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Pentaplegic cerebral palsy

MedGen UID:
824628
Concept ID:
C3838782
Disease or Syndrome
SNOMED CT: Pentaplegic cerebral palsy (702321005)

Definition

A form of spastic cerebral palsy affecting all four limbs with neck and head paralysis, often accompanied by eating and breathing complications. [from SNOMEDCT_US]

Professional guidelines

PubMed

Patricios JS, Schneider KJ, Dvorak J, Ahmed OH, Blauwet C, Cantu RC, Davis GA, Echemendia RJ, Makdissi M, McNamee M, Broglio S, Emery CA, Feddermann-Demont N, Fuller GW, Giza CC, Guskiewicz KM, Hainline B, Iverson GL, Kutcher JS, Leddy JJ, Maddocks D, Manley G, McCrea M, Purcell LK, Putukian M, Sato H, Tuominen MP, Turner M, Yeates KO, Herring SA, Meeuwisse W
Br J Sports Med 2023 Jun;57(11):695-711. doi: 10.1136/bjsports-2023-106898. PMID: 37316210
Conde-Agudelo A, Romero R, Jung EJ, Garcia Sánchez ÁJ
Am J Obstet Gynecol 2020 Dec;223(6):848-869. Epub 2020 Sep 29 doi: 10.1016/j.ajog.2020.09.044. PMID: 33007269Free PMC Article
Novak I, Morgan C, Adde L, Blackman J, Boyd RN, Brunstrom-Hernandez J, Cioni G, Damiano D, Darrah J, Eliasson AC, de Vries LS, Einspieler C, Fahey M, Fehlings D, Ferriero DM, Fetters L, Fiori S, Forssberg H, Gordon AM, Greaves S, Guzzetta A, Hadders-Algra M, Harbourne R, Kakooza-Mwesige A, Karlsson P, Krumlinde-Sundholm L, Latal B, Loughran-Fowlds A, Maitre N, McIntyre S, Noritz G, Pennington L, Romeo DM, Shepherd R, Spittle AJ, Thornton M, Valentine J, Walker K, White R, Badawi N
JAMA Pediatr 2017 Sep 1;171(9):897-907. doi: 10.1001/jamapediatrics.2017.1689. PMID: 28715518Free PMC Article

Recent clinical studies

Etiology

Paul S, Nahar A, Bhagawati M, Kunwar AJ
Oxid Med Cell Longev 2022;2022:2622310. Epub 2022 Jul 30 doi: 10.1155/2022/2622310. PMID: 35941906Free PMC Article
Upadhyay J, Tiwari N, Ansari MN
Clin Exp Pharmacol Physiol 2020 Dec;47(12):1891-1901. Epub 2020 Aug 19 doi: 10.1111/1440-1681.13379. PMID: 32662125
Novak I, Morgan C, Adde L, Blackman J, Boyd RN, Brunstrom-Hernandez J, Cioni G, Damiano D, Darrah J, Eliasson AC, de Vries LS, Einspieler C, Fahey M, Fehlings D, Ferriero DM, Fetters L, Fiori S, Forssberg H, Gordon AM, Greaves S, Guzzetta A, Hadders-Algra M, Harbourne R, Kakooza-Mwesige A, Karlsson P, Krumlinde-Sundholm L, Latal B, Loughran-Fowlds A, Maitre N, McIntyre S, Noritz G, Pennington L, Romeo DM, Shepherd R, Spittle AJ, Thornton M, Valentine J, Walker K, White R, Badawi N
JAMA Pediatr 2017 Sep 1;171(9):897-907. doi: 10.1001/jamapediatrics.2017.1689. PMID: 28715518Free PMC Article
Graham HK, Rosenbaum P, Paneth N, Dan B, Lin JP, Damiano DL, Becher JG, Gaebler-Spira D, Colver A, Reddihough DS, Crompton KE, Lieber RL
Nat Rev Dis Primers 2016 Jan 7;2:15082. doi: 10.1038/nrdp.2015.82. PMID: 27188686Free PMC Article
Wimalasundera N, Stevenson VL
Pract Neurol 2016 Jun;16(3):184-94. Epub 2016 Feb 2 doi: 10.1136/practneurol-2015-001184. PMID: 26837375

Diagnosis

Paul S, Nahar A, Bhagawati M, Kunwar AJ
Oxid Med Cell Longev 2022;2022:2622310. Epub 2022 Jul 30 doi: 10.1155/2022/2622310. PMID: 35941906Free PMC Article
Upadhyay J, Tiwari N, Ansari MN
Clin Exp Pharmacol Physiol 2020 Dec;47(12):1891-1901. Epub 2020 Aug 19 doi: 10.1111/1440-1681.13379. PMID: 32662125
Vitrikas K, Dalton H, Breish D
Am Fam Physician 2020 Feb 15;101(4):213-220. PMID: 32053326
Novak I, Morgan C, Adde L, Blackman J, Boyd RN, Brunstrom-Hernandez J, Cioni G, Damiano D, Darrah J, Eliasson AC, de Vries LS, Einspieler C, Fahey M, Fehlings D, Ferriero DM, Fetters L, Fiori S, Forssberg H, Gordon AM, Greaves S, Guzzetta A, Hadders-Algra M, Harbourne R, Kakooza-Mwesige A, Karlsson P, Krumlinde-Sundholm L, Latal B, Loughran-Fowlds A, Maitre N, McIntyre S, Noritz G, Pennington L, Romeo DM, Shepherd R, Spittle AJ, Thornton M, Valentine J, Walker K, White R, Badawi N
JAMA Pediatr 2017 Sep 1;171(9):897-907. doi: 10.1001/jamapediatrics.2017.1689. PMID: 28715518Free PMC Article
Wimalasundera N, Stevenson VL
Pract Neurol 2016 Jun;16(3):184-94. Epub 2016 Feb 2 doi: 10.1136/practneurol-2015-001184. PMID: 26837375

Therapy

Rebelo F, Mansur IR, Miglioli TC, Meio MDB, Junior SCG
PLoS One 2022;17(7):e0271993. Epub 2022 Jul 22 doi: 10.1371/journal.pone.0271993. PMID: 35867728Free PMC Article
Liang X, Tan Z, Yun G, Cao J, Wang J, Liu Q, Chen T
J Rehabil Med 2021 Apr 1;53(4):jrm00176. doi: 10.2340/16501977-2772. PMID: 33225375Free PMC Article
Hoare BJ, Wallen MA, Thorley MN, Jackman ML, Carey LM, Imms C
Cochrane Database Syst Rev 2019 Apr 1;4(4):CD004149. doi: 10.1002/14651858.CD004149.pub3. PMID: 30932166Free PMC Article
Novak I, McIntyre S, Morgan C, Campbell L, Dark L, Morton N, Stumbles E, Wilson SA, Goldsmith S
Dev Med Child Neurol 2013 Oct;55(10):885-910. Epub 2013 Aug 21 doi: 10.1111/dmcn.12246. PMID: 23962350
Steultjens EM, Dekker J, Bouter LM, van de Nes JC, Lambregts BL, van den Ende CH
Clin Rehabil 2004 Feb;18(1):1-14. doi: 10.1191/0269215504cr697oa. PMID: 14763715

Prognosis

Barron-Garza F, Coronado-Garza M, Gutierrez-Ramirez S, Ramos-Rincon JM, Guzman-de la Garza F, Lozano-Morantes A, Flores-Rodriguez A, Nieto-Sanjuanero A, Alvarez-Villalobos N, Flores-Villarreal M, Covarrubias-Contreras L
Pediatr Neurol 2023 Jun;143:50-58. Epub 2023 Mar 3 doi: 10.1016/j.pediatrneurol.2023.02.005. PMID: 37001462
San Juan AM, Swaroop VT
Pediatr Ann 2022 Sep;51(9):e353-e356. Epub 2022 Sep 1 doi: 10.3928/19382359-20220706-06. PMID: 36098607
Koy A, Timmermann L
Eur J Paediatr Neurol 2017 Jan;21(1):118-121. Epub 2016 May 27 doi: 10.1016/j.ejpn.2016.05.015. PMID: 27289260
Baker R, Esquenazi A, Benedetti MG, Desloovere K
Eur J Phys Rehabil Med 2016 Aug;52(4):560-74. PMID: 27618499
Dabney KW, Lipton GE, Miller F
Curr Opin Pediatr 1997 Feb;9(1):81-8. doi: 10.1097/00008480-199702000-00017. PMID: 9088760

Clinical prediction guides

Saranti A, Dragoumi P, Papavasiliou A, Zafeiriou D
Eur J Paediatr Neurol 2024 Jul;51:49-57. Epub 2024 May 31 doi: 10.1016/j.ejpn.2024.05.015. PMID: 38824721
Novak I, Morgan C, Fahey M, Finch-Edmondson M, Galea C, Hines A, Langdon K, Namara MM, Paton MC, Popat H, Shore B, Khamis A, Stanton E, Finemore OP, Tricks A, Te Velde A, Dark L, Morton N, Badawi N
Curr Neurol Neurosci Rep 2020 Feb 21;20(2):3. doi: 10.1007/s11910-020-1022-z. PMID: 32086598Free PMC Article
Wimalasundera N, Stevenson VL
Pract Neurol 2016 Jun;16(3):184-94. Epub 2016 Feb 2 doi: 10.1136/practneurol-2015-001184. PMID: 26837375
Einspieler C, Prechtl HF
Ment Retard Dev Disabil Res Rev 2005;11(1):61-7. doi: 10.1002/mrdd.20051. PMID: 15856440
Palisano R, Rosenbaum P, Walter S, Russell D, Wood E, Galuppi B
Dev Med Child Neurol 1997 Apr;39(4):214-23. doi: 10.1111/j.1469-8749.1997.tb07414.x. PMID: 9183258

Recent systematic reviews

Tapia C, Constanzo J, González V, Barría RM
Dev Neurorehabil 2023 Aug-Oct;26(6-7):371-376. Epub 2024 Jan 6 doi: 10.1080/17518423.2023.2259986. PMID: 37728374
McIntyre S, Goldsmith S, Webb A, Ehlinger V, Hollung SJ, McConnell K, Arnaud C, Smithers-Sheedy H, Oskoui M, Khandaker G, Himmelmann K; Global CP Prevalence Group*
Dev Med Child Neurol 2022 Dec;64(12):1494-1506. Epub 2022 Aug 11 doi: 10.1111/dmcn.15346. PMID: 35952356Free PMC Article
Novak I, Morgan C, Fahey M, Finch-Edmondson M, Galea C, Hines A, Langdon K, Namara MM, Paton MC, Popat H, Shore B, Khamis A, Stanton E, Finemore OP, Tricks A, Te Velde A, Dark L, Morton N, Badawi N
Curr Neurol Neurosci Rep 2020 Feb 21;20(2):3. doi: 10.1007/s11910-020-1022-z. PMID: 32086598Free PMC Article
Dewar R, Love S, Johnston LM
Dev Med Child Neurol 2015 Jun;57(6):504-20. Epub 2014 Dec 18 doi: 10.1111/dmcn.12660. PMID: 25523410
Novak I, McIntyre S, Morgan C, Campbell L, Dark L, Morton N, Stumbles E, Wilson SA, Goldsmith S
Dev Med Child Neurol 2013 Oct;55(10):885-910. Epub 2013 Aug 21 doi: 10.1111/dmcn.12246. PMID: 23962350

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