Ann Rheum Dis. 1991 Oct;50(10):713-6.

Acquired C1 inhibitor deficiency associated with systemic lupus erythematosus affecting the central nervous system.

Nakamura S, Yoshinari M, Saku Y, Hirakawa K, Miishima C, Murai K, Tokiyama K, Fujishima M.

Source

Second Department of Internal Medicine, Faculty of Medicine, Kyushu University, Japan.

Abstract

A 22 year old woman with systemic lupus erythematosus affecting the central nervous system had acquired C1 inhibitor deficiency. She was admitted for treatment of psychotic behaviour, but showed no signs of angioedema. The serum complement profile of the patient showed normal C3 concentration and a depletion of C4, C2, C1 inhibitor, and C1q. Her parents had normal complement profiles. An extremely reduced C4 concentration may lead to involvement of the central nervous system in systemic lupus erythematosus.

PMID:: 1958096; [PubMed - indexed for MEDLINE]
PMCID:: PMC1004538

Free PMC Article

Publication Types, MeSH Terms, Substances

Publication Types

Case Reports

MeSH Terms

Substances

LinkOut - more resources

Full Text Sources

Other Literature Sources

Labome Researcher Resource - ExactAntigen/Labome

Medical

Libraries

LinkOut Holdings

Supplemental Content

Save items

Related citations in PubMed

C1 inhibitor deficiency simulating systemic lupus erythematosus. [Br J Dermatol. 1982]
C1 inhibitor deficiency simulating systemic lupus erythematosus.
Shiraishi S, Nara Y, Watanabe Y, Matsuda K, Miki Y. Br J Dermatol. 1982 Apr; 106(4):455-60.
A new type of acquired C1 inhibitor deficiency associated with systemic lupus erythematosus. [Arthritis Rheum. 2001]
A new type of acquired C1 inhibitor deficiency associated with systemic lupus erythematosus.
Cacoub P, Frémeaux-Bacchi V, De Lacroix I, Guillien F, Kahn MF, Kazatchkine MD, Godeau P, Piette JC. Arthritis Rheum. 2001 Aug; 44(8):1836-40.
Acquired C1 inhibitor deficiency associated with systemic lupus erythematosus, secondary antiphospholipid syndrome and IgM monoclonal paraproteinaemia. [Clin Rheumatol. 1999]
Acquired C1 inhibitor deficiency associated with systemic lupus erythematosus, secondary antiphospholipid syndrome and IgM monoclonal paraproteinaemia.
Nagy L, Hannema A, Swaak A. Clin Rheumatol. 1999; 18(1):56-8.
Review Lupus erythematosus associated with C1 inhibitor deficiency. [J Dermatol. 2002]
Review Lupus erythematosus associated with C1 inhibitor deficiency.
Koide M, Shirahama S, Tokura Y, Takigawa M, Hayakawa M, Furukawa F. J Dermatol. 2002 Aug; 29(8):503-7.
Review Lupus diseases associated with hereditary and acquired deficiencies of complement. [Springer Semin Immunopathol. 1...]
Review Lupus diseases associated with hereditary and acquired deficiencies of complement.
Agnello V. Springer Semin Immunopathol. 1986; 9(2-3):161-78.

See reviews... See all...

Cited by 1 PubMed Central article

Acquired angioedema. [Allergy Asthma Clin Immunol. 2...]
Acquired angioedema.
Cicardi M, Zanichelli A. Allergy Asthma Clin Immunol. 2010 Jul 28; 6(1):14. Epub 2010 Jul 28.

Related information

Related Citations
Calculated set of PubMed citations closely related to the selected article(s) retrieved using a word weight algorithm. Related articles are displayed in ranked order from most to least relevant, with the “linked from” citation displayed first.
References for this PMC Article
Citation referenced in PubMed article. Only valid for PubMed citations that are also in PMC.
Substance (MeSH Keyword)
PubChem chemical substance (submitted) records that are classified under the same Medical Subject Headings (MeSH) controlled vocabulary as the current articles.
Free in PMC
Free full text articles in PMC
Cited in PMC
Full-text articles in the PubMed Central Database that cite the current articles.

Recent activity

Clear Turn Off Turn On

Acquired C1 inhibitor deficiency associated with systemic lupus erythematosus af...
Acquired C1 inhibitor deficiency associated with systemic lupus erythematosus affecting the central nervous system.
Ann Rheum Dis. 1991 Oct ;50(10):713-6.

PubMed
Cinryze, a Human Plasma-Derived C1 Esterase Inhibitor for Prophylaxis Of Heredit...
Cinryze, a Human Plasma-Derived C1 Esterase Inhibitor for Prophylaxis Of Hereditary Angioedema.
P T. 2009 Jun;34(6):293-328.

PubMed
[Pedicle torsion, hemorrhagic ovarian infarct. A rare cause of pediatric acute a...
[Pedicle torsion, hemorrhagic ovarian infarct. A rare cause of pediatric acute abdomen].
Zentralbl Chir. 1991 ;116(11):679-82.

PubMed
Self-administration of intravenous C1-inhibitor therapy for hereditary angioedem...
Self-administration of intravenous C1-inhibitor therapy for hereditary angioedema and associated quality of life benefits.
Eur J Dermatol. 2009 Mar-Apr ;19(2):147-51.

PubMed
Cord serum IgE: an insensitive method for prediction of atopy.
Cord serum IgE: an insensitive method for prediction of atopy.
Clin Exp Allergy. 1991 Nov ;21(6):739-43.

PubMed

Your browsing activity is empty.

Activity recording is turned off.

Turn recording back on

PubMed

Result Filters

Display Settings:

Send to: