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Mixed total anomalous pulmonary venous connection

MedGen UID:
866777
•Concept ID:
C4021128
•
Anatomical Abnormality
Synonyms: Mixed total anomalous pulmonary venous connexion; Total anomalous pulmonary venous connection, mixed; Type 4 total anomalous pulmonary venous connection
 
HPO: HP:0011722

Definition

Type 4 total anomalous pulmonary venous connection. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMixed total anomalous pulmonary venous connection

Professional guidelines

PubMed

Integrated model for the prenatal diagnosis and postnatal surgical treatment of total anomalous pulmonary venous connection: A multidisciplinary collaborative experience and preliminary results.
Yang L, He X, Lu Y, Huang F, Shi G, Chen H, Zheng J, Zhu Z, Chen P
J Card Surg 2019 Nov;34(11):1264-1272. Epub 2019 Sep 2 doi: 10.1111/jocs.14242. PMID: 31475761
Single Ventricle and Total Anomalous Pulmonary Venous Connection: Implications of Prenatal Diagnosis.
Hancock HS, Romano JC, Armstrong A, Yu S, Lowery R, Gelehrter S
World J Pediatr Congenit Heart Surg 2018 Jul;9(4):434-439. doi: 10.1177/2150135118771344. PMID: 29945508
Surgery for total anomalous pulmonary venous connection: primary sutureless repair vs. conventional repair.
Yoshimura N, Fukahara K, Yamashita A, Doi T, Takeuchi K, Yamashita S, Homma T, Yokoyama S, Aoki M, Ikeno Y
Gen Thorac Cardiovasc Surg 2017 May;65(5):245-251. Epub 2017 Mar 22 doi: 10.1007/s11748-017-0769-x. PMID: 28332089

Recent clinical studies

Etiology

Review of surgical experience in 61 patients with mixed total anomalous pulmonary venous connection.
Wen C, Shi G, Zhang Q, Zhu F, Zhang H, Zhu Z, Chen H
Eur J Cardiothorac Surg 2022 May 27;61(6):1299-1305. doi: 10.1093/ejcts/ezac020. PMID: 35076062
Multidisciplinary management of a rare case of mixed total anomalous pulmonary venous connection.
Ghidini F, Castaldi B, Padalino M, Dall'Igna P
J Card Surg 2021 Jul;36(7):2562-2564. Epub 2021 Mar 29 doi: 10.1111/jocs.15545. PMID: 33783038
Postoperative Obstruction of the Pulmonary Veins in Mixed Total Anomalous Pulmonary Venous Connection.
Ho DY, White BR, Glatz AC, Mascio CE, Stephens P Jr, Cohen MS
Pediatr Cardiol 2018 Oct;39(7):1489-1495. Epub 2018 Jun 5 doi: 10.1007/s00246-018-1921-9. PMID: 29872881
Mixed total anomalous pulmonary venous connection: anatomic variations, surgical approach, techniques, and results.
Chowdhury UK, Airan B, Malhotra A, Bisoi AK, Saxena A, Kothari SS, Kalaivani M, Venugopal P
J Thorac Cardiovasc Surg 2008 Jan;135(1):106-16, 116.e1-5. doi: 10.1016/j.jtcvs.2007.08.028. PMID: 18179926
Cross sectional echocardiographic diagnosis of total anomalous pulmonary venous connection.
Huhta JC, Gutgesell HP, Nihill MR
Br Heart J 1985 May;53(5):525-34. doi: 10.1136/hrt.53.5.525. PMID: 3994866Free PMC Article

Diagnosis

Multidisciplinary management of a rare case of mixed total anomalous pulmonary venous connection.
Ghidini F, Castaldi B, Padalino M, Dall'Igna P
J Card Surg 2021 Jul;36(7):2562-2564. Epub 2021 Mar 29 doi: 10.1111/jocs.15545. PMID: 33783038
Two-stage approach for mixed total anomalous pulmonary venous connection.
Kasama K, Gewillig M, Rega F, Meyns B
Asian Cardiovasc Thorac Ann 2016 Feb;24(2):165-6. Epub 2014 Sep 2 doi: 10.1177/0218492314549198. PMID: 25182337
Mixed total anomalous pulmonary venous connection: anatomic variations, surgical approach, techniques, and results.
Chowdhury UK, Airan B, Malhotra A, Bisoi AK, Saxena A, Kothari SS, Kalaivani M, Venugopal P
J Thorac Cardiovasc Surg 2008 Jan;135(1):106-16, 116.e1-5. doi: 10.1016/j.jtcvs.2007.08.028. PMID: 18179926
Mixed total anomalous pulmonary venous connection: Case report with bilateral venous collectors.
Cayre RO, Civetta JD, Roldan AO, Rousseau JJ, Knudson OA Jr, Valdes-Cruz LM
J Am Soc Echocardiogr 2003 Jan;16(1):84-7. doi: 10.1067/mje.2003.28. PMID: 12514641
Cross sectional echocardiographic diagnosis of total anomalous pulmonary venous connection.
Huhta JC, Gutgesell HP, Nihill MR
Br Heart J 1985 May;53(5):525-34. doi: 10.1136/hrt.53.5.525. PMID: 3994866Free PMC Article

Therapy

Postoperative Obstruction of the Pulmonary Veins in Mixed Total Anomalous Pulmonary Venous Connection.
Ho DY, White BR, Glatz AC, Mascio CE, Stephens P Jr, Cohen MS
Pediatr Cardiol 2018 Oct;39(7):1489-1495. Epub 2018 Jun 5 doi: 10.1007/s00246-018-1921-9. PMID: 29872881
Left-sided scimitar vein causing cyanosis after Fontan operation: successful transcatheter device occlusion using magnetic resonance imaging X-ray fusion.
Downing TE, Dori Y, Harris MA, Glatz AC
Congenit Heart Dis 2014 Nov-Dec;9(6):E199-203. Epub 2013 Aug 14 doi: 10.1111/chd.12133. PMID: 23941525

Prognosis

Review of surgical experience in 61 patients with mixed total anomalous pulmonary venous connection.
Wen C, Shi G, Zhang Q, Zhu F, Zhang H, Zhu Z, Chen H
Eur J Cardiothorac Surg 2022 May 27;61(6):1299-1305. doi: 10.1093/ejcts/ezac020. PMID: 35076062
A rare variety of mixed total anomalous pulmonary venous connection.
Mishra A, Sharma P, Patel R, Panchal J, Solanki A
Asian Cardiovasc Thorac Ann 2014 Sep;22(7):849-51. Epub 2013 Oct 17 doi: 10.1177/0218492313486120. PMID: 24887821
Left-sided scimitar vein causing cyanosis after Fontan operation: successful transcatheter device occlusion using magnetic resonance imaging X-ray fusion.
Downing TE, Dori Y, Harris MA, Glatz AC
Congenit Heart Dis 2014 Nov-Dec;9(6):E199-203. Epub 2013 Aug 14 doi: 10.1111/chd.12133. PMID: 23941525
Modified repair of mixed total anomalous pulmonary venous connection.
Berdat PA, Pfammatter JP, Genyk I, Carrel TP
Ann Thorac Surg 2001 Feb;71(2):723-5. doi: 10.1016/s0003-4975(00)02239-6. PMID: 11235745
Cross sectional echocardiographic diagnosis of total anomalous pulmonary venous connection.
Huhta JC, Gutgesell HP, Nihill MR
Br Heart J 1985 May;53(5):525-34. doi: 10.1136/hrt.53.5.525. PMID: 3994866Free PMC Article

Clinical prediction guides

Review of surgical experience in 61 patients with mixed total anomalous pulmonary venous connection.
Wen C, Shi G, Zhang Q, Zhu F, Zhang H, Zhu Z, Chen H
Eur J Cardiothorac Surg 2022 May 27;61(6):1299-1305. doi: 10.1093/ejcts/ezac020. PMID: 35076062
Left-sided scimitar vein causing cyanosis after Fontan operation: successful transcatheter device occlusion using magnetic resonance imaging X-ray fusion.
Downing TE, Dori Y, Harris MA, Glatz AC
Congenit Heart Dis 2014 Nov-Dec;9(6):E199-203. Epub 2013 Aug 14 doi: 10.1111/chd.12133. PMID: 23941525
Mixed total anomalous pulmonary venous connection: anatomic variations, surgical approach, techniques, and results.
Chowdhury UK, Airan B, Malhotra A, Bisoi AK, Saxena A, Kothari SS, Kalaivani M, Venugopal P
J Thorac Cardiovasc Surg 2008 Jan;135(1):106-16, 116.e1-5. doi: 10.1016/j.jtcvs.2007.08.028. PMID: 18179926
Cross sectional echocardiographic diagnosis of total anomalous pulmonary venous connection.
Huhta JC, Gutgesell HP, Nihill MR
Br Heart J 1985 May;53(5):525-34. doi: 10.1136/hrt.53.5.525. PMID: 3994866Free PMC Article

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