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Central Nervous System Epithelioid Hemangioendothelioma

MedGen UID:
1386444
•Concept ID:
C4329630
•
Neoplastic Process

Definition

A low-grade malignant blood vessel neoplasm that arises from the central nervous system. It is characterized by the presence of epithelioid endothelial cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCentral Nervous System Epithelioid Hemangioendothelioma

Recent clinical studies

Etiology

PRIMARY EPITHELIOID HEMANGIOENDOTHELIOMA IN THE CEREBELLUM: CASE REPORT WITH REFERENCE TO DRASTIC CHANGE IN THE WHO CLASSIFICATION.
Omerhodžić I, Bilalović N, Rovčanin B, Imširović B, Suljić E, Rotim A, Arnautović K
Acta Clin Croat 2018 Sep;57(3):570-576. doi: 10.20471/acc.2018.57.03.21. PMID: 31168191Free PMC Article
Epithelioid hemangioendothelioma of the central nervous system. Immunohistochemical and ultrastructural observations of a pediatric case.
Taratuto AL, Zurbriggen G, Sevlever G, Saccoliti M
Pediatr Neurosci 1988;14(1):11-4. doi: 10.1159/000120355. PMID: 3217280

Diagnosis

Pulmonary epitheloid hemangioendothelioma PET CT findings and review of literature.
Nizami I, Mohammed S, Abouzied Mel D
Ann Saudi Med 2014 Sep-Oct;34(5):447-9. doi: 10.5144/0256-4947.2014.447. PMID: 25827705Free PMC Article
Epithelioid hemangioendothelioma of the suprasellar area: a case report and review of the literature.
Baehring JM, Dickey PS, Bannykh SI
Arch Pathol Lab Med 2004 Nov;128(11):1289-93. doi: 10.5858/2004-128-1289-EHOTSA. PMID: 15504067
Epithelioid hemangioendothelioma of the infundibular-hypothalamic region: case report and literature review.
Hamlat A, Casallo-Quilliano C, Saikali S, Lesimple T, Brassier G
J Neurooncol 2004 May;67(3):361-6. doi: 10.1023/b:neon.0000024240.97378.d0. PMID: 15164993
Central nervous system metastases of a pulmonary epitheloid haemangioendothelioma.
Díaz R, Segura A, Calderero V, Cervera I, Aparicio J, Jordá MV, Pellín L
Eur Respir J 2004 Mar;23(3):483-6. doi: 10.1183/09031936.04.00060104. PMID: 15065842
Primary epithelioid hemangioendothelioma of the brain.
Nora FE, Scheithauer BW
Am J Surg Pathol 1996 Jun;20(6):707-14. doi: 10.1097/00000478-199606000-00008. PMID: 8651350

Therapy

Localized bacillary angiomatosis in the oral cavity: observations about a neoplasm with atypical behavior. Description of a case and review of the literature.
Tucci E, Della Rocca C, Santilli F
Minerva Stomatol 2006 Jan-Feb;55(1-2):67-75. PMID: 16495874

Prognosis

Epithelioid hemangioendothelioma of the craniocervical junction; case report and review.
Ofluoglu AE, Aydogan M, Erdogan U, Ofluoglu O
Acta Orthop Traumatol Turc 2017 Jul;51(4):342-346. Epub 2017 May 3 doi: 10.1016/j.aott.2017.03.012. PMID: 28478911Free PMC Article
Pulmonary epitheloid hemangioendothelioma PET CT findings and review of literature.
Nizami I, Mohammed S, Abouzied Mel D
Ann Saudi Med 2014 Sep-Oct;34(5):447-9. doi: 10.5144/0256-4947.2014.447. PMID: 25827705Free PMC Article
Epithelioid hemangioendothelioma of the infundibular-hypothalamic region: case report and literature review.
Hamlat A, Casallo-Quilliano C, Saikali S, Lesimple T, Brassier G
J Neurooncol 2004 May;67(3):361-6. doi: 10.1023/b:neon.0000024240.97378.d0. PMID: 15164993
Central nervous system metastases of a pulmonary epitheloid haemangioendothelioma.
Díaz R, Segura A, Calderero V, Cervera I, Aparicio J, Jordá MV, Pellín L
Eur Respir J 2004 Mar;23(3):483-6. doi: 10.1183/09031936.04.00060104. PMID: 15065842
Primary epithelioid hemangioendothelioma of the brain.
Nora FE, Scheithauer BW
Am J Surg Pathol 1996 Jun;20(6):707-14. doi: 10.1097/00000478-199606000-00008. PMID: 8651350

Clinical prediction guides

Localized bacillary angiomatosis in the oral cavity: observations about a neoplasm with atypical behavior. Description of a case and review of the literature.
Tucci E, Della Rocca C, Santilli F
Minerva Stomatol 2006 Jan-Feb;55(1-2):67-75. PMID: 16495874
Epithelioid hemangioendothelioma of the central nervous system. Immunohistochemical and ultrastructural observations of a pediatric case.
Taratuto AL, Zurbriggen G, Sevlever G, Saccoliti M
Pediatr Neurosci 1988;14(1):11-4. doi: 10.1159/000120355. PMID: 3217280

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