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Unilateral retinoblastoma

MedGen UID:
208929
Concept ID:
C0854915
Neoplastic Process
Synonyms: Unilateral Retinoblastoma; unilateral retinoblastoma
 
Monarch Initiative: MONDO:0003076

Definition

A retinoblastoma that only involves a single eye. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVUnilateral retinoblastoma

Professional guidelines

PubMed

Arazi M, Baum A, Casavilca-Zambrano S, Alarcon-Leon S, Diaz-Coronado R, Ahmad A, Mushtaq A, Hussain M, Ushakova T, Yuri S, Vladimir P, Shields CL, Eagle RC Jr, Berry JL, Pike S, Brown B, Roy SR, Huque F, Fabian I, Frenkel S, Eiger-Moscovich M, Pe'er J, Hubbard GB 3rd, Olson TA, Grossniklaus H, Reddy MA, Sagoo MS, Staffieri SE, Elder JE, McKenzie JD, Tanabe M, Kaliki S, Fabian ID
Am J Ophthalmol 2024 Dec;268:399-408. Epub 2024 Sep 25 doi: 10.1016/j.ajo.2024.09.023. PMID: 39332513
Lee YJ, Kim JH, Lee SY, Jo DH
Exp Eye Res 2024 Nov;248:110102. Epub 2024 Sep 18 doi: 10.1016/j.exer.2024.110102. PMID: 39303840
Shields CL, Lally SE, Leahey AM, Jabbour PM, Caywood EH, Schwendeman R, Shields JA
Curr Opin Ophthalmol 2014 Sep;25(5):374-85. doi: 10.1097/ICU.0000000000000091. PMID: 25014750

Recent clinical studies

Etiology

Ye H, Xue K, Zhang P, Chen R, Zhai X, Ling L, Xiao W, Tang L, Wang H, Mao Y, Ai S, Bi Y, Liu Q, Zou Y, Qian J, Yang H
JAMA 2024 Nov 19;332(19):1634-1641. doi: 10.1001/jama.2024.19981. PMID: 39432296Free PMC Article
Shields CL, Bas Z, Laiton A, Silva AMV, Sheikh A, Lally SE, Shields JA
Eye (Lond) 2023 Apr;37(5):815-822. Epub 2022 Feb 25 doi: 10.1038/s41433-022-01980-0. PMID: 35217824Free PMC Article
Thompson S, Ritz B, Cockburn M, Heck JE
Int J Hyg Environ Health 2022 Aug;245:114025. Epub 2022 Aug 26 doi: 10.1016/j.ijheh.2022.114025. PMID: 36037576Free PMC Article
Zhou C, Wen X, Ding Y, Ding J, Jin M, Liu Z, Wang S, Han M, Yuan H, Xiao Y, Wu L, Wang J, Li Y, Yu J, Wen Y, Ye J, Liu R, Chen Z, Xue S, Lu W, Liao H, Cui J, Zhu D, Lu F, Tang S, Wu Y, Yangkyi T, Zhang G, Wubuli M, Guo H, Wang X, He Y, Sheng X, Wang Q, Luo Y, Fan J, Qi J, Yu Z, Tan J, Liang J, Sun X, Jin L, Yang X, Zhang J, Ji X, Zhao J, Jia R, Fan X
Ophthalmology 2022 Feb;129(2):209-219. Epub 2021 Sep 15 doi: 10.1016/j.ophtha.2021.09.002. PMID: 34536465
El Zomor H, Nour R, Saad A, Taha H, Shelil AE, Aleieldin A, Saad Zaghloul M, Alfaar AS
Eye (Lond) 2021 Sep;35(9):2564-2572. Epub 2020 Nov 13 doi: 10.1038/s41433-020-01275-2. PMID: 33188294Free PMC Article

Diagnosis

Arazi M, Baum A, Casavilca-Zambrano S, Alarcon-Leon S, Diaz-Coronado R, Ahmad A, Mushtaq A, Hussain M, Ushakova T, Yuri S, Vladimir P, Shields CL, Eagle RC Jr, Berry JL, Pike S, Brown B, Roy SR, Huque F, Fabian I, Frenkel S, Eiger-Moscovich M, Pe'er J, Hubbard GB 3rd, Olson TA, Grossniklaus H, Reddy MA, Sagoo MS, Staffieri SE, Elder JE, McKenzie JD, Tanabe M, Kaliki S, Fabian ID
Am J Ophthalmol 2024 Dec;268:399-408. Epub 2024 Sep 25 doi: 10.1016/j.ajo.2024.09.023. PMID: 39332513
Shields CL, Bas Z, Laiton A, Silva AMV, Sheikh A, Lally SE, Shields JA
Eye (Lond) 2023 Apr;37(5):815-822. Epub 2022 Feb 25 doi: 10.1038/s41433-022-01980-0. PMID: 35217824Free PMC Article
Zhou C, Wen X, Ding Y, Ding J, Jin M, Liu Z, Wang S, Han M, Yuan H, Xiao Y, Wu L, Wang J, Li Y, Yu J, Wen Y, Ye J, Liu R, Chen Z, Xue S, Lu W, Liao H, Cui J, Zhu D, Lu F, Tang S, Wu Y, Yangkyi T, Zhang G, Wubuli M, Guo H, Wang X, He Y, Sheng X, Wang Q, Luo Y, Fan J, Qi J, Yu Z, Tan J, Liang J, Sun X, Jin L, Yang X, Zhang J, Ji X, Zhao J, Jia R, Fan X
Ophthalmology 2022 Feb;129(2):209-219. Epub 2021 Sep 15 doi: 10.1016/j.ophtha.2021.09.002. PMID: 34536465
Wagner RS
J Pediatr Ophthalmol Strabismus 2021 Nov-Dec;58(6):344. Epub 2021 Nov 1 doi: 10.3928/01913913-20211012-01. PMID: 34851786
Limn YS, Juraida E, Alagaratnam J, Menon BS
Med J Malaysia 2011 Jun;66(2):156-7. PMID: 22106703

Therapy

Ye H, Xue K, Zhang P, Chen R, Zhai X, Ling L, Xiao W, Tang L, Wang H, Mao Y, Ai S, Bi Y, Liu Q, Zou Y, Qian J, Yang H
JAMA 2024 Nov 19;332(19):1634-1641. doi: 10.1001/jama.2024.19981. PMID: 39432296Free PMC Article
Thompson S, Ritz B, Cockburn M, Heck JE
Int J Hyg Environ Health 2022 Aug;245:114025. Epub 2022 Aug 26 doi: 10.1016/j.ijheh.2022.114025. PMID: 36037576Free PMC Article
Zhou C, Wen X, Ding Y, Ding J, Jin M, Liu Z, Wang S, Han M, Yuan H, Xiao Y, Wu L, Wang J, Li Y, Yu J, Wen Y, Ye J, Liu R, Chen Z, Xue S, Lu W, Liao H, Cui J, Zhu D, Lu F, Tang S, Wu Y, Yangkyi T, Zhang G, Wubuli M, Guo H, Wang X, He Y, Sheng X, Wang Q, Luo Y, Fan J, Qi J, Yu Z, Tan J, Liang J, Sun X, Jin L, Yang X, Zhang J, Ji X, Zhao J, Jia R, Fan X
Ophthalmology 2022 Feb;129(2):209-219. Epub 2021 Sep 15 doi: 10.1016/j.ophtha.2021.09.002. PMID: 34536465
El Zomor H, Nour R, Saad A, Taha H, Shelil AE, Aleieldin A, Saad Zaghloul M, Alfaar AS
Eye (Lond) 2021 Sep;35(9):2564-2572. Epub 2020 Nov 13 doi: 10.1038/s41433-020-01275-2. PMID: 33188294Free PMC Article
Shields CL, Fulco EM, Arias JD, Alarcon C, Pellegrini M, Rishi P, Kaliki S, Bianciotto CG, Shields JA
Eye (Lond) 2013 Feb;27(2):253-64. Epub 2012 Sep 21 doi: 10.1038/eye.2012.175. PMID: 22995941Free PMC Article

Prognosis

Arazi M, Baum A, Casavilca-Zambrano S, Alarcon-Leon S, Diaz-Coronado R, Ahmad A, Mushtaq A, Hussain M, Ushakova T, Yuri S, Vladimir P, Shields CL, Eagle RC Jr, Berry JL, Pike S, Brown B, Roy SR, Huque F, Fabian I, Frenkel S, Eiger-Moscovich M, Pe'er J, Hubbard GB 3rd, Olson TA, Grossniklaus H, Reddy MA, Sagoo MS, Staffieri SE, Elder JE, McKenzie JD, Tanabe M, Kaliki S, Fabian ID
Am J Ophthalmol 2024 Dec;268:399-408. Epub 2024 Sep 25 doi: 10.1016/j.ajo.2024.09.023. PMID: 39332513
Atima MO, Idakwo U, Komolafe O, Eisuke S, Shintaro N, Balogun EO, Dingwoke EJ, Orugun AJ, Ukumobe KO, Pam JD, Aladiuba A
BMC Pediatr 2023 Oct 28;23(1):538. doi: 10.1186/s12887-023-04347-w. PMID: 37891551Free PMC Article
Zhou C, Wen X, Ding Y, Ding J, Jin M, Liu Z, Wang S, Han M, Yuan H, Xiao Y, Wu L, Wang J, Li Y, Yu J, Wen Y, Ye J, Liu R, Chen Z, Xue S, Lu W, Liao H, Cui J, Zhu D, Lu F, Tang S, Wu Y, Yangkyi T, Zhang G, Wubuli M, Guo H, Wang X, He Y, Sheng X, Wang Q, Luo Y, Fan J, Qi J, Yu Z, Tan J, Liang J, Sun X, Jin L, Yang X, Zhang J, Ji X, Zhao J, Jia R, Fan X
Ophthalmology 2022 Feb;129(2):209-219. Epub 2021 Sep 15 doi: 10.1016/j.ophtha.2021.09.002. PMID: 34536465
El Zomor H, Nour R, Saad A, Taha H, Shelil AE, Aleieldin A, Saad Zaghloul M, Alfaar AS
Eye (Lond) 2021 Sep;35(9):2564-2572. Epub 2020 Nov 13 doi: 10.1038/s41433-020-01275-2. PMID: 33188294Free PMC Article
Limn YS, Juraida E, Alagaratnam J, Menon BS
Med J Malaysia 2011 Jun;66(2):156-7. PMID: 22106703

Clinical prediction guides

Ye H, Xue K, Zhang P, Chen R, Zhai X, Ling L, Xiao W, Tang L, Wang H, Mao Y, Ai S, Bi Y, Liu Q, Zou Y, Qian J, Yang H
JAMA 2024 Nov 19;332(19):1634-1641. doi: 10.1001/jama.2024.19981. PMID: 39432296Free PMC Article
Atima MO, Idakwo U, Komolafe O, Eisuke S, Shintaro N, Balogun EO, Dingwoke EJ, Orugun AJ, Ukumobe KO, Pam JD, Aladiuba A
BMC Pediatr 2023 Oct 28;23(1):538. doi: 10.1186/s12887-023-04347-w. PMID: 37891551Free PMC Article
Fang X, Chen J, Wang Y, Zhao M, Zhang X, Yang L, Ni X, Zhao J, Gallie BL
Ophthalmic Genet 2021 Oct;42(5):593-599. Epub 2021 Jun 30 doi: 10.1080/13816810.2021.1946703. PMID: 34190019
Soliman SE, Dimaras H, Souka AA, Ashry MH, Gallie BL
J Fr Ophtalmol 2015 Jun;38(6):550-8. Epub 2015 May 14 doi: 10.1016/j.jfo.2015.03.003. PMID: 25982424
Lombardi C, Ganguly A, Bunin GR, Azary S, Alfonso V, Ritz B, Heck JE
Cancer Causes Control 2015 Mar;26(3):387-97. Epub 2014 Dec 27 doi: 10.1007/s10552-014-0514-z. PMID: 25542139Free PMC Article

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