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    Results: 18

    1.

    Hair-shaft abnormality in a 7-year-old girl. Trichorrhexis nodosa dueto biotinidase deficiency.

    Lünnemann L, Vogt A, Blume-Peytavi U, Garcia Bartels N.

    JAMA Dermatol. 2013 Mar;149(3):357-63. doi: 10.1001/jamadermatol.2013.1490a 10.1001/jamadermatol.2013.1490b. No abstract available.

    PMID:
    23552716
    [PubMed - indexed for MEDLINE]
    2.

    Biotinidase deficiency in Pakistani children; what needs to be known and done.

    Afroze B, Wasay M.

    J Pak Med Assoc. 2012 Apr;62(4):312-3. No abstract available.

    PMID:
    22755269
    [PubMed - indexed for MEDLINE]
    3.

    Increased incidence of profound biotinidase deficiency among Hispanic newborns in California.

    Cowan TM, Kazerouni NN, Dharajiya N, Lorey F, Roberson M, Hodgkinson C, Schrijver I.

    Mol Genet Metab. 2012 Aug;106(4):485-7. doi: 10.1016/j.ymgme.2012.05.017. Epub 2012 May 30.

    PMID:
    22698809
    [PubMed - indexed for MEDLINE]
    4.

    Hemophagocytic syndrome in a 4-month-old infant with biotinidase deficiency.

    Kardas F, Patiroglu T, Unal E, Chiang SC, Bryceson YT, Kendirci M.

    Pediatr Blood Cancer. 2012 Jul 15;59(1):191-3. doi: 10.1002/pbc.23247. Epub 2011 Aug 16.

    PMID:
    22605457
    [PubMed - indexed for MEDLINE]
    5.

    Clinical utility gene card for: biotinidase deficiency.

    Küry S, Ramaekers V, Bézieau S, Wolf B.

    Eur J Hum Genet. 2012 May;20(5). doi: 10.1038/ejhg.2012.28. Epub 2012 Feb 29. No abstract available.

    PMID:
    22378278
    [PubMed - indexed for MEDLINE]
    Free PMC Article
    6.

    Biotinidase deficiency: "if you have to have an inherited metabolic disease, this is the one to have".

    Wolf B.

    Genet Med. 2012 Jun;14(6):565-75. doi: 10.1038/gim.2011.6. Epub 2012 Jan 5. Review.

    PMID:
    22241090
    [PubMed - indexed for MEDLINE]
    7.

    Mutational analysis for biotinidase deficiency of a Greek patients' cohort ascertained through expanded newborn screening.

    Thodi G, Molou E, Georgiou V, Loukas YL, Dotsikas Y, Biti S, Papadopoulos K, Konstantinou D, Antoniadi M, Doulgerakis E.

    J Hum Genet. 2011 Dec;56(12):861-5. doi: 10.1038/jhg.2011.119. Epub 2011 Oct 20.

    PMID:
    22011816
    [PubMed - indexed for MEDLINE]
    8.

    VACTERL association: a new case with biotinidase deficiency and annular pancreas.

    Sezer RG, Aydemir G, Bozaykut A, Paketci C, Aydinoz S.

    Ren Fail. 2012;34(1):123-5. doi: 10.3109/0886022X.2011.623491. Epub 2011 Oct 20.

    PMID:
    22010814
    [PubMed - indexed for MEDLINE]
    9.

    Biotinidase deficiency presenting as recurrent myelopathy in a 7-year-old boy and a review of the literature.

    Raha S, Udani V.

    Pediatr Neurol. 2011 Oct;45(4):261-4. doi: 10.1016/j.pediatrneurol.2011.06.010. Review.

    PMID:
    21907891
    [PubMed - indexed for MEDLINE]
    10.

    The neurology of biotinidase deficiency.

    Wolf B.

    Mol Genet Metab. 2011 Sep-Oct;104(1-2):27-34. doi: 10.1016/j.ymgme.2011.06.001. Epub 2011 Jun 12. Review.

    PMID:
    21696988
    [PubMed - indexed for MEDLINE]
    11.

    A girl with spastic tetraparesis associated with biotinidase deficiency.

    Komur M, Okuyaz C, Ezgu F, Atici A.

    Eur J Paediatr Neurol. 2011 Nov;15(6):551-3. doi: 10.1016/j.ejpn.2011.04.012. Epub 2011 May 14.

    PMID:
    21571559
    [PubMed - indexed for MEDLINE]
    12.

    Biotinidase deficiency--clinching the diagnosis rapidly can make all the difference!

    Rajendiran A, Sampath S.

    BMJ Case Rep. 2011 Sep 28;2011. doi:pii: bcr0720114494. 10.1136/bcr.07.2011.4494.

    PMID:
    22679321
    [PubMed - indexed for MEDLINE]
    13.

    Newborn screening conditions: What we know, what we do not know, and how we will know it.

    Levy HL.

    Genet Med. 2010 Dec;12(12 Suppl):S213-4. doi: 10.1097/GIM.0b013e3181fe5d77.

    PMID:
    21150366
    [PubMed - indexed for MEDLINE]
    14.

    Peculiar neuroimaging and electrophysiological findings in a patient with biotinidase deficiency.

    Bunch M, Singh A.

    Seizure. 2011 Jan;20(1):83-6. doi: 10.1016/j.seizure.2010.10.001. Epub 2010 Dec 3.

    PMID:
    21123088
    [PubMed - indexed for MEDLINE]
    15.

    Ohtahara syndrome with biotinidase deficiency.

    Singhi P, Ray M.

    J Child Neurol. 2011 Apr;26(4):507-9. doi: 10.1177/0883073810383018. Epub 2010 Nov 29.

    PMID:
    21115748
    [PubMed - indexed for MEDLINE]
    16.

    The national Austrian newborn screening program - eight years experience with mass spectrometry. past, present, and future goals.

    Kasper DC, Ratschmann R, Metz TF, Mechtler TP, Möslinger D, Konstantopoulou V, Item CB, Pollak A, Herkner KR.

    Wien Klin Wochenschr. 2010 Nov;122(21-22):607-13. doi: 10.1007/s00508-010-1457-3. Epub 2010 Oct 15.

    PMID:
    20938748
    [PubMed - indexed for MEDLINE]
    17.

    Analysis of mutations causing biotinidase deficiency.

    Pindolia K, Jordan M, Wolf B.

    Hum Mutat. 2010 Sep;31(9):983-91. doi: 10.1002/humu.21303.

    PMID:
    20556795
    [PubMed - indexed for MEDLINE]
    18.

    Two unusual clinical and radiological presentations of biotinidase deficiency.

    Mc Sweeney N, Grunewald S, Bhate S, Ganesan V, Chong WK, Hemingway C.

    Eur J Paediatr Neurol. 2010 Nov;14(6):535-8. doi: 10.1016/j.ejpn.2010.01.001. Epub 2010 Feb 12.

    PMID:
    20153672
    [PubMed - indexed for MEDLINE]

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