PubMed

Codistribution of amyloid beta plaques and spongiform degeneration in familial Creutzfeldt-Jakob disease with the E200K-129M haplotype.

Ghoshal N, Cali I, Perrin RJ, Josephson SA, Sun N, Gambetti P, Morris JC.

Arch Neurol. 2009 Oct;66(10):1240-6.PMID: 19822779 [PubMed - indexed for MEDLINE]Related articles

Localization of disease-related PrP in Danish patients with different subtypes of prion disease.

Bergström AL, Heegaard PM, Dyrbye H, Lind P, Laursen H.

Clin Neuropathol. 2009 Sep-Oct;28(5):321-32.PMID: 19788047 [PubMed - indexed for MEDLINE]Related articles

Spontaneous generation of prion infectivity in fatal familial insomnia knockin mice.

Jackson WS, Borkowski AW, Faas H, Steele AD, King OD, Watson N, Jasanoff A, Lindquist S.

Neuron. 2009 Aug 27;63(4):438-50.PMID: 19709627 [PubMed - indexed for MEDLINE]Related articles

Survey of public perceptions of prion disease risks in Canada: what does the public care about?

Lemyre L, Gibson S, Markon MP, Lee JE, Brazeau I, Carroll A, Boutette P, Krewski D.

J Toxicol Environ Health A. 2009;72(17):1113-21.PMID: 19697248 [PubMed - indexed for MEDLINE]Related articles

International case studies of psychosocial ripple effects of bovine spongiform encephalopathy (BSE) in European countries.

Lemyre L, Boutette P, Karyakina N, Markon MP, Brazeau I, Krewski D.

J Toxicol Environ Health A. 2009;72(17):1092-5.PMID: 19697245 [PubMed - indexed for MEDLINE]Related articles

Different prion conformers target the olfactory pathway in sporadic Creutzfeldt-Jakob disease.

Zanusso G, Ferrari S, Benedetti D, Sbriccoli M, Rizzuto N, Monaco S.

Ann N Y Acad Sci. 2009 Jul;1170:637-43.PMID: 19686205 [PubMed - indexed for MEDLINE]Related articles

A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP.

Yang W, Cook J, Rassbach B, Lemus A, DeArmond SJ, Mastrianni JA.

J Neurosci. 2009 Aug 12;29(32):10072-80.PMID: 19675240 [PubMed - indexed for MEDLINE]Related articles

Therapeutic interventions ameliorating prion disease.

Brazier MW, Wall VA, Brazier BW, Masters CL, Collins SJ.

Expert Rev Anti Infect Ther. 2009 Feb;7(1):83-105. Review.PMID: 19622059 [PubMed - indexed for MEDLINE]Related articles

An atypical case of sporadic fatal insomnia.

Priano L, Giaccone G, Mangieri M, Albani G, Limido L, Brioschi A, Pradotto L, Orsi L, Mortara P, Fociani P, Mauro A, Tagliavini F.

J Neurol Neurosurg Psychiatry. 2009 Aug;80(8):924-7.PMID: 19608785 [PubMed - indexed for MEDLINE]Related articles

Prion infectivity in fat of deer with chronic wasting disease.

Race B, Meade-White K, Race R, Chesebro B.

J Virol. 2009 Sep;83(18):9608-10. Epub 2009 Jul 1.PMID: 19570855 [PubMed - indexed for MEDLINE]Related articles

Selective processing and metabolism of disease-causing mutant prion proteins.

Ashok A, Hegde RS.

PLoS Pathog. 2009 Jun;5(6):e1000479. Epub 2009 Jun 19.PMID: 19543376 [PubMed - indexed for MEDLINE]Related articlesFree article

Prion topology and toxicity.

Aguzzi A, Steele AD.

Cell. 2009 Jun 12;137(6):994-6.PMID: 19524502 [PubMed - indexed for MEDLINE]Related articles

De novo generation of infectious prions in vitro produces a new disease phenotype.

Barria MA, Mukherjee A, Gonzalez-Romero D, Morales R, Soto C.

PLoS Pathog. 2009 May;5(5):e1000421. Epub 2009 May 15.PMID: 19436715 [PubMed - indexed for MEDLINE]Related articlesFree article

Broadening spectrum of bovine spongiform encephalopathies.

Füzi M, Horváth P.

Acta Microbiol Immunol Hung. 2009 Mar;56(1):53-60.PMID: 19388556 [PubMed - indexed for MEDLINE]Related articles

Early onset prion disease from octarepeat expansion correlates with copper binding properties.

Stevens DJ, Walter ED, Rodríguez A, Draper D, Davies P, Brown DR, Millhauser GL.

PLoS Pathog. 2009 Apr;5(4):e1000390. Epub 2009 Apr 17.PMID: 19381258 [PubMed - indexed for MEDLINE]Related articlesFree article

Failure to detect the presence of prions in the uterine and gestational tissues from a Gravida with Creutzfeldt-Jakob disease.

Xiao X, Miravalle L, Yuan J, McGeehan J, Dong Z, Wyza R, MacLennan GT, Golichowski AM, Kneale G, King N, Kong Q, Spina S, Vidal R, Ghetti B, Roos K, Gambetti P, Zou WQ.

Am J Pathol. 2009 May;174(5):1602-8. Epub 2009 Apr 6.PMID: 19349373 [PubMed - indexed for MEDLINE]Related articlesFree article

Rapid fracture healing in a patient with inherited prion disease.

Khan RM, Gunaratne LA, Kinmont JC.

Ann R Coll Surg Engl. 2009 Apr;91(3):261-2.PMID: 19335973 [PubMed - indexed for MEDLINE]Related articles

A systems approach to prion disease.

Hwang D, Lee IY, Yoo H, Gehlenborg N, Cho JH, Petritis B, Baxter D, Pitstick R, Young R, Spicer D, Price ND, Hohmann JG, Dearmond SJ, Carlson GA, Hood LE.

Mol Syst Biol. 2009;5:252. Epub 2009 Mar 24.PMID: 19308092 [PubMed - indexed for MEDLINE]Related articlesFree article

Abnormal brain iron homeostasis in human and animal prion disorders.

Singh A, Isaac AO, Luo X, Mohan ML, Cohen ML, Chen F, Kong Q, Bartz J, Singh N.

PLoS Pathog. 2009 Mar;5(3):e1000336. Epub 2009 Mar 13.PMID: 19283067 [PubMed - indexed for MEDLINE]Related articlesFree article

Safety and efficacy of quinacrine in human prion disease (PRION-1 study): a patient-preference trial.

Collinge J, Gorham M, Hudson F, Kennedy A, Keogh G, Pal S, Rossor M, Rudge P, Siddique D, Spyer M, Thomas D, Walker S, Webb T, Wroe S, Darbyshire J.

Lancet Neurol. 2009 Apr;8(4):334-44. Epub 2009 Mar 9.PMID: 19278902 [PubMed - indexed for MEDLINE]Related articlesFree article