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Nephrogenic Fibrosing Dermopathy

MedGen UID:
301436
Concept ID:
C1619692
Disease or Syndrome
Synonyms: Dermopathies, Nephrogenic Fibrosing; Dermopathy, Nephrogenic Fibrosing; Fibroses, Nephrogenic Systemic; Fibrosing Dermopathies, Nephrogenic; Fibrosing Dermopathy, Nephrogenic; Fibrosis, Nephrogenic Systemic; Nephrogenic Fibrosing Dermopathies; Nephrogenic Systemic Fibroses; Nephrogenic Systemic Fibrosis; Systemic Fibroses, Nephrogenic; Systemic Fibrosis, Nephrogenic
SNOMED CT: Nephrogenic fibrosing dermopathy (424114000); NSF - Nephrogenic fibrosing dermopathy (424114000)
 
Orphanet: ORPHA137617

Definition

A rare disorder characterized by fibrosis of the skin and internal organs. It occurs in patients with renal failure who had imaging studies performed using gadolinium. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNephrogenic systemic fibrosis
Follow this link to review classifications for Nephrogenic Fibrosing Dermopathy in Orphanet.

Recent clinical studies

Etiology

Firoz BF, Hunzeker CM, Soldano AC, Franks AG Jr
Dermatol Online J 2008 May 15;14(5):11. PMID: 18627747
Stratta P, Canavese C, Aime S
Curr Med Chem 2008;15(12):1229-35. PMID: 18473815
Aluma MS, Restrepo R, Gaviria M
Dermatol Online J 2007 Jul 13;13(3):24. PMID: 18328218
Sanchez-Ross M, Snyder R, Colome-Grimmer MI, Blumberg M, Huttenbach Y, Raimer S
Pediatr Dermatol 2007 Sep-Oct;24(5):E36-9. doi: 10.1111/j.1525-1470.2007.00437.x. PMID: 17958777
Cassis TB, Jackson JM, Sonnier GB, Callen JP
Int J Dermatol 2006 Jan;45(1):56-9. doi: 10.1111/j.1365-4632.2005.02701.x. PMID: 16426379

Diagnosis

Al Habeeb A, Partington S, Rosenthal D, Salama S
J Cutan Med Surg 2009 Mar-Apr;13(2):110-4. doi: 10.2310/7750.2008.07085. PMID: 19298781
Ragunatha S, Palit A, Inamadar AC, Madraki RM, Yelikar BR
Indian J Dermatol Venereol Leprol 2009 Jan-Feb;75(1):63-7. PMID: 19172035
Firoz BF, Hunzeker CM, Soldano AC, Franks AG Jr
Dermatol Online J 2008 May 15;14(5):11. PMID: 18627747
Prasad SR, Jagirdar J
J Comput Assist Tomogr 2008 Jan-Feb;32(1):1-3. doi: 10.1097/RCT.0b013e31805d08ee. PMID: 18303280
Sanchez-Ross M, Snyder R, Colome-Grimmer MI, Blumberg M, Huttenbach Y, Raimer S
Pediatr Dermatol 2007 Sep-Oct;24(5):E36-9. doi: 10.1111/j.1525-1470.2007.00437.x. PMID: 17958777

Therapy

Ragunatha S, Palit A, Inamadar AC, Madraki RM, Yelikar BR
Indian J Dermatol Venereol Leprol 2009 Jan-Feb;75(1):63-7. PMID: 19172035
Su HS, Nazarian RM, Scott JA
Br J Radiol 2009 Feb;82(974):e35-6. doi: 10.1259/bjr/20570152. PMID: 19168688
Prasad SR, Jagirdar J
J Comput Assist Tomogr 2008 Jan-Feb;32(1):1-3. doi: 10.1097/RCT.0b013e31805d08ee. PMID: 18303280
Sanchez-Ross M, Snyder R, Colome-Grimmer MI, Blumberg M, Huttenbach Y, Raimer S
Pediatr Dermatol 2007 Sep-Oct;24(5):E36-9. doi: 10.1111/j.1525-1470.2007.00437.x. PMID: 17958777
Hamilton-Persaud K, Ezell LD, Macklin JG
Nephrol Nurs J 2007 May-Jun;34(3):283-7; quiz 288. PMID: 17644872

Prognosis

Ragunatha S, Palit A, Inamadar AC, Madraki RM, Yelikar BR
Indian J Dermatol Venereol Leprol 2009 Jan-Feb;75(1):63-7. PMID: 19172035
Mathur K, Morris S, Deighan C, Green R, Douglas KW
J Clin Apher 2008;23(4):144-50. doi: 10.1002/jca.20170. PMID: 18633995
Firoz BF, Hunzeker CM, Soldano AC, Franks AG Jr
Dermatol Online J 2008 May 15;14(5):11. PMID: 18627747
Gibson SE, Farver CF, Prayson RA
Arch Pathol Lab Med 2006 Feb;130(2):209-12. doi: 10.1043/1543-2165(2006)130[209:MIINFD]2.0.CO;2. PMID: 16454565
Dupont A, Majithia V, Ahmad S, McMurray R
Am J Med Sci 2005 Oct;330(4):192-4. PMID: 16234612

Clinical prediction guides

Bose C, Megyesi JK, Shah SV, Hiatt KM, Hall KA, Karaduta O, Swaminathan S
PLoS One 2015;10(8):e0136563. Epub 2015 Aug 25 doi: 10.1371/journal.pone.0136563. PMID: 26305890Free PMC Article
Deng AC, Bilu Martin D, Sina B, Gaspari A
J Am Acad Dermatol 2008 Feb;58(2):336-9. doi: 10.1016/j.jaad.2007.10.491. PMID: 18222333
Boyd AS, Zic JA, Abraham JL
J Am Acad Dermatol 2007 Jan;56(1):27-30. Epub 2006 Nov 15 doi: 10.1016/j.jaad.2006.10.048. PMID: 17109993
Lewis KG, Lester BW, Pan TD, Robinson-Bostom L
J Cutan Pathol 2006 Oct;33(10):695-700. doi: 10.1111/j.1600-0560.2006.00490.x. PMID: 17026522
Cassis TB, Jackson JM, Sonnier GB, Callen JP
Int J Dermatol 2006 Jan;45(1):56-9. doi: 10.1111/j.1365-4632.2005.02701.x. PMID: 16426379

Recent systematic reviews

Haneder S, Kucharczyk W, Schoenberg SO, Michaely HJ
Top Magn Reson Imaging 2015 Feb;24(1):57-65. doi: 10.1097/RMR.0b013e3182a14e79. PMID: 25654421
Thomsen HS
Acta Radiol 2014 Sep;55(7):771-5. doi: 10.1177/0284185114533537. PMID: 25138436
Heverhagen JT, Krombach GA, Gizewski E
Rofo 2014 Jul;186(7):661-9. Epub 2014 Jan 29 doi: 10.1055/s-0033-1356403. PMID: 24477507
Morcos SK
Eur Radiol 2011 Mar;21(3):496-500. Epub 2010 Sep 17 doi: 10.1007/s00330-010-1951-z. PMID: 20848109
Abdel-Kader K, Patel PR, Kallen AJ, Sinkowitz-Cochran RL, Bolton WK, Unruh ML
Clin J Am Soc Nephrol 2010 Jun;5(6):964-71. Epub 2010 Mar 18 doi: 10.2215/CJN.00140110. PMID: 20299369Free PMC Article

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