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Dandy-Walker variant

MedGen UID:
418961
•Concept ID:
C2931015
•
Disease or Syndrome
Synonym: Dandy Walker variant

Professional guidelines

PubMed

Enlarged posterior fossa on prenatal imaging: differential diagnosis, associated anomalies and postnatal outcome.
Wüest A, Surbek D, Wiest R, Weisstanner C, Bonel H, Steinlin M, Raio L, Tutschek B
Acta Obstet Gynecol Scand 2017 Jul;96(7):837-843. Epub 2017 Apr 10 doi: 10.1111/aogs.13131. PMID: 28295149
The fetal cerebellum. Pitfalls in diagnosis and management.
Malinger G, Lev D, Lerman-Sagie T
Prenat Diagn 2009 Apr;29(4):372-80. doi: 10.1002/pd.2196. PMID: 19194867
Dandy-Walker malformation: a review of 78 cases diagnosed by prenatal sonography.
Has R, Ermiş H, Yüksel A, Ibrahimoğlu L, Yildirim A, Sezer HD, Başaran S
Fetal Diagn Ther 2004 Jul-Aug;19(4):342-7. doi: 10.1159/000077963. PMID: 15192294

Recent clinical studies

Etiology

Management of Dandy-Walker complex-associated infant hydrocephalus by combined endoscopic third ventriculostomy and choroid plexus cauterization.
Warf BC, Dewan M, Mugamba J
J Neurosurg Pediatr 2011 Oct;8(4):377-83. doi: 10.3171/2011.7.PEDS1198. PMID: 21961544
Brain abnormalities on MR imaging in patients with retinoblastoma.
Rodjan F, de Graaf P, Moll AC, Imhof SM, Verbeke JI, Sanchez E, Castelijns JA
AJNR Am J Neuroradiol 2010 Sep;31(8):1385-9. Epub 2010 Apr 22 doi: 10.3174/ajnr.A2102. PMID: 20413604Free PMC Article
The fetal dandy walker complex: associated anomalies, perinatal outcome and postnatal imaging.
Harper T, Fordham LA, Wolfe HM
Fetal Diagn Ther 2007;22(4):277-81. doi: 10.1159/000100790. PMID: 17369695
Congenital unilateral hydrocephalus--CT findings.
Schulman H, Landau D, Schulman P, Hertzanu Y
Eur J Radiol 2000 Dec;36(3):161-4. doi: 10.1016/s0720-048x(00)00181-9. PMID: 11091018
Dandy-Walker malformation diagnosed before 21 weeks of gestation: associated malformations and chromosomal abnormalities.
Ulm B, Ulm MR, Deutinger J, Bernaschek G
Ultrasound Obstet Gynecol 1997 Sep;10(3):167-70. doi: 10.1046/j.1469-0705.1997.10030167.x. PMID: 9339523

Diagnosis

Hypoglycemia and Dandy-Walker variant in a Kabuki syndrome patient: a case report.
Guo W, Zhao Y, Li S, Wang J, Liu X
BMC Med Genet 2020 Oct 2;21(1):193. doi: 10.1186/s12881-020-01117-8. PMID: 33008324Free PMC Article
Posterior fossa malformations.
Shekdar K
Semin Ultrasound CT MR 2011 Jun;32(3):228-41. doi: 10.1053/j.sult.2011.02.003. PMID: 21596278
The fetal cerebellum. Pitfalls in diagnosis and management.
Malinger G, Lev D, Lerman-Sagie T
Prenat Diagn 2009 Apr;29(4):372-80. doi: 10.1002/pd.2196. PMID: 19194867
Dandy-Walker malformation: a review of 78 cases diagnosed by prenatal sonography.
Has R, Ermiş H, Yüksel A, Ibrahimoğlu L, Yildirim A, Sezer HD, Başaran S
Fetal Diagn Ther 2004 Jul-Aug;19(4):342-7. doi: 10.1159/000077963. PMID: 15192294
Dandy-Walker variant: prenatal sonographic features and clinical outcome.
Estroff JA, Scott MR, Benacerraf BR
Radiology 1992 Dec;185(3):755-8. doi: 10.1148/radiology.185.3.1438757. PMID: 1438757

Therapy

Lateral ventricle pleomorphic xanthoastrocytoma concurrent with Dandy-Walker complex: A case report.
Luo TF, Wang YB, Wang DH, Zhan S, Deng SL
Medicine (Baltimore) 2022 Sep 9;101(36):e30492. doi: 10.1097/MD.0000000000030492. PMID: 36086683Free PMC Article
Dandy-Walker variant with precocious puberty: a rare association.
Rajput R, Mishra S, Ahlawat P, Yadav PK
BMJ Case Rep 2018 Nov 28;11(1) doi: 10.1136/bcr-2018-226281. PMID: 30567100Free PMC Article
Atypical psychotic symptoms and Dandy-Walker variant.
Williams AJ, Wang Z, Taylor SF
Neurocase 2016 Oct;22(5):472-475. Epub 2016 Sep 23 doi: 10.1080/13554794.2016.1237657. PMID: 27662527
Endoscopic third ventriculostomy for obstructive hydrocephalus in children younger than 6 months of age.
Ogiwara H, Dipatri AJ Jr, Alden TD, Bowman RM, Tomita T
Childs Nerv Syst 2010 Mar;26(3):343-7. doi: 10.1007/s00381-009-1019-z. PMID: 19915853
Early-onset schizophrenia and obsessive-compulsive disorder in a young man with Dandy-Walker variant.
Papazisis G, Mastrogianni A, Karastergiou A
Schizophr Res 2007 Jul;93(1-3):403-5. Epub 2007 May 2 doi: 10.1016/j.schres.2007.03.019. PMID: 17478081

Prognosis

Not Dandy Walker variant: a review of prominent retrocerebellar CSF space in children.
Wee T, Gupta N, Miller E, Pauranik A
Clin Radiol 2024 May;79(5):330-337. Epub 2024 Feb 3 doi: 10.1016/j.crad.2024.01.025. PMID: 38429135
Atypical psychotic symptoms and Dandy-Walker variant.
Williams AJ, Wang Z, Taylor SF
Neurocase 2016 Oct;22(5):472-475. Epub 2016 Sep 23 doi: 10.1080/13554794.2016.1237657. PMID: 27662527
Dandy-Walker malformation: a review of 78 cases diagnosed by prenatal sonography.
Has R, Ermiş H, Yüksel A, Ibrahimoğlu L, Yildirim A, Sezer HD, Başaran S
Fetal Diagn Ther 2004 Jul-Aug;19(4):342-7. doi: 10.1159/000077963. PMID: 15192294
The sonographic diagnosis of Dandy-Walker and Dandy-Walker variant: associated findings and outcomes.
Ecker JL, Shipp TD, Bromley B, Benacerraf B
Prenat Diagn 2000 Apr;20(4):328-32. PMID: 10740206
Dandy-Walker variant: prenatal sonographic features and clinical outcome.
Estroff JA, Scott MR, Benacerraf BR
Radiology 1992 Dec;185(3):755-8. doi: 10.1148/radiology.185.3.1438757. PMID: 1438757

Clinical prediction guides

Not Dandy Walker variant: a review of prominent retrocerebellar CSF space in children.
Wee T, Gupta N, Miller E, Pauranik A
Clin Radiol 2024 May;79(5):330-337. Epub 2024 Feb 3 doi: 10.1016/j.crad.2024.01.025. PMID: 38429135
Basilar invagination in a child with atlanto-occipital subluxation and suspected prenatal Dandy-Walker malformation.
Miura I, Aihara Y, Mitsuyama T, Chiba K, Nakano H, Kawamata T
Childs Nerv Syst 2019 Aug;35(8):1429-1434. Epub 2019 May 17 doi: 10.1007/s00381-019-04164-6. PMID: 31101983
The Dandy-Walker variant: a case series of 24 pediatric patients and evaluation of associated anomalies, incidence of hydrocephalus, and developmental outcomes.
Sasaki-Adams D, Elbabaa SK, Jewells V, Carter L, Campbell JW, Ritter AM
J Neurosurg Pediatr 2008 Sep;2(3):194-9. doi: 10.3171/PED/2008/2/9/194. PMID: 18759601
The fetal dandy walker complex: associated anomalies, perinatal outcome and postnatal imaging.
Harper T, Fordham LA, Wolfe HM
Fetal Diagn Ther 2007;22(4):277-81. doi: 10.1159/000100790. PMID: 17369695
The sonographic diagnosis of Dandy-Walker and Dandy-Walker variant: associated findings and outcomes.
Ecker JL, Shipp TD, Bromley B, Benacerraf B
Prenat Diagn 2000 Apr;20(4):328-32. PMID: 10740206

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