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Cryptogenic Organizing Pneumonia

An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts.

Year introduced: 2009 (1995)

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Tree Number(s): C08.127.446.135.140.600.750, C08.381.483.652.500.750.249, C08.381.495.146.135.140.600.750

MeSH Unique ID: D018549

Entry Terms:

  • Cryptogenic Organizing Pneumonias
  • Organizing Pneumonia, Cryptogenic
  • Pneumonia, Cryptogenic Organizing
  • Bronchiolitis Obliterans Organizing Pneumonia
  • BOOP Bronchiolitis Obliterans Organizing Pneumonia
  • Primary Organizing Pneumonia
  • Organizing Pneumonia, Primary
  • Organizing Pneumonias, Primary
  • Pneumonia, Primary Organizing
  • Primary Organizing Pneumonias

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