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Results: 1 to 20 of 59

1.

Disruption of interleukin-1β autocrine signaling rescues complex I activity and improves ROS levels in immortalized epithelial cells with impaired cystic fibrosis transmembrane conductance regulator (CFTR) function.

Clauzure M, Valdivieso AG, Massip Copiz MM, Schulman G, Teiber ML, Santa-Coloma TA.

PLoS One. 2014 Jun 5;9(6):e99257. doi: 10.1371/journal.pone.0099257. eCollection 2014.

PMID:
24901709
[PubMed - in process]
Free PMC Article
2.

Birth of a new therapeutic platform: 47 years of adeno-associated virus biology from virus discovery to licensed gene therapy.

Flotte TR.

Mol Ther. 2013 Nov;21(11):1976-81. doi: 10.1038/mt.2013.226. No abstract available.

PMID:
24201212
[PubMed - indexed for MEDLINE]
Free PMC Article
3.

Correction of mutations within the cystic fibrosis transmembrane conductance regulator by site-directed RNA editing.

Montiel-Gonzalez MF, Vallecillo-Viejo I, Yudowski GA, Rosenthal JJ.

Proc Natl Acad Sci U S A. 2013 Nov 5;110(45):18285-90. doi: 10.1073/pnas.1306243110. Epub 2013 Oct 9.

PMID:
24108353
[PubMed - indexed for MEDLINE]
Free PMC Article
4.

A distal enhancer controls cytokine-dependent human cPLA2α gene expression.

Bickford JS, Beachy DE, Newsom KJ, Barilovits SJ, Herlihy JD, Qiu X, Walters JN, Li N, Nick HS.

J Lipid Res. 2013 Jul;54(7):1915-26. doi: 10.1194/jlr.M037382. Epub 2013 Apr 2.

PMID:
23549331
[PubMed - indexed for MEDLINE]
Free PMC Article
5.

The mitochondrial complex I activity is reduced in cells with impaired cystic fibrosis transmembrane conductance regulator (CFTR) function.

Valdivieso AG, Clauzure M, Marín MC, Taminelli GL, Massip Copiz MM, Sánchez F, Schulman G, Teiber ML, Santa-Coloma TA.

PLoS One. 2012;7(11):e48059. doi: 10.1371/journal.pone.0048059. Epub 2012 Nov 21.

PMID:
23185247
[PubMed - indexed for MEDLINE]
Free PMC Article
6.

Effect of allergy and inflammation on eicosanoid gene expression in CFTR deficiency.

Bickford JS, Mueller C, Newsom KJ, Barilovits SJ, Beachy DE, Herlihy JD, Keeler B, Flotte TR, Nick HS.

J Cyst Fibros. 2013 May;12(3):258-65. doi: 10.1016/j.jcf.2012.08.014. Epub 2012 Sep 15.

PMID:
22985691
[PubMed - indexed for MEDLINE]
Free PMC Article
7.

Cystic fibrosis-niche adaptation of Pseudomonas aeruginosa reduces virulence in multiple infection hosts.

Lorè NI, Cigana C, De Fino I, Riva C, Juhas M, Schwager S, Eberl L, Bragonzi A.

PLoS One. 2012;7(4):e35648. doi: 10.1371/journal.pone.0035648. Epub 2012 Apr 25.

PMID:
22558188
[PubMed - indexed for MEDLINE]
Free PMC Article
8.

The prevalence of common CFTR mutations in Iranian infertile men with non-CAVD obstructive azoospermia by using ARMS PCR techniques.

Safinejad K, Darbouy M, Kalantar SM, Zeinali S, Mirfakhraie R, Yadegar L, Houshmand M.

J Assist Reprod Genet. 2011 Oct 6. [Epub ahead of print]

PMID:
21976147
[PubMed - as supplied by publisher]
Free PMC Article
9.

Increased elongase 6 and Δ9-desaturase activity are associated with n-7 and n-9 fatty acid changes in cystic fibrosis.

Thomsen KF, Laposata M, Njoroge SW, Umunakwe OC, Katrangi W, Seegmiller AC.

Lipids. 2011 Aug;46(8):669-77. doi: 10.1007/s11745-011-3563-z. Epub 2011 May 5.

PMID:
21544602
[PubMed - indexed for MEDLINE]
Free PMC Article
10.

Pseudomonas aeruginosa exploits lipid A and muropeptides modification as a strategy to lower innate immunity during cystic fibrosis lung infection.

Cigana C, Curcurù L, Leone MR, Ieranò T, Lorè NI, Bianconi I, Silipo A, Cozzolino F, Lanzetta R, Molinaro A, Bernardini ML, Bragonzi A.

PLoS One. 2009 Dec 23;4(12):e8439. doi: 10.1371/journal.pone.0008439.

PMID:
20037649
[PubMed - indexed for MEDLINE]
Free PMC Article
11.

Expression and distribution of cystic fibrosis transmembrane conductance regulator in neurons of the human brain.

Guo Y, Su M, McNutt MA, Gu J.

J Histochem Cytochem. 2009 Dec;57(12):1113-20. doi: 10.1369/jhc.2009.953455. Epub 2009 Aug 3.

PMID:
19654104
[PubMed - indexed for MEDLINE]
Free PMC Article
12.

Defective acid sphingomyelinase pathway with Pseudomonas aeruginosa infection in cystic fibrosis.

Yu H, Zeidan YH, Wu BX, Jenkins RW, Flotte TR, Hannun YA, Virella-Lowell I.

Am J Respir Cell Mol Biol. 2009 Sep;41(3):367-75. doi: 10.1165/rcmb.2008-0295OC. Epub 2009 Jan 23.

PMID:
19168701
[PubMed - indexed for MEDLINE]
Free PMC Article
13.

Cystic fibrosis and estrogens: a perfect storm.

Zeitlin PL.

J Clin Invest. 2008 Dec;118(12):3841-4. doi: 10.1172/JCI37778. Epub 2008 Nov 20.

PMID:
19033654
[PubMed - indexed for MEDLINE]
Free PMC Article
14.

Elevated furin levels in human cystic fibrosis cells result in hypersusceptibility to exotoxin A-induced cytotoxicity.

Ornatowski W, Poschet JF, Perkett E, Taylor-Cousar JL, Deretic V.

J Clin Invest. 2007 Nov;117(11):3489-97.

PMID:
17948127
[PubMed - indexed for MEDLINE]
Free PMC Article
15.

The relevance of sweat testing for the diagnosis of cystic fibrosis in the genomic era.

Mishra A, Greaves R, Massie J.

Clin Biochem Rev. 2005 Nov;26(4):135-53.

PMID:
16648884
[PubMed]
Free PMC Article
16.

Nonclassical pathway of Pseudomonas aeruginosa DNA-induced interleukin-8 secretion in cystic fibrosis airway epithelial cells.

Delgado MA, Poschet JF, Deretic V.

Infect Immun. 2006 May;74(5):2975-84.

PMID:
16622236
[PubMed - indexed for MEDLINE]
Free PMC Article
17.

Endosomal hyperacidification in cystic fibrosis is due to defective nitric oxide-cylic GMP signalling cascade.

Poschet JF, Fazio JA, Timmins GS, Ornatowski W, Perkett E, Delgado M, Deretic V.

EMBO Rep. 2006 May;7(5):553-9. Epub 2006 Apr 13.

PMID:
16612392
[PubMed - indexed for MEDLINE]
Free PMC Article
18.

Mechanisms of lipid malabsorption in Cystic Fibrosis: the impact of essential fatty acids deficiency.

Peretti N, Marcil V, Drouin E, Levy E.

Nutr Metab (Lond). 2005 May 3;2(1):11.

PMID:
15869703
[PubMed - as supplied by publisher]
Free PMC Article
19.

Nasal airway ion transport is linked to the cystic fibrosis phenotype in adult patients.

Fajac I, Hubert D, Guillemot D, Honoré I, Bienvenu T, Volter F, Dall'Ava-Santucci J, Dusser DJ.

Thorax. 2004 Nov;59(11):971-6.

PMID:
15516474
[PubMed - indexed for MEDLINE]
Free PMC Article
20.

CLC-2 single nucleotide polymorphisms (SNPs) as potential modifiers of cystic fibrosis disease severity.

Blaisdell CJ, Howard TD, Stern A, Bamford P, Bleecker ER, Stine OC.

BMC Med Genet. 2004 Oct 26;5:26.

PMID:
15507145
[PubMed - indexed for MEDLINE]
Free PMC Article
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