Conserved Protein Domain Family
Mit_KHE1

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pfam10173: Mit_KHE1 (This model is not part of the current CDD release)
Mitochondrial K+-H+ exchange-related
The members of this family function as mitochondrial potassium-hydrogen exchange transporters. The family is part of a large mitochondrial KHE protein complex.
Statistics
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PSSM-Id: 519218
Aligned: 108 rows
Threshold Bit Score: 128.093
Created: 15-Feb-2025
Updated: 25-Apr-2025
Structure
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Aligned Rows:
PubMed ReferencesClick to see Conserved Features Help

Sequence Alignment
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Format: Row Display: Color Bits: Type Selection:
XP_060975336  60 VISLPITTK-QSFIYCNHRP-GI----LSKTQASKIEL----------------------------VTKIEAKLVNLATK 105
Q553P8         3 VFLFKIASKqRWTLYIEKSEfFSkkvdIEPTIVTTSSNnnnitl-----------------ptqskGVLILNKLKNIAIE 65  Dictyostelium d...
XP_005849796   7 VLLLPIFR--RHWLWH-----------AEGGAAAAAAAaadvqgkagqalrnwregrnleekvqllGQRANRWVQRRLWT 73 
CAG1849270     5 LVVFPIKG--RSWCFSRSAE------------SVSGADssstpppglrdlw--rrisshgrsaqesAEIVGDFIADKMNR 68 
KAH0749375     5 LVVFPIRG--RNWCFSRSIE------------SSQSEAqssntpstlkdlwkkissksshdspaanIEVVVDFASDKMNK 70 
XP_002533326   5 LVVFPVKG--RNWCFSRSIE------------PSVAEAasayapntlkelw---knisssnsnahnAELVIDFVSNKMNR 67 
XP_006369072   5 LVVFPVKG--RNWCFSRSID------------PSLEEAaashtpstlkhlw--kkissssnssaknVELVIDYASNKMDK 68 
XP_002264196   5 LVVFPIKG--RKWCFARSVD------------PAAADSqaahtpstlrdlw--nrissnpkplnanAELLLDFASNKMNK 68 
ERM99439       5 LVIFPIRG--RSWCFTKSID------------KVAQDSgfnpssltlkdlw--kritkneegvqgkAEIVTEFFSEKMNR 68 
NP_175779      5 LVVFPIKG--KKWCFSRSVD------------PFAAQSpsgvtpttvrglw--kkisseskpinanAELLVDFISDKMNK 68  thale cress
XP_060975336 106 GWNKLTTSKSK--INIKITHFIKQLLDTIPYKESCLRSFPnknamireineeslhlikptkksenenenenekenknknk 183
Q553P8        66 SKNEIDNAQDGvgLKGKLKSLLSYLESKIHPEEAVLQQFSkindnnlikkhnhhnh------------------------ 121 Dictyostelium d...
XP_005849796  74 EWHKLETASEGt-LRNRGYRMAQAVLAREDPRETFLKNLP---------------------------------------- 112
CAG1849270    69 AWTGLEKAPAGt-LKSKIHSLGLRLLSRVKPSEIFLKSVT---------------------------------------- 107
KAH0749375    71 AWTSLEKAPAGs-LKNRIHGLGLTLLSRVKPSEIFLKSIS---------------------------------------- 109
XP_002533326  68 AWVGLEKAPEGt-LKNKLHGLGLKLLSRVKPSEIFLKSIS---------------------------------------- 106
XP_006369072  69 AWMGLEKAPEGt-FKNKLHGLGLKLLSRVKPSEIFLKSIS---------------------------------------- 107
XP_002264196  69 AWVGLEKAPEGt-LKNKLYGLGLRLLARVKPSEIFLKSIS---------------------------------------- 107
ERM99439      69 AWLALGEAPDGs-FKHKIHGMGQLLLARVQPSEFFLKSIS---------------------------------------- 107
NP_175779     69 AWVGLEKAPDGs-IKNKIHGFGLKLLARVKPSEIFLKSIS---------------------------------------- 107 thale cress
XP_060975336 184 nknknkneiedgnviqskstgdtktdietaraseissqsaknegvnprptvIVQSEVQNLDIPTNQLKPIPLYHP-QFqS 262
Q553P8       122 ------------------------------------hnhihhnnnnnnnqnETVKHQFEHFNEQRDKASFTIYYPsNI-G 164 Dictyostelium d...
XP_005849796 113 ----------------------------------------------------------------SKPAPVEVIYPtAY-K 127
CAG1849270   108 ----------------------------------------------------------------KDITTVEITYPaNL-N 122
KAH0749375   110 ----------------------------------------------------------------KEVTRVDITYPsSL-N 124
XP_002533326 107 ----------------------------------------------------------------KEVTDVEIIYPsSL-N 121
XP_006369072 108 ----------------------------------------------------------------KEVSSVEITYPsSL-N 122
XP_002264196 108 ----------------------------------------------------------------KEVSKVHVAYPsSL-N 122
ERM99439     108 ----------------------------------------------------------------KDITEVEVTFPaSL-N 122
NP_175779    108 ----------------------------------------------------------------KEVTSVQVTYPpSL-D 122 thale cress
XP_060975336 263 PSTIREELQEFRDHGLEHEKKWAIICAIGIPITLPFALVPVvPNVPGFYVAYRLYCHIKALYGIRNLDYLL 333
Q553P8       165 YRRANRFSQVLMRQKIRFHQKWMIINSLLIPITFAATILPG-PNIFLAYNLYRLYGHFQALKGCTNLSRYT 234 Dictyostelium discoideum...
XP_005849796 128 ERMVRRQLRHVAADGRRRHTMRLVWWMLAMVPQLPLMLTPL-PNITVYYTGYRIYSHFRALQGTKALEQNL 197
CAG1849270   123 PRFVRRRLRHMAMWGSAVHRNYFYGSISLLPLTSVLSVLPL-PNIPFFWILFRTYSHWRALKGSERLMLLV 192
KAH0749375   125 GQLVRRRLRHIASRGAIIHKKYLYGSATLLPLTSFFMVLPL-PNIPFFWVLFRTYSHWRALQGSENLLRLV 194
XP_002533326 122 PRLVRRRLRHVALSGSAIHKKYFYSSVSLLPLTSAFMVLPL-PNIPFFWVLFRAYSHWRALQGSEKLLELV 191
XP_006369072 123 ARLVRRRLRHIAMRGAAIHKKYFYGSVMLLPLSSALAVLPL-PNIPFFWFLFRSYSNWRALKGSEKLLQLV 192
XP_002264196 123 ARLVRRRLRHVALRGNFIHKKYFYGSVSLLPFTFAFSVLPL-PNIPFFWISFRTYSHWQALQGSERLLRLV 192
ERM99439     123 PRLVRRRLRHVAMRGSIYHRRFFYGSMSLLPFTTALAVLPL-PNIPFFWILFRAYSHWRACQGSERLLLLa 192
NP_175779    123 PRLVRRRLRHIAMSGTILHKKYLVGSVTLLPLTSAFMVLPL-PNIPFFWVLFRTYSHWRALQGSEKLLKLI 192 thale cress
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