3SC0,5UJC


Conserved Protein Domain Family
MMACHC

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pfam16690: MMACHC (This model is not part of the current CDD release)
Methylmalonic aciduria and homocystinuria type C family
Statistics
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PSSM-Id: 522497
Aligned: 23 rows
Threshold Bit Score: 319.195
Created: 17-Feb-2025
Updated: 28-Apr-2025
Structure
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Program:
Drawing:
Aligned Rows:
PubMed ReferencesClick to see Conserved Features Help

Sequence Alignment
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Format: Row Display: Color Bits: Type Selection:
3SC0_A        23 GfevypfQVAWYNELL--PPAFHLPLPGPTLAFLVLSTPAMFDRALKPFL----------------------QS-CHLRM 77  human
1_pfamImport   1 K------QIGSYNSVV--SSDFTLDYPSHSLAVLILSTPKMFDVAYKRWV----------------------REeTSKAG 50 
XP_011405503  24 GleahpfKIQWYNDKV--SDSFKLPYNGDTLAVLIISAPKMFEELLKPFIlggkykre------gfnalkdeENeRKEEG 95 
5_pfamImport   1 GmetylfKVGWYNDTV--IPSFKLPYDNDTLCAVILTIPSFFENAFLPNL----------------------STfFSQSD 56 
Q7Z144        24 GfeshmfKIGSYNEAVgeSSPFALPYDDSTMALLILSTPDMFDVAFRKWV----------------------VQkTMDFG 81  Caenorhabditis ...
XP_032236147  29 gleaypfKIGWYNNQVt-HKQFQFPFDPDTLAFVIISTPEMFEKGFKPFI----------------------TD-ADCLG 84 
XP_002115419  20 GfecapfKISWYNDQV--DDHFKLKCNQNALAFIIISLPQMFDKTFKTFImkkynidnfpledkaewneeekEEfSYNQN 97 
EFX90307      19 GlechpfKVGWYNERV--KSGYQLEHHEDTLCFVVISSPSFFEKGFIPFV----------------------RNsTESNN 74 
XP_002404566  18 GieshpfKIQWYNDRV--PGAFKFQRHPDTLCFVSLSTPSTFEKAFLPFV----------------------LN-DRNLT 72 
XP_009009623  20 GleaypfKIGWYNDEV--HKSFHLEYDYDTLAFSLVSLPKMFDILFCPFL----------------------EQ-WDGKG 74 
3SC0_A        78 L--------TDPVDQCVAYHLGRVRESLpeLQ--IEIIADYEVHP-NRRPKILAQTAAHVAGAAYYYQRQDV----EADP 142 human
1_pfamImport  51 SfdafteemSSPISEFIDSRLEKVQEELssMP--FEIIHDHSMWP-NRKPKILMCTCGHVAGAAYYYRQSDP----TLSE 123
XP_011405503  96 G--------SDPLDQCFRDVFNKLQTHFsqYK--TTFIQDYELHH-NRRPKILLQTAGHVSGSAYYYQRGDV----PRAP 160
5_pfamImport  57 S--------KDPIDKCIAHHINSALSNLdiNG--VEVMYDYEILP-NRRPKVLVQTAAHVSGAAFYYQRHHCnskcLNDH 125
Q7Z144        82 SfdevcemvSSPIQSFLEDRLEIMSEKLrkVEenFEILHDYSMTP-QRRPKILMQTCGHVAGAAFYYQ--------PCHF 152 Caenorhabditis ...
XP_032236147  85 S--------RDPIDECMTAFFLKVKQAFpcHE--IDAIHDFELHP-NRRPKVLVQTAAHAAGAAYFYQRKDI----TDDP 149
XP_002115419  98 V--------YDPLDQCMLDYFQKIRNHFpdHQ--LHIIRDFEMDA-SHRPKVLVQTAGHVAGAVRYYQRCDV----HDDP 162
EFX90307      75 ---------QDYLDQAISSCLKTAIQSIsgYD--ISILHDYEMRPgTRRPKVLVQTAGHVSGAVYFYQKTDV----INPP 139
XP_002404566  73 L--------KDPFDQCMTACFARAIQAFpgES--VELLQDFELHP-NRRPKVIMQTAGHVSGAVHYYGCNDM----EITE 137
XP_009009623  75 G--------NDALDECMRFYLNKLKSNF--TD--VELIHDFEFHH-SKRPKVLVQTAGHVSGGVFYFQRKDIk---HSDP 138
3SC0_A       143 W-GNQ------------RISGVCIHPRFGGWFAIRGVVLLPGIEV-PD-LPPRKpHDCVPTRADRIALLEGFNFHWRDWT 207 human
1_pfamImport 124 TkDGKkwdpkp-aaanlKFIGLSLHSDFGGHFAFRSVLIFPHISL-PSsFKEREpVAVLHTIDEIKDALEKFNYAWKDSR 201
XP_011405503 161 WgEDK------------PIYGVSVHPRYGGWFAFRGVLIFEDIRVkGEeLEYKDpIDCVSKREKRIELLEEFNYHWEEWR 228
5_pfamImport 126 WdKNR------------RIYGVCIHPKYGGWFAIRAVLVFKDMKD-PD-LQIQPpTDCVKSRNDRIDLLERFNGNWKDWT 191
Q7Z144       153 QeDGVtwppagrmgpnlKFIGLSLHPIYGGHFAFRSVLIFPNVKI-PE-FCEKEpRPILTASEDVRTALEKFNYNWKDSG 230 Caenorhabditis ...
XP_032236147 150 WpPTQ------------RICGVCVHPKYGGWFAIRGVLIFKTFKY-PD-LPRKPpMDVVVGDEKRIELLEKFNFHWEDWS 215
XP_002115419 163 WdESQ------------RIYGTCVHPKYGGWFALRGVIIFEDVN--ANkLAQVDpPDMIKTDQDRIRLLNLYNFHWRDWS 228
EFX90307     140 WlTDQ------------PIYGVCLHPSYIGWFALRAVIIFQKVLV-PD-LVYKPpKDILVDETKKIELLNRYNNSWQDWS 205
XP_002404566 138 SpPNK------------KLLGVCIHPKYGGWFAFRGVFIFSDILV-PD-LEQRQpADVVQREDVRRDLLRLFNFSWQNGL 203
XP_009009623 139 WpENR------------KICGVCLHPKYGGWFGLRGILIFKNVKV-PN-LMKKE-LECFLSNEQIISLLDKFNNSWRDGT 203
3SC0_A       208 YRDAV---TPQERYSEEQKAYFSTPPAQRLALL 237 human
1_pfamImport 202 FRDCG---NPKERYSSTQMEYFGKPPSERWEVI 231
XP_011405503 229 YRDILdggDVEDRYSEEQKEYFGTLPKDRHKLV 261
5_pfamImport 192 YRDII---PVVEKYSELQKLYFITAPKERKH-- 219
Q7Z144       231 FRDFG---NPTRRYSTTQMEFFGRPVAERWEVL 260 Caenorhabditis elegans
XP_032236147 216 FRDVV---PSERKYSDQQIKYFSTLPVNRKDLL 245
XP_002115419 229 FRDVLp--GVVARYSDEQKTFFSTPPSQRPQIL 259
EFX90307     206 FRDIM---EPTERYSELQQKYLSTRPSERSHLI 235
XP_002404566 204 YRDVI---DVDERYSARQQEYFRTVPSQRWELI 233
XP_009009623 204 FRDVI---EPLERYSTLQQKYFNVTPDERLELI 233
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