Kidney Dis.
2021 Feb;77(2):255-263. doi: 10.1053/j.ajkd.2020.05.024. Epub 2020 Aug 6. PubMed PMID:
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Autosomal Dominant Polycystic Kidney Disease does not significantly alter major COVID-19 outcomes among veterans.
medRxiv.
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Role of chemokines, innate and adaptive immunity.
Cell Signal.
2020 Sep;73:109647. doi: 10.1016/j.cellsig.2020.109647. Epub 2020 Apr 20. Review. PubMed PMID:
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The value of genotypic and imaging information to predict functional and structural outcomes in ADPKD.
JCI Insight.
2020 Aug 6;5(15). doi: 10.1172/jci.insight.138724. PubMed PMID:
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Interferon Regulatory Factor-5 in Resident Macrophage Promotes Polycystic Kidney Disease.
Kidney360.
2020 Mar;1(3):179-190. doi: 10.34067/KID.0001052019. Epub 2020 Mar 26. PubMed PMID:
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Ketosis Ameliorates Renal Cyst Growth in Polycystic Kidney Disease.
Cell Metab.
2019 Dec 3;30(6):1007-1023.e5. doi: 10.1016/j.cmet.2019.09.012. Epub 2019 Oct 17. PubMed PMID:
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Tissue-Resident Macrophages Promote Renal Cystic Disease.
J Am Soc Nephrol.
2019 Oct;30(10):1841-1856. doi: 10.1681/ASN.2018080810. Epub 2019 Jul 23. PubMed PMID:
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Sodium and potassium excretion predict increased depression in urban adolescents.
Physiol Rep.
2019 Aug;7(16):e14213. doi: 10.14814/phy2.14213. PubMed PMID:
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Crystal deposition triggers tubule dilation that accelerates cystogenesis in polycystic kidney disease.
J Clin Invest.
2019 Jul 30;129(10):4506-4522. doi: 10.1172/JCI128503. PubMed PMID:
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Growth Pattern of Kidney Cyst Number and Volume in Autosomal Dominant Polycystic Kidney Disease.
Clin J Am Soc Nephrol.
2019 Jun 7;14(6):823-833. doi: 10.2215/CJN.10360818. Epub 2019 May 14. PubMed PMID:
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Long-term trajectory of kidney function in autosomal-dominant polycystic kidney disease.
Kidney Int.
2019 May;95(5):1253-1261. doi: 10.1016/j.kint.2018.12.023. Epub 2019 Mar 4. PubMed PMID:
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Single-Cell RNA Sequencing Identifies Candidate Renal Resident Macrophage Gene Expression Signatures across Species.
J Am Soc Nephrol.
2019 May;30(5):767-781. doi: 10.1681/ASN.2018090931. Epub 2019 Apr 4. PubMed PMID:
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Truncating PKHD1 and PKD2 mutations alter energy metabolism.
Am J Physiol Renal Physiol.
2019 Mar 1;316(3):F414-F425. doi: 10.1152/ajprenal.00167.2018. Epub 2018 Dec 19. PubMed PMID:
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Heterozygous Pkhd1(C642*) mice develop cystic liver disease and proximal tubule ectasia that mimics radiographic signs of medullary sponge kidney.
Am J Physiol Renal Physiol.
2019 Mar 1;316(3):F463-F472. doi: 10.1152/ajprenal.00181.2018. Epub 2019 Jan 2. PubMed PMID:
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Resident macrophages reprogram toward a developmental state after acute kidney injury.
JCI Insight.
2019 Jan 24;4(2). doi: 10.1172/jci.insight.125503. PubMed PMID:
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Urinary T cells correlate with rate of renal function loss in autosomal dominant polycystic kidney disease.
Physiol Rep.
2019 Jan;7(1):e13951. doi: 10.14814/phy2.13951. PubMed PMID:
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Mks6 mutations reveal tissue- and cell type-specific roles for the cilia transition zone.
FASEB J.
2019 Jan;33(1):1440-1455. doi: 10.1096/fj.201801149R. Epub 2018 Aug 22. PubMed PMID:
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Relationship between caffeine intake and autosomal dominant polycystic kidney disease progression: a retrospective analysis using the CRISP cohort.
BMC Nephrol.
2018 Dec 27;19(1):378. doi: 10.1186/s12882-018-1182-0. PubMed PMID:
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A Practical Guide for Treatment of Rapidly Progressive ADPKD with Tolvaptan.
J Am Soc Nephrol.
2018 Oct;29(10):2458-2470. doi: 10.1681/ASN.2018060590. Epub 2018 Sep 18. Review. PubMed PMID:
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Casein kinase 1ε and 1α as novel players in polycystic kidney disease and mechanistic targets for (R)-roscovitine and (S)-CR8.
Am J Physiol Renal Physiol.
2018 Jul 1;315(1):F57-F73. doi: 10.1152/ajprenal.00489.2017. Epub 2018 Mar 14. PubMed PMID:
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Baseline total kidney volume and the rate of kidney growth are associated with chronic kidney disease progression in Autosomal Dominant Polycystic Kidney Disease.
Kidney Int.
2018 Mar;93(3):691-699. doi: 10.1016/j.kint.2017.09.027. Epub 2017 Dec 28. PubMed PMID:
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Tolvaptan in Later-Stage Autosomal Dominant Polycystic Kidney Disease.
N Engl J Med.
2017 Nov 16;377(20):1930-1942. doi: 10.1056/NEJMoa1710030. Epub 2017 Nov 4. PubMed PMID:
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Image texture features predict renal function decline in patients with autosomal dominant polycystic kidney disease.
Kidney Int.
2017 Nov;92(5):1206-1216. doi: 10.1016/j.kint.2017.03.026. Epub 2017 May 20. PubMed PMID:
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Recovery of methotrexate-induced anuric acute kidney injury after glucarpidase therapy.
SAGE Open Med Case Rep.
2017;5:2050313X17705050. doi: 10.1177/2050313X17705050. eCollection 2017. PubMed PMID:
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Uric Acid Excretion Predicts Increased Blood Pressure Among American Adolescents of African Descent.
Am J Med Sci.
2017 Apr;353(4):336-341. doi: 10.1016/j.amjms.2017.01.008. Epub 2017 Jan 20. PubMed PMID:
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Performance of the CKD-EPI Equation to Estimate GFR in a Longitudinal Study of Autosomal Dominant Polycystic Kidney Disease.
Am J Kidney Dis.
2017 Mar;69(3):482-484. doi: 10.1053/j.ajkd.2016.10.021. Epub 2016 Dec 24. PubMed PMID:
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Automated segmentation of liver and liver cysts from bounded abdominal MR images in patients with autosomal dominant polycystic kidney disease.
Phys Med Biol.
2016 Nov 21;61(22):7864-7880. doi: 10.1088/0031-9155/61/22/7864. Epub 2016 Oct 25. PubMed PMID:
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International Multi-Specialty Delphi Survey: Identification of Diagnostic Criteria for Hepatic and Renal Cyst Infection.
Nephron.
2016;134(4):205-214. doi: 10.1159/000446664. Epub 2016 Sep 3. PubMed PMID:
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Predicted Mutation Strength of Nontruncating PKD1 Mutations Aids Genotype-Phenotype Correlations in Autosomal Dominant Polycystic Kidney Disease.
J Am Soc Nephrol.
2016 Sep;27(9):2872-84. doi: 10.1681/ASN.2015050583. Epub 2016 Jan 28. PubMed PMID:
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