1M3D,1M3D,6MPX,8TYS,8TYS,8TYS,8TYS


Conserved Protein Domain Family
C4

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pfam01413: C4 (This model is not part of the current CDD release)
C-terminal tandem repeated domain in type 4 procollagen
Duplicated domain in C-terminus of type 4 collagens. Mutations in alpha-5 collagen IV are associated with X-linked Alport syndrome.
Statistics
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PSSM-Id: 514248
Aligned: 85 rows
Threshold Bit Score: 136.931
Created: 13-Feb-2025
Updated: 28-Apr-2025
Structure
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Program:
Drawing:
Aligned Rows:
PubMed ReferencesClick to see Conserved Features Help

Sequence Alignment
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Format: Row Display: Color Bits: Type Selection:
1M3D_A           6 FLVTRHSQTTDDPQCPPGTKILYHGYSLLYVQGNE-RAHGQDLGTAGSCLRKFSTMPFLFCNIN-NVCNFASrNDYSYWL 83   domestic cattle
XP_040026384  1548 NVIAVHSQTTLTPECPQNWESLWTGYSFVMQTGAGaEGSSQPLVSPGSCLESFRQVPFIECHGr-GTCNYYP-DSYSYWL 1625
47_pfamImport    1 NVIAVHSQTISVPDCPSGWEPLWQGYSFVMQTGVGaEGSGQPLSSPGSCLENFQKVPFIECHGR-GTCSFYT-DSYSYWL 78  
32_pfamImport    1 TVIAIHSQTSMIPTCPTNWVSLWTGYSFVMETGAGaEGSGQPLASPGSCLEHFRKLPFIECHER-GTCNFYT-NSYSYWL 78  
XP_009025072   620 QPIAIHSQATSVPDCPRGWSNIWSGFSLALMTGEGgLGVGQTLHSPGSCLTTFRSSPVFECHGd-GKCNHYA-NHISYFL 697 
XP_009015091  1363 IAMAIHSQTRNVPDCPPGWSSLWIGYSFFMQA-AGrSGTGQQLSSTGSCLEDFRTTPFIECSTErGSCHYYP-DKVSFWL 1440
XP_009012334  1662 NVLTVHSQDITEPRCPLGWKALWVGYSFFMHIVHGvSGGGQQLVSSGSCLEDFRVLPFIECVe--GKCQFPM-NDMSYWM 1738
XP_002116296  1399 PVAAFHSQTSTAPSCPNGWQQLWEGYSYIMQTGTGnQGSGQQLQSPGSCLRNFRSQPFIECNSr-GTCINTV-GGLSFWM 1476
XP_002116198   175 NSIALHSQSQTPPSCPSGYELLWQGYSYWMHTGQGkSVAGQDLSSPGSCLRRFQSMPFIECDGPsGSCFFYS-NSKSFWV 253 
XP_011615542  1554 NVIAIHSQTSVVPDCPLGWLPLWVGYSFVMETGVGaEGSGQPLASPGSCLEQFRKIPFIECHGr-GTCNYYT-DSYSYWL 1631 torafugu
1M3D_A          84 S-TPEPM----PMSMAPITGENIRPFISRCAVCEA 113  domestic cattle
XP_040026384  1626 AsLDPRSmfsnPVPQTVKGPS-LQSVISRCRVCRK 1659
47_pfamImport   79 AaLDPTLmfskPNPKTLKDDC-QQRIISRCRVCMK 112 
32_pfamImport   79 AaLNPSNmfsrPQL-WRDSGLLPGNRISRCRVCMN 112 
XP_009025072   698 SvLDRFNqyskPMSDTYKAAN-LMNKISRCSVCLA 731 
XP_009015091  1441 SaFEPYEqfekPQHNKYQGGN-LRDYVSRCHVCAK 1474
XP_009012334  1739 TtVDVNSqfltPNSRTLKAGS-LRSVISRCSVCSR 1772
XP_002116296  1477 KaINASQqfdpPTQQVLSASA-TSSEISRCIVCKK 1510
XP_002116198   254 TaVNVTDqfepPTATVLNFNDNPQSYISRCSVCLR 288 
XP_011615542  1632 AaLSPHDmfskPKPHTDTGEF-PGSLISRCRVCMK 1665 torafugu
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