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Hypoplastic left heart

MedGen UID:
505616
Concept ID:
CN003882
Finding
Synonyms: Underdeveloped left heart
 

Definition

Underdevelopment of the left side of the heart. May include atresia of the aortic or mitral orifice and hypoplasia of the ascending aorta. [from HPO]

Recent clinical studies

Etiology

Lloyd DF, Rutherford MA, Simpson JM, Razavi R
Cardiol Young 2017 Mar;27(2):217-223. Epub 2016 Nov 8 doi: 10.1017/S1047951116001645. PMID: 27821206
Yerebakan C, Valeske K, Elmontaser H, Yörüker U, Mueller M, Thul J, Mann V, Latus H, Villanueva A, Hofmann K, Schranz D, Akintuerk H
J Thorac Cardiovasc Surg 2016 Apr;151(4):1112-21, 1123.e1-5. Epub 2015 Oct 27 doi: 10.1016/j.jtcvs.2015.10.066. PMID: 26704055
Kobayashi D, Natarajan G, Turner DR, Forbes TJ, Delius RE, Walters HL, Aggarwal S
Cardiol Young 2016 Jun;26(5):867-75. Epub 2015 Sep 8 doi: 10.1017/S1047951115001419. PMID: 26345472
Voges I, Jerosch-Herold M, Wegner P, Hart C, Gabbert D, Al Bulushi A, Fischer G, Andrade AC, Pham HM, Kristo I, Kramer HH, Rickers C
J Am Heart Assoc 2015 Oct 5;4(10):e002107. doi: 10.1161/JAHA.115.002107. PMID: 26438562Free PMC Article
Arai S, Fujii Y, Kotani Y, Kuroko Y, Kasahara S, Sano S
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1034-8. Epub 2015 Sep 23 doi: 10.1177/0218492315606581. PMID: 26405018

Diagnosis

Lloyd DF, Rutherford MA, Simpson JM, Razavi R
Cardiol Young 2017 Mar;27(2):217-223. Epub 2016 Nov 8 doi: 10.1017/S1047951116001645. PMID: 27821206
Yerebakan C, Valeske K, Elmontaser H, Yörüker U, Mueller M, Thul J, Mann V, Latus H, Villanueva A, Hofmann K, Schranz D, Akintuerk H
J Thorac Cardiovasc Surg 2016 Apr;151(4):1112-21, 1123.e1-5. Epub 2015 Oct 27 doi: 10.1016/j.jtcvs.2015.10.066. PMID: 26704055
Sathanandam SK, Philip R, Gamboa D, Van Bergen A, Ilbawi MN, Knott-Craig C, Waller BR, Javois AJ, Cuneo BF
Cardiol Young 2016 Aug;26(6):1072-81. Epub 2015 Sep 8 doi: 10.1017/S1047951115001791. PMID: 26346529
Voges I, Jerosch-Herold M, Wegner P, Hart C, Gabbert D, Al Bulushi A, Fischer G, Andrade AC, Pham HM, Kristo I, Kramer HH, Rickers C
J Am Heart Assoc 2015 Oct 5;4(10):e002107. doi: 10.1161/JAHA.115.002107. PMID: 26438562Free PMC Article
Arai S, Fujii Y, Kotani Y, Kuroko Y, Kasahara S, Sano S
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1034-8. Epub 2015 Sep 23 doi: 10.1177/0218492315606581. PMID: 26405018

Therapy

Ohye RG, Schranz D, D'Udekem Y
Circulation 2016 Oct 25;134(17):1265-1279. doi: 10.1161/CIRCULATIONAHA.116.022816. PMID: 27777296Free PMC Article
Yerebakan C, Valeske K, Elmontaser H, Yörüker U, Mueller M, Thul J, Mann V, Latus H, Villanueva A, Hofmann K, Schranz D, Akintuerk H
J Thorac Cardiovasc Surg 2016 Apr;151(4):1112-21, 1123.e1-5. Epub 2015 Oct 27 doi: 10.1016/j.jtcvs.2015.10.066. PMID: 26704055
Arai S, Fujii Y, Kotani Y, Kuroko Y, Kasahara S, Sano S
Asian Cardiovasc Thorac Ann 2015 Nov;23(9):1034-8. Epub 2015 Sep 23 doi: 10.1177/0218492315606581. PMID: 26405018
Malik S, Bird TM, Jaquiss RD, Morrow WR, Robbins JM
J Thorac Cardiovasc Surg 2015 Sep;150(3):474-80.e2. Epub 2015 Jul 4 doi: 10.1016/j.jtcvs.2015.06.071. PMID: 26242838
Ishigami S, Ohtsuki S, Tarui S, Ousaka D, Eitoku T, Kondo M, Okuyama M, Kobayashi J, Baba K, Arai S, Kawabata T, Yoshizumi K, Tateishi A, Kuroko Y, Iwasaki T, Sato S, Kasahara S, Sano S, Oh H
Circ Res 2015 Feb 13;116(4):653-64. Epub 2014 Nov 17 doi: 10.1161/CIRCRESAHA.116.304671. PMID: 25403163

Prognosis

Hoffman GM, Ghanayem NS, Scott JP, Tweddell JS, Mitchell ME, Mussatto KA
Ann Thorac Surg 2017 May;103(5):1527-1535. Epub 2016 Dec 21 doi: 10.1016/j.athoracsur.2016.09.100. PMID: 28012642
Sathanandam SK, Philip R, Gamboa D, Van Bergen A, Ilbawi MN, Knott-Craig C, Waller BR, Javois AJ, Cuneo BF
Cardiol Young 2016 Aug;26(6):1072-81. Epub 2015 Sep 8 doi: 10.1017/S1047951115001791. PMID: 26346529
Voges I, Jerosch-Herold M, Wegner P, Hart C, Gabbert D, Al Bulushi A, Fischer G, Andrade AC, Pham HM, Kristo I, Kramer HH, Rickers C
J Am Heart Assoc 2015 Oct 5;4(10):e002107. doi: 10.1161/JAHA.115.002107. PMID: 26438562Free PMC Article
Malik S, Bird TM, Jaquiss RD, Morrow WR, Robbins JM
J Thorac Cardiovasc Surg 2015 Sep;150(3):474-80.e2. Epub 2015 Jul 4 doi: 10.1016/j.jtcvs.2015.06.071. PMID: 26242838
Schlangen J, Petko C, Hansen JH, Michel M, Hart C, Uebing A, Fischer G, Becker K, Kramer HH
Circ Cardiovasc Imaging 2014 Nov;7(6):880-6. Epub 2014 Sep 30 doi: 10.1161/CIRCIMAGING.114.002110. PMID: 25270741

Clinical prediction guides

Hoffman GM, Ghanayem NS, Scott JP, Tweddell JS, Mitchell ME, Mussatto KA
Ann Thorac Surg 2017 May;103(5):1527-1535. Epub 2016 Dec 21 doi: 10.1016/j.athoracsur.2016.09.100. PMID: 28012642
Sathanandam SK, Philip R, Gamboa D, Van Bergen A, Ilbawi MN, Knott-Craig C, Waller BR, Javois AJ, Cuneo BF
Cardiol Young 2016 Aug;26(6):1072-81. Epub 2015 Sep 8 doi: 10.1017/S1047951115001791. PMID: 26346529
Voges I, Jerosch-Herold M, Wegner P, Hart C, Gabbert D, Al Bulushi A, Fischer G, Andrade AC, Pham HM, Kristo I, Kramer HH, Rickers C
J Am Heart Assoc 2015 Oct 5;4(10):e002107. doi: 10.1161/JAHA.115.002107. PMID: 26438562Free PMC Article
Malik S, Bird TM, Jaquiss RD, Morrow WR, Robbins JM
J Thorac Cardiovasc Surg 2015 Sep;150(3):474-80.e2. Epub 2015 Jul 4 doi: 10.1016/j.jtcvs.2015.06.071. PMID: 26242838
Schlangen J, Petko C, Hansen JH, Michel M, Hart C, Uebing A, Fischer G, Becker K, Kramer HH
Circ Cardiovasc Imaging 2014 Nov;7(6):880-6. Epub 2014 Sep 30 doi: 10.1161/CIRCIMAGING.114.002110. PMID: 25270741

Recent systematic reviews

Pigula FA, Mettler B
Semin Thorac Cardiovasc Surg 2017 Spring;29(1):64-69. Epub 2017 Feb 20 doi: 10.1053/j.semtcvs.2017.02.004. PMID: 28684000
Thakur V, Munk N, Mertens L, Nield LE
Prenat Diagn 2016 Sep;36(9):854-63. Epub 2016 Aug 21 doi: 10.1002/pd.4873. PMID: 27416335
Saul D, Degenhardt K, Iyoob SD, Surrey LF, Johnson AM, Johnson MP, Rychik J, Victoria T
Pediatr Radiol 2016 Apr;46(4):483-9. Epub 2015 Dec 21 doi: 10.1007/s00247-015-3514-6. PMID: 26691156
Danford DA, Karels Q, Kulkarni A, Hussain A, Xiao Y, Kutty S
Orphanet J Rare Dis 2015 Oct 22;10:137. doi: 10.1186/s13023-015-0355-1. PMID: 26494006Free PMC Article
Miller-Tate H, Stewart J, Allen R, Husain N, Rosen K, Cheatham JP, Galantowicz M, Cua CL
Congenit Heart Dis 2013 May-Jun;8(3):228-33. Epub 2012 Sep 25 doi: 10.1111/chd.12007. PMID: 23006134

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