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Stage 2A Neuroblastoma

MedGen UID:
769601
Concept ID:
C3640961
Neoplastic Process
Synonym: Stage IIA Neuroblastoma

Definition

Localized tumor with incomplete gross excision; representative ipsilateral nonadherent lymph nodes negative for tumor microscopically. (cancer.gov) [from NCI]

Term Hierarchy

Professional guidelines

PubMed

Fuji H, Schneider U, Ishida Y, Konno M, Yamashita H, Kase Y, Murayama S, Onoe T, Ogawa H, Harada H, Asakura H, Nishimura T
Radiat Oncol 2013 Nov 1;8:255. doi: 10.1186/1748-717X-8-255. PMID: 24180282Free PMC Article
Iehara T, Hamazaki M, Tajiri T, Kawano Y, Kaneko M, Ikeda H, Hosoi H, Sugimoto T, Sawada T; Japanese Infantile Neuroblastoma Cooperative Study Group
Int J Clin Oncol 2013 Jun;18(3):389-95. Epub 2012 Mar 2 doi: 10.1007/s10147-012-0391-y. PMID: 22383024
Haase GM, Atkinson JB, Stram DO, Lukens JN, Matthay KK
J Pediatr Surg 1995 Feb;30(2):289-94; discussion 295. doi: 10.1016/0022-3468(95)90576-6. PMID: 7738753

Recent clinical studies

Etiology

Twist CJ, Schmidt ML, Naranjo A, London WB, Tenney SC, Marachelian A, Shimada H, Collins MH, Esiashvili N, Adkins ES, Mattei P, Handler M, Katzenstein H, Attiyeh E, Hogarty MD, Gastier-Foster J, Wagner E, Matthay KK, Park JR, Maris JM, Cohn SL
J Clin Oncol 2019 Dec 1;37(34):3243-3255. Epub 2019 Aug 6 doi: 10.1200/JCO.19.00919. PMID: 31386611Free PMC Article
Iehara T, Hamazaki M, Tajiri T, Kawano Y, Kaneko M, Ikeda H, Hosoi H, Sugimoto T, Sawada T; Japanese Infantile Neuroblastoma Cooperative Study Group
Int J Clin Oncol 2013 Jun;18(3):389-95. Epub 2012 Mar 2 doi: 10.1007/s10147-012-0391-y. PMID: 22383024
Ikeda H, Iehara T, Tsuchida Y, Kaneko M, Hata J, Naito H, Iwafuchi M, Ohnuma N, Mugishima H, Toyoda Y, Hamazaki M, Mimaya J, Kondo S, Kawa K, Okada A, Hiyama E, Suita S, Takamatsu H
Br J Cancer 2002 Apr 8;86(7):1110-6. doi: 10.1038/sj.bjc.6600231. PMID: 11953858Free PMC Article
Halperin EC
Int J Radiat Oncol Biol Phys 2000 Apr 1;47(1):171-8. doi: 10.1016/s0360-3016(00)00424-7. PMID: 10758320
Cheung NK, Kushner BH, LaQuaglia MP, Kramer K, Ambros P, Ambros I, Ladanyi M, Eddy J, Bonilla MA, Gerald W
Eur J Cancer 1997 Oct;33(12):2117-20. doi: 10.1016/s0959-8049(97)00281-5. PMID: 9516865

Diagnosis

Martucciello G, Lerone M, Bricco L, Tonini GP, Lombardi L, Del Rossi CG, Bernasconi S
Ital J Pediatr 2012 Mar 19;38:9. doi: 10.1186/1824-7288-38-9. PMID: 22429913Free PMC Article
Tajiri T, Souzaki R, Kinoshita Y, Tanaka S, Koga Y, Suminoe A, Matsuzaki A, Hara T, Taguchi T
J Pediatr Surg 2009 Dec;44(12):2253-7. doi: 10.1016/j.jpedsurg.2009.07.050. PMID: 20006005
Michels E, Vandesompele J, De Preter K, Hoebeeck J, Vermeulen J, Schramm A, Molenaar JJ, Menten B, Marques B, Stallings RL, Combaret V, Devalck C, De Paepe A, Versteeg R, Eggert A, Laureys G, Van Roy N, Speleman F
Genes Chromosomes Cancer 2007 Dec;46(12):1098-108. doi: 10.1002/gcc.20496. PMID: 17823929
Gondim J, Ramos F Jr, Azevedo J, Carrero FP Jr, Tella OI Jr
Arq Neuropsiquiatr 2002 Jun;60(2-A):303-7. doi: 10.1590/s0004-282x2002000200024. PMID: 12068366
Halperin EC
Int J Radiat Oncol Biol Phys 2000 Apr 1;47(1):171-8. doi: 10.1016/s0360-3016(00)00424-7. PMID: 10758320

Therapy

Ambros IM, Tonini GP, Pötschger U, Gross N, Mosseri V, Beiske K, Berbegall AP, Bénard J, Bown N, Caron H, Combaret V, Couturier J, Defferrari R, Delattre O, Jeison M, Kogner P, Lunec J, Marques B, Martinsson T, Mazzocco K, Noguera R, Schleiermacher G, Valent A, Van Roy N, Villamon E, Janousek D, Pribill I, Glogova E, Attiyeh EF, Hogarty MD, Monclair TF, Holmes K, Valteau-Couanet D, Castel V, Tweddle DA, Park JR, Cohn S, Ladenstein R, Beck-Popovic M, De Bernardi B, Michon J, Pearson ADJ, Ambros PF
J Clin Oncol 2020 Nov 1;38(31):3685-3697. Epub 2020 Sep 9 doi: 10.1200/JCO.18.02132. PMID: 32903140Free PMC Article
Twist CJ, Schmidt ML, Naranjo A, London WB, Tenney SC, Marachelian A, Shimada H, Collins MH, Esiashvili N, Adkins ES, Mattei P, Handler M, Katzenstein H, Attiyeh E, Hogarty MD, Gastier-Foster J, Wagner E, Matthay KK, Park JR, Maris JM, Cohn SL
J Clin Oncol 2019 Dec 1;37(34):3243-3255. Epub 2019 Aug 6 doi: 10.1200/JCO.19.00919. PMID: 31386611Free PMC Article
Fuji H, Schneider U, Ishida Y, Konno M, Yamashita H, Kase Y, Murayama S, Onoe T, Ogawa H, Harada H, Asakura H, Nishimura T
Radiat Oncol 2013 Nov 1;8:255. doi: 10.1186/1748-717X-8-255. PMID: 24180282Free PMC Article
Iehara T, Hamazaki M, Tajiri T, Kawano Y, Kaneko M, Ikeda H, Hosoi H, Sugimoto T, Sawada T; Japanese Infantile Neuroblastoma Cooperative Study Group
Int J Clin Oncol 2013 Jun;18(3):389-95. Epub 2012 Mar 2 doi: 10.1007/s10147-012-0391-y. PMID: 22383024
Navarro S, Amann G, Beiske K, Cullinane CJ, d'Amore ES, Gambini C, Mosseri V, De Bernardi B, Michon J, Peuchmaur M; European Study Group 94.01 Trial and Protocol
J Clin Oncol 2006 Feb 1;24(4):695-9. doi: 10.1200/JCO.2004.00.8631. PMID: 16446343

Prognosis

Twist CJ, Schmidt ML, Naranjo A, London WB, Tenney SC, Marachelian A, Shimada H, Collins MH, Esiashvili N, Adkins ES, Mattei P, Handler M, Katzenstein H, Attiyeh E, Hogarty MD, Gastier-Foster J, Wagner E, Matthay KK, Park JR, Maris JM, Cohn SL
J Clin Oncol 2019 Dec 1;37(34):3243-3255. Epub 2019 Aug 6 doi: 10.1200/JCO.19.00919. PMID: 31386611Free PMC Article
Iehara T, Hamazaki M, Tajiri T, Kawano Y, Kaneko M, Ikeda H, Hosoi H, Sugimoto T, Sawada T; Japanese Infantile Neuroblastoma Cooperative Study Group
Int J Clin Oncol 2013 Jun;18(3):389-95. Epub 2012 Mar 2 doi: 10.1007/s10147-012-0391-y. PMID: 22383024
Martucciello G, Lerone M, Bricco L, Tonini GP, Lombardi L, Del Rossi CG, Bernasconi S
Ital J Pediatr 2012 Mar 19;38:9. doi: 10.1186/1824-7288-38-9. PMID: 22429913Free PMC Article
Gondim J, Ramos F Jr, Azevedo J, Carrero FP Jr, Tella OI Jr
Arq Neuropsiquiatr 2002 Jun;60(2-A):303-7. doi: 10.1590/s0004-282x2002000200024. PMID: 12068366
Halperin EC
Int J Radiat Oncol Biol Phys 2000 Apr 1;47(1):171-8. doi: 10.1016/s0360-3016(00)00424-7. PMID: 10758320

Clinical prediction guides

Sahu U, Sidhar H, Ghate PS, Advirao GM, Raghavan SC, Giri RK
PLoS One 2013;8(6):e66430. Epub 2013 Jun 18 doi: 10.1371/journal.pone.0066430. PMID: 23824039Free PMC Article
Pu J, Li Y, Liu Z, Yan Y, Tian J, Chen S, Zhang B
Mol Vis 2011 Feb 24;17:591-7. PMID: 21386928Free PMC Article
Michels E, Vandesompele J, De Preter K, Hoebeeck J, Vermeulen J, Schramm A, Molenaar JJ, Menten B, Marques B, Stallings RL, Combaret V, Devalck C, De Paepe A, Versteeg R, Eggert A, Laureys G, Van Roy N, Speleman F
Genes Chromosomes Cancer 2007 Dec;46(12):1098-108. doi: 10.1002/gcc.20496. PMID: 17823929
Navarro S, Amann G, Beiske K, Cullinane CJ, d'Amore ES, Gambini C, Mosseri V, De Bernardi B, Michon J, Peuchmaur M; European Study Group 94.01 Trial and Protocol
J Clin Oncol 2006 Feb 1;24(4):695-9. doi: 10.1200/JCO.2004.00.8631. PMID: 16446343
Cheung NK, Kushner BH, LaQuaglia MP, Kramer K, Ambros P, Ambros I, Ladanyi M, Eddy J, Bonilla MA, Gerald W
Eur J Cancer 1997 Oct;33(12):2117-20. doi: 10.1016/s0959-8049(97)00281-5. PMID: 9516865

Supplemental Content

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