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Paratesticular Rhabdomyosarcoma

MedGen UID:
1695863
Concept ID:
C5206600
Neoplastic Process

Definition

A rhabdomyosarcoma that arises from the paratesticular region. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVParatesticular Rhabdomyosarcoma

Professional guidelines

PubMed

Rogers TN, Seitz G, Fuchs J, Martelli H, Dasgupta R, Routh JC, Hawkins DS, Koscielniak E, Bisogno G, Rodeberg DA
Pediatr Blood Cancer 2021 Apr;68(4):e28938. Epub 2021 Feb 1 doi: 10.1002/pbc.28938. PMID: 33522706Free PMC Article
Hughes LL, Baruzzi MJ, Ribeiro RC, Ayers GD, Rao B, Parham DM, Pratt CB, Kun LE
Cancer 1994 Jan 15;73(2):476-82. doi: 10.1002/1097-0142(19940115)73:2<476::aid-cncr2820730237>3.0.co;2-n. PMID: 8293416
Olive D, Flamant F, Zucker JM, Voute P, Brunat-Mentigny M, Otten J, Dutou L
Cancer 1984 Oct 1;54(7):1283-7. doi: 10.1002/1097-0142(19841001)54:7<1283::aid-cncr2820540709>3.0.co;2-j. PMID: 6467153

Recent clinical studies

Etiology

Rhee DS, Rodeberg DA, Baertschiger RM, Aldrink JH, Lautz TB, Grant C, Meyers RL, Tracy ET, Christison-Lagay ER, Glick RD, Mattei P, Dasgupta R; American Pediatric Surgical Association Cancer Committee
J Pediatr Surg 2020 Oct;55(10):1987-1995. Epub 2020 Jun 18 doi: 10.1016/j.jpedsurg.2020.06.015. PMID: 32674846
Hammond WJ, Farber BA, Price AP, Wolden SL, Heaton TE, Wexler LH, La Quaglia MP
J Pediatr Surg 2017 Feb;52(2):304-308. Epub 2016 Nov 14 doi: 10.1016/j.jpedsurg.2016.11.027. PMID: 27894767Free PMC Article
Dangle PP, Correa A, Tennyson L, Gayed B, Reyes-Múgica M, Ost M
Urol Oncol 2016 Feb;34(2):84-92. Epub 2015 Nov 11 doi: 10.1016/j.urolonc.2015.10.004. PMID: 26572723
Merguerian PA, Chang B
Curr Opin Oncol 2002 May;14(3):273-9. doi: 10.1097/00001622-200205000-00004. PMID: 11981271
de Vries JD
World J Urol 1995;13(4):219-25. doi: 10.1007/BF00182966. PMID: 8528295

Diagnosis

Rhee DS, Rodeberg DA, Baertschiger RM, Aldrink JH, Lautz TB, Grant C, Meyers RL, Tracy ET, Christison-Lagay ER, Glick RD, Mattei P, Dasgupta R; American Pediatric Surgical Association Cancer Committee
J Pediatr Surg 2020 Oct;55(10):1987-1995. Epub 2020 Jun 18 doi: 10.1016/j.jpedsurg.2020.06.015. PMID: 32674846
Hammond WJ, Farber BA, Price AP, Wolden SL, Heaton TE, Wexler LH, La Quaglia MP
J Pediatr Surg 2017 Feb;52(2):304-308. Epub 2016 Nov 14 doi: 10.1016/j.jpedsurg.2016.11.027. PMID: 27894767Free PMC Article
Merguerian PA, Chang B
Curr Opin Oncol 2002 May;14(3):273-9. doi: 10.1097/00001622-200205000-00004. PMID: 11981271
de Vries JD
World J Urol 1995;13(4):219-25. doi: 10.1007/BF00182966. PMID: 8528295
Raney RB Jr, Hays DM, Lawrence W Jr, Soule EH, Tefft M, Donaldson MH
Cancer 1978 Aug;42(2):729-36. doi: 10.1002/1097-0142(197808)42:2<729::aid-cncr2820420246>3.0.co;2-r. PMID: 354776

Therapy

Merguerian PA, Chang B
Curr Opin Oncol 2002 May;14(3):273-9. doi: 10.1097/00001622-200205000-00004. PMID: 11981271
Hughes LL, Baruzzi MJ, Ribeiro RC, Ayers GD, Rao B, Parham DM, Pratt CB, Kun LE
Cancer 1994 Jan 15;73(2):476-82. doi: 10.1002/1097-0142(19940115)73:2<476::aid-cncr2820730237>3.0.co;2-n. PMID: 8293416
Blyth B, Mandell J, Bauer SB, Colodny AH, Grier HE, Weinstein HJ, Tarbell NJ, Hendren WH, Retik AB
J Urol 1990 Dec;144(6):1450-3. doi: 10.1016/s0022-5347(17)39764-1. PMID: 2122010
Quesada EM, Diez B, Silva M, Muriel FS, Chemes H
J Urol 1986 Jul;136(1 Pt 2):303-4. doi: 10.1016/s0022-5347(17)44849-x. PMID: 3723682
Raney RB Jr, Hays DM, Lawrence W Jr, Soule EH, Tefft M, Donaldson MH
Cancer 1978 Aug;42(2):729-36. doi: 10.1002/1097-0142(197808)42:2<729::aid-cncr2820420246>3.0.co;2-r. PMID: 354776

Prognosis

Quiroz YY, Moncada E, Llorens E, Schwartzmann I, Caffarati J, Bujons A
J Pediatr Urol 2022 Jun;18(3):401-403. Epub 2022 Mar 3 doi: 10.1016/j.jpurol.2022.02.027. PMID: 35410803
Rhee DS, Rodeberg DA, Baertschiger RM, Aldrink JH, Lautz TB, Grant C, Meyers RL, Tracy ET, Christison-Lagay ER, Glick RD, Mattei P, Dasgupta R; American Pediatric Surgical Association Cancer Committee
J Pediatr Surg 2020 Oct;55(10):1987-1995. Epub 2020 Jun 18 doi: 10.1016/j.jpedsurg.2020.06.015. PMID: 32674846
Merguerian PA, Chang B
Curr Opin Oncol 2002 May;14(3):273-9. doi: 10.1097/00001622-200205000-00004. PMID: 11981271
de Vries JD
World J Urol 1995;13(4):219-25. doi: 10.1007/BF00182966. PMID: 8528295
Raney RB Jr, Hays DM, Lawrence W Jr, Soule EH, Tefft M, Donaldson MH
Cancer 1978 Aug;42(2):729-36. doi: 10.1002/1097-0142(197808)42:2<729::aid-cncr2820420246>3.0.co;2-r. PMID: 354776

Clinical prediction guides

Lachi PK, Armugham N, Triveni B, Sheela B, Krishna MR
J Cancer Res Ther 2021 Apr-Jun;17(2):590-592. doi: 10.4103/jcrt.JCRT_585_15. PMID: 34121716
Hammond WJ, Farber BA, Price AP, Wolden SL, Heaton TE, Wexler LH, La Quaglia MP
J Pediatr Surg 2017 Feb;52(2):304-308. Epub 2016 Nov 14 doi: 10.1016/j.jpedsurg.2016.11.027. PMID: 27894767Free PMC Article
Tröbs RB, Krauss M, Geyer C, Tannapfel A, Körholz D, Hirsch W
Klin Padiatr 2007 May-Jun;219(3):146-51. doi: 10.1055/s-2007-973847. PMID: 17525908
Merguerian PA, Chang B
Curr Opin Oncol 2002 May;14(3):273-9. doi: 10.1097/00001622-200205000-00004. PMID: 11981271
Ferrari A, Bisogno G, Casanova M, Meazza C, Piva L, Cecchetto G, Zanetti I, Pilz T, Mattke A, Treuner J, Carli M
J Clin Oncol 2002 Jan 15;20(2):449-55. doi: 10.1200/JCO.2002.20.2.449. PMID: 11786573

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