PubMed

Novel Loci Interacting Epistatically With Bone Morphogenetic Protein Receptor 2 Cause Familial Pulmonary Arterial Hypertension.

Rodriguez-Murillo L, Subaran R, Stewart WC, Pramanik S, Marathe S, Barst RJ, Chung WK, Greenberg DA.

J Heart Lung Transplant. 2009 Oct 26. [Epub ahead of print]PMID: 19864167 [PubMed - as supplied by publisher]Related articles

Pulmonary Arterial Hypertension: Baseline Characteristics From the REVEAL Registry.

Badesch DB, Raskob GE, Elliott CG, Krichman AM, Farber HW, Frost AE, Barst RJ, Benza RL, Liou TG, Turner M, Giles S, Feldkircher K, Miller DP, McGoon M.

Chest. 2009 Oct 16. [Epub ahead of print]PMID: 19837821 [PubMed - as supplied by publisher]Related articles

Longterm survival among patients with scleroderma-associated pulmonary arterial hypertension treated with intravenous epoprostenol.

Badesch DB, McGoon MD, Barst RJ, Tapson VF, Rubin LJ, Wigley FM, Kral KM, Raphiou IH, Crater GD.

J Rheumatol. 2009 Oct;36(10):2244-9. Epub 2009 Sep 1.PMID: 19723905 [PubMed - in process]Related articles

Updated evidence-based treatment algorithm in pulmonary arterial hypertension.

Barst RJ, Gibbs JS, Ghofrani HA, Hoeper MM, McLaughlin VV, Rubin LJ, Sitbon O, Tapson VF, Galiè N.

J Am Coll Cardiol. 2009 Jun 30;54(1 Suppl):S78-84. Review.PMID: 19555861 [PubMed - indexed for MEDLINE]Related articles

Future perspectives for the treatment of pulmonary arterial hypertension.

Ghofrani HA, Barst RJ, Benza RL, Champion HC, Fagan KA, Grimminger F, Humbert M, Simonneau G, Stewart DJ, Ventura C, Rubin LJ.

J Am Coll Cardiol. 2009 Jun 30;54(1 Suppl):S108-17. Review.PMID: 19555854 [PubMed - indexed for MEDLINE]Related articles

Doppler-defined pulmonary hypertension and the risk of death in children with sickle cell disease followed for a mean of three years.

Lee MT, Small T, Khan MA, Rosenzweig EB, Barst RJ, Brittenham GM.

Br J Haematol. 2009 Aug;146(4):437-41. Epub 2009 Jun 25.PMID: 19563512 [PubMed - indexed for MEDLINE]Related articles

Tadalafil therapy for pulmonary arterial hypertension.

Galiè N, Brundage BH, Ghofrani HA, Oudiz RJ, Simonneau G, Safdar Z, Shapiro S, White RJ, Chan M, Beardsworth A, Frumkin L, Barst RJ; Pulmonary Arterial Hypertension and Response to Tadalafil (PHIRST) Study Group.

Circulation. 2009 Jun 9;119(22):2894-903. Epub 2009 May 26.PMID: 19470885 [PubMed - in process]Related articles

Conventional and targeted medical therapies.

Barst RJ, Stewart D.

Cardiol Young. 2009 May;19 Suppl 1:28-34. No abstract available. PMID: 19419603 [PubMed - indexed for MEDLINE]Related articles

Pulmonary arterial hypertension in children: a medical update.

Rosenzweig EB, Barst RJ.

Indian J Pediatr. 2009 Jan;76(1):77-81. Epub 2009 Apr 18. Review.PMID: 19391006 [PubMed - indexed for MEDLINE]Related articles

ACCF/AHA 2009 expert consensus document on pulmonary hypertension a report of the American College of Cardiology Foundation Task Force on Expert Consensus Documents and the American Heart Association developed in collaboration with the American College of Chest Physicians; American Thoracic Society, Inc.; and the Pulmonary Hypertension Association.

McLaughlin VV, Archer SL, Badesch DB, Barst RJ, Farber HW, Lindner JR, Mathier MA, McGoon MD, Park MH, Rosenson RS, Rubin LJ, Tapson VF, Varga J; American College of Cardiology Foundation Task Force on Expert Consensus Documents; American Heart Association; American College of Chest Physicians; American Thoracic Society, Inc; Pulmonary Hypertension Association.

J Am Coll Cardiol. 2009 Apr 28;53(17):1573-619. No abstract available. PMID: 19389575 [PubMed - indexed for MEDLINE]Related articles

ACCF/AHA 2009 expert consensus document on pulmonary hypertension: a report of the American College of Cardiology Foundation Task Force on Expert Consensus Documents and the American Heart Association: developed in collaboration with the American College of Chest Physicians, American Thoracic Society, Inc., and the Pulmonary Hypertension Association.

McLaughlin VV, Archer SL, Badesch DB, Barst RJ, Farber HW, Lindner JR, Mathier MA, McGoon MD, Park MH, Rosenson RS, Rubin LJ, Tapson VF, Varga J, Harrington RA, Anderson JL, Bates ER, Bridges CR, Eisenberg MJ, Ferrari VA, Grines CL, Hlatky MA, Jacobs AK, Kaul S, Lichtenberg RC, Lindner JR, Moliterno DJ, Mukherjee D, Pohost GM, Rosenson RS, Schofield RS, Shubrooks SJ, Stein JH, Tracy CM, Weitz HH, Wesley DJ; ACCF/AHA.

Circulation. 2009 Apr 28;119(16):2250-94. Epub 2009 Mar 30. Review. No abstract available. Erratum in: Circulation. 2009 Jul 14;120(2):e13. PMID: 19332472 [PubMed - indexed for MEDLINE]Related articles

Polymorphism in the angiotensin II type 1 receptor (AGTR1) is associated with age at diagnosis in pulmonary arterial hypertension.

Chung WK, Deng L, Carroll JS, Mallory N, Diamond B, Rosenzweig EB, Barst RJ, Morse JH.

J Heart Lung Transplant. 2009 Apr;28(4):373-9.PMID: 19332265 [PubMed - indexed for MEDLINE]Related articles

Familial pulmonary arterial hypertension, leucopenia, and atrial septal defect: a probable new familial syndrome with multisystem involvement.

Dursun A, Ozgul RK, Soydas A, Tugrul T, Gurgey A, Celiker A, Barst RJ, Knowles JA, Mahesh M, Morse JH.

Clin Dysmorphol. 2009 Jan;18(1):19-23.PMID: 19011569 [PubMed - indexed for MEDLINE]Related articles

Addition of sildenafil to long-term intravenous epoprostenol therapy in patients with pulmonary arterial hypertension: a randomized trial.

Simonneau G, Rubin LJ, Galiè N, Barst RJ, Fleming TR, Frost AE, Engel PJ, Kramer MR, Burgess G, Collings L, Cossons N, Sitbon O, Badesch DB; PACES Study Group.

Ann Intern Med. 2008 Oct 21;149(8):521-30. Erratum in: Ann Intern Med. 2009 Jan 6;150(1):63. Ann Intern Med. 2009 Sep 15;151(6):435. PMID: 18936500 [PubMed - indexed for MEDLINE]Related articlesFree article

Determinants of right ventricular ejection fraction in pulmonary arterial hypertension.

Kawut SM, Al-Naamani N, Agerstrand C, Rosenzweig EB, Rowan C, Barst RJ, Bergmann S, Horn EM.

Chest. 2009 Mar;135(3):752-9. Epub 2008 Oct 10.PMID: 18849396 [PubMed - indexed for MEDLINE]Related articles

Design of the REVEAL registry for US patients with pulmonary arterial hypertension.

McGoon MD, Krichman A, Farber HW, Barst RJ, Raskob GE, Liou TG, Miller DP, Feldkircher K, Giles S.

Mayo Clin Proc. 2008 Aug;83(8):923-31.PMID: 18674477 [PubMed - indexed for MEDLINE]Related articlesFree article

Guidelines for the prevention of central venous catheter-related blood stream infections with prostanoid therapy for pulmonary arterial hypertension.

Doran AK, Ivy DD, Barst RJ, Hill N, Murali S, Benza RL; Scientific Leadership Council of the Pulmonary Hypertension Association.

Int J Clin Pract Suppl. 2008 Jul;(160):5-9.PMID: 18638170 [PubMed - indexed for MEDLINE]Related articles

Sitaxsentan for the treatment of pulmonary arterial hypertension: a 1-year, prospective, open-label observation of outcome and survival.

Benza RL, Barst RJ, Galie N, Frost A, Girgis RE, Highland KB, Strange C, Black CM, Badesch DB, Rubin L, Fleming TR, Naeije R.

Chest. 2008 Oct;134(4):775-82. Epub 2008 Jul 14. Erratum in: Chest. 2009 Apr;135(4):1114. PMID: 18625676 [PubMed - indexed for MEDLINE]Related articlesFree article

Continuous hemodynamic monitoring in patients with pulmonary arterial hypertension.

Frantz RP, Benza RL, Kjellström B, Bourge RC, Barst RJ, Bennett TD, McGoon MD.

J Heart Lung Transplant. 2008 Jul;27(7):780-8. Epub 2008 Jun 2.PMID: 18582809 [PubMed - indexed for MEDLINE]Related articles

Clinical implications of determining BMPR2 mutation status in a large cohort of children and adults with pulmonary arterial hypertension.

Rosenzweig EB, Morse JH, Knowles JA, Chada KK, Khan AM, Roberts KE, McElroy JJ, Juskiw NK, Mallory NC, Rich S, Diamond B, Barst RJ.

J Heart Lung Transplant. 2008 Jun;27(6):668-74. Epub 2008 Apr 9.PMID: 18503968 [PubMed - indexed for MEDLINE]Related articles

Pulmonary arterial hypertension in children: a medical update.

Rosenzweig EB, Barst RJ.

Curr Opin Pediatr. 2008 Jun;20(3):288-93. Review.PMID: 18475097 [PubMed - indexed for MEDLINE]Related articles

Bloodstream infections in patients given treatment with intravenous prostanoids.

Kallen AJ, Lederman E, Balaji A, Trevino I, Petersen EE, Shoulson R, Saiman L, Horn EM, Gomberg-Maitland M, Barst RJ, Srinivasan A.

Infect Control Hosp Epidemiol. 2008 Apr;29(4):342-9.PMID: 18462147 [PubMed - indexed for MEDLINE]Related articles

Short- and long-term effects of inhaled iloprost therapy in children with pulmonary arterial hypertension.

Ivy DD, Doran AK, Smith KJ, Mallory GB Jr, Beghetti M, Barst RJ, Brady D, Law Y, Parker D, Claussen L, Abman SH.

J Am Coll Cardiol. 2008 Jan 15;51(2):161-9.PMID: 18191742 [PubMed - indexed for MEDLINE]Related articles

Pulmonary hypertension: Past, present and future.

Barst RJ.

Ann Thorac Med. 2008 Jan;3(1):1-4. No abstract available. PMID: 19561874 [PubMed - in process]Related articlesFree article

Sildenafil for pulmonary arterial hypertension associated with connective tissue disease.

Badesch DB, Hill NS, Burgess G, Rubin LJ, Barst RJ, Galiè N, Simonneau G; SUPER Study Group.

J Rheumatol. 2007 Dec;34(12):2417-22. Epub 2007 Nov 1.PMID: 17985403 [PubMed - indexed for MEDLINE]Related articles

The effect of atrial septostomy on the concentration of brain-type natriuretic peptide in patients with idiopathic pulmonary arterial hypertension.

O'Byrne ML, Rosenzweig ES, Barst RJ.

Cardiol Young. 2007 Oct;17(5):557-9. Epub 2007 Sep 17.PMID: 17868499 [PubMed - indexed for MEDLINE]Related articles

Creation of a model comparing 6-minute walk test to metabolic equivalent in evaluating treatment effects in pulmonary arterial hypertension.

Gomberg-Maitland M, Huo D, Benza RL, McLaughlin VV, Tapson VF, Barst RJ.

J Heart Lung Transplant. 2007 Jul;26(7):732-8. Epub 2007 Jun 13.PMID: 17613405 [PubMed - indexed for MEDLINE]Related articles

A review of pulmonary arterial hypertension: role of ambrisentan.

Barst RJ.

Vasc Health Risk Manag. 2007;3(1):11-22. Review.PMID: 17583171 [PubMed - indexed for MEDLINE]Related articlesFree article

Right ventricular pressure waveform and wave reflection analysis in patients with pulmonary arterial hypertension.

Karamanoglu M, McGoon M, Frantz RP, Benza RL, Bourge RC, Barst RJ, Kjellström B, Bennett TD.

Chest. 2007 Jul;132(1):37-43. Epub 2007 May 15.PMID: 17505045 [PubMed - indexed for MEDLINE]Related articlesFree article

Selective endothelin A receptor antagonism with sitaxsentan for pulmonary arterial hypertension associated with connective tissue disease.

Girgis RE, Frost AE, Hill NS, Horn EM, Langleben D, McLaughlin VV, Oudiz RJ, Robbins IM, Seibold JR, Shapiro S, Tapson VF, Barst RJ.

Ann Rheum Dis. 2007 Nov;66(11):1467-72. Epub 2007 May 1.PMID: 17472992 [PubMed - indexed for MEDLINE]Related articles

Plasma serotonin levels are normal in pulmonary arterial hypertension.

Lederer DJ, Horn EM, Rosenzweig EB, Karmally W, Jahnes M, Barst RJ, Kawut SM.

Pulm Pharmacol Ther. 2008;21(1):112-4. Epub 2007 Feb 12.PMID: 17374499 [PubMed - indexed for MEDLINE]Related articlesFree article

Sitaxsentan treatment for patients with pulmonary arterial hypertension discontinuing bosentan.

Benza RL, Mehta S, Keogh A, Lawrence EC, Oudiz RJ, Barst RJ.

J Heart Lung Transplant. 2007 Jan;26(1):63-9.PMID: 17234519 [PubMed - indexed for MEDLINE]Related articles

Complications of right heart catheterization procedures in patients with pulmonary hypertension in experienced centers.

Hoeper MM, Lee SH, Voswinckel R, Palazzini M, Jais X, Marinelli A, Barst RJ, Ghofrani HA, Jing ZC, Opitz C, Seyfarth HJ, Halank M, McLaughlin V, Oudiz RJ, Ewert R, Wilkens H, Kluge S, Bremer HC, Baroke E, Rubin LJ.

J Am Coll Cardiol. 2006 Dec 19;48(12):2546-52. Epub 2006 Nov 28.PMID: 17174196 [PubMed - indexed for MEDLINE]Related articles

Sitaxsentan: a selective endothelin-A receptor antagonist, for the treatment of pulmonary arterial hypertension.

Barst RJ.

Expert Opin Pharmacother. 2007 Jan;8(1):95-109. Review.PMID: 17163810 [PubMed - indexed for MEDLINE]Related articles

Right ventricular function and failure: report of a National Heart, Lung, and Blood Institute working group on cellular and molecular mechanisms of right heart failure.

Voelkel NF, Quaife RA, Leinwand LA, Barst RJ, McGoon MD, Meldrum DR, Dupuis J, Long CS, Rubin LJ, Smart FW, Suzuki YJ, Gladwin M, Denholm EM, Gail DB; National Heart, Lung, and Blood Institute Working Group on Cellular and Molecular Mechanisms of Right Heart Failure.

Circulation. 2006 Oct 24;114(17):1883-91. No abstract available. PMID: 17060398 [PubMed - indexed for MEDLINE]Related articlesFree article

Delivery of intravenous treprostinil at low infusion rates using a miniaturized infusion pump in patients with pulmonary arterial hypertension.

Tapson VF, McLaughlin VV, Gomberg-Maitland M, Widlitz AC, Krichman AD, Laliberte KJ, Zaccardelli DS, Barst RJ.

J Vasc Access. 2006 Jul-Sep;7(3):112-7.PMID: 17019662 [PubMed - indexed for MEDLINE]Related articles

Randomized study of adding inhaled iloprost to existing bosentan in pulmonary arterial hypertension.

McLaughlin VV, Oudiz RJ, Frost A, Tapson VF, Murali S, Channick RN, Badesch DB, Barst RJ, Hsu HH, Rubin LJ.

Am J Respir Crit Care Med. 2006 Dec 1;174(11):1257-63. Epub 2006 Aug 31.PMID: 16946127 [PubMed - indexed for MEDLINE]Related articlesFree article

Temporal trends and drug exposures in pulmonary hypertension: an American experience.

Walker AM, Langleben D, Korelitz JJ, Rich S, Rubin LJ, Strom BL, Gonin R, Keast S, Badesch D, Barst RJ, Bourge RC, Channick R, Frost A, Gaine S, McGoon M, McLaughlin V, Murali S, Oudiz RJ, Robbins IM, Tapson V, Abenhaim L, Constantine G.

Am Heart J. 2006 Sep;152(3):521-6.PMID: 16923424 [PubMed - indexed for MEDLINE]Related articles

Long-term outcome in pulmonary arterial hypertension patients treated with subcutaneous treprostinil.

Barst RJ, Galie N, Naeije R, Simonneau G, Jeffs R, Arneson C, Rubin LJ.

Eur Respir J. 2006 Dec;28(6):1195-203. Epub 2006 Aug 9.PMID: 16899485 [PubMed - indexed for MEDLINE]Related articlesFree article

Treatment of pulmonary arterial hypertension with the selective endothelin-A receptor antagonist sitaxsentan.

Barst RJ, Langleben D, Badesch D, Frost A, Lawrence EC, Shapiro S, Naeije R, Galie N; STRIDE-2 Study Group.

J Am Coll Cardiol. 2006 May 16;47(10):2049-56. Epub 2006 Apr 24.PMID: 16697324 [PubMed - indexed for MEDLINE]Related articles

Safety and efficacy of IV treprostinil for pulmonary arterial hypertension: a prospective, multicenter, open-label, 12-week trial.

Tapson VF, Gomberg-Maitland M, McLaughlin VV, Benza RL, Widlitz AC, Krichman A, Barst RJ.

Chest. 2006 Mar;129(3):683-8.PMID: 16537868 [PubMed - indexed for MEDLINE]Related articlesFree article

Pulmonary arterial hypertension : a comprehensive review of pharmacological treatment.

Berman Rosenzweig E, Barst RJ.

Treat Respir Med. 2006;5(2):117-27.PMID: 16512692 [PubMed - in process]Related articles

A study of aspirin and clopidogrel in idiopathic pulmonary arterial hypertension.

Robbins IM, Kawut SM, Yung D, Reilly MP, Lloyd W, Cunningham G, Loscalzo J, Kimmel SE, Christman BW, Barst RJ.

Eur Respir J. 2006 Mar;27(3):578-84.PMID: 16507859 [PubMed - indexed for MEDLINE]Related articlesFree article

Report of the National Heart, Lung, and Blood Institute Working Group on research in adult congenital heart disease.

Williams RG, Pearson GD, Barst RJ, Child JS, del Nido P, Gersony WM, Kuehl KS, Landzberg MJ, Myerson M, Neish SR, Sahn DJ, Verstappen A, Warnes CA, Webb CL; National Heart, Lung, and Blood Institute Working Group on research in adult congenital heart disease.

J Am Coll Cardiol. 2006 Feb 21;47(4):701-7. Epub 2006 Jan 26.PMID: 16487831 [PubMed - indexed for MEDLINE]Related articles

Selective serotonin reuptake inhibitor use and outcomes in pulmonary arterial hypertension.

Kawut SM, Horn EM, Berekashvili KK, Lederer DJ, Widlitz AC, Rosenzweig EB, Barst RJ.

Pulm Pharmacol Ther. 2006;19(5):370-4. Epub 2006 Feb 17.PMID: 16483811 [PubMed - indexed for MEDLINE]Related articles

Cardiopulmonary exercise testing and six-minute walk correlations in pulmonary arterial hypertension.

Oudiz RJ, Barst RJ, Hansen JE, Sun XG, Garofano R, Wu X, Wasserman K.

Am J Cardiol. 2006 Jan 1;97(1):123-6. Epub 2005 Nov 10.PMID: 16377296 [PubMed - indexed for MEDLINE]Related articles

Bone morphogenetic protein receptor 2 mutations in adults and children with idiopathic pulmonary arterial hypertension: association with thyroid disease.

Roberts KE, Barst RJ, McElroy JJ, Widlitz A, Chada K, Knowles JA, Morse JH.

Chest. 2005 Dec;128(6 Suppl):618S. No abstract available. PMID: 16373874 [PubMed - indexed for MEDLINE]Related articlesFree article

Serotonin transporter polymorphisms in familial and idiopathic pulmonary arterial hypertension.

Willers ED, Newman JH, Loyd JE, Robbins IM, Wheeler LA, Prince MA, Stanton KC, Cogan JA, Runo JR, Byrne D, Humbert M, Simonneau G, Sztrymf B, Morse JA, Knowles JA, Roberts KE, McElroy JJ, Barst RJ, Phillips JA 3rd.

Am J Respir Crit Care Med. 2006 Apr 1;173(7):798-802. Epub 2005 Dec 9.PMID: 16339917 [PubMed - indexed for MEDLINE]Related articlesFree article

Sitaxsentan: a novel endothelin-A receptor antagonist for pulmonary arterial hypertension.

Widlitz AC, Barst RJ, Horn EM.

Expert Rev Cardiovasc Ther. 2005 Nov;3(6):985-91. Review.PMID: 16292989 [PubMed - indexed for MEDLINE]Related articles

Sildenafil citrate therapy for pulmonary arterial hypertension.

Galiè N, Ghofrani HA, Torbicki A, Barst RJ, Rubin LJ, Badesch D, Fleming T, Parpia T, Burgess G, Branzi A, Grimminger F, Kurzyna M, Simonneau G; Sildenafil Use in Pulmonary Arterial Hypertension (SUPER) Study Group.

N Engl J Med. 2005 Nov 17;353(20):2148-57. Erratum in: N Engl J Med. 2006 Jun 1;354(22):2400-1. PMID: 16291984 [PubMed - indexed for MEDLINE]Related articlesFree article