Meesmann corneal dystrophy (MECD): report of 2 families and a novel mutation in the cornea specific keratin 12 (KRT12) gene

Ophthalmic Genet. 2005 Dec;26(4):169-73. doi: 10.1080/13816810500374391.

Abstract

Purpose: Meesmann corneal dystrophy (MECD) is an autosomal dominant disorder affecting the corneal epithelium. It is caused by heterozygous mutations in KRT3 or KRT12 gene. Actually, 14 mutations have been reported, 1 in KRT3 and 13 in KRT12. These genes were screened in several patients suffering from MECD.

Methods: Patients from 2 families were screened for mutation in KRT3 and KRT12. Exons were PCR-amplified and directly sequenced. The new mutation was checked by DHPLC in 51 control individuals of Swiss origin.

Results/conclusions: In one family, the M129T heterozygous mutation was observed in KRT12. In the second family, we identified a novel I426S heterozygous mutation in exon 6 of KRT12.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Chromatography, High Pressure Liquid
  • Corneal Dystrophies, Hereditary / genetics*
  • Corneal Dystrophies, Hereditary / pathology
  • Corneal Dystrophies, Hereditary / surgery
  • Epithelium, Corneal / ultrastructure
  • Exons / genetics
  • Female
  • Heterozygote
  • Humans
  • Keratin-12
  • Keratin-3
  • Keratins / genetics*
  • Male
  • Mutation / genetics*
  • Pedigree
  • Polymerase Chain Reaction

Substances

  • KRT12 protein, human
  • KRT3 protein, human
  • Keratin-12
  • Keratin-3
  • Keratins