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Results: 1 to 20 of 58

1.

Ubiquitin ligase ITCH recruitment suppresses the aggregation and cellular toxicity of cytoplasmic misfolded proteins.

Chhangani D, Upadhyay A, Amanullah A, Joshi V, Mishra A.

Sci Rep. 2014 May 28;4:5077. doi: 10.1038/srep05077.

PMID:
24865853
[PubMed - in process]
Free PMC Article
2.

Ataxin-3 protein and RNA toxicity in spinocerebellar ataxia type 3: current insights and emerging therapeutic strategies.

Evers MM, Toonen LJ, van Roon-Mom WM.

Mol Neurobiol. 2014 Jun;49(3):1513-31. doi: 10.1007/s12035-013-8596-2. Epub 2013 Nov 29.

PMID:
24293103
[PubMed - in process]
Free PMC Article
3.

Multiple Aspects of Gene Dysregulation in Huntington's Disease.

Moumné L, Betuing S, Caboche J.

Front Neurol. 2013 Oct 23;4:127. doi: 10.3389/fneur.2013.00127. Review.

PMID:
24167500
[PubMed]
Free PMC Article
4.

Trinucleotide repeats: a structural perspective.

Almeida B, Fernandes S, Abreu IA, Macedo-Ribeiro S.

Front Neurol. 2013 Jun 20;4:76. doi: 10.3389/fneur.2013.00076. eCollection 2013.

PMID:
23801983
[PubMed]
Free PMC Article
5.

Sleep and circadian dysfunction in neurodegenerative disorders: insights from a mouse model of Huntington's disease.

Kuljis D, Schroeder AM, Kudo T, Loh DH, Willison DL, Colwell CS.

Minerva Pneumol. 2012 Sep;51(3):93-106.

PMID:
23687390
[PubMed]
Free PMC Article
6.

Cytoplasmic location of α1A voltage-gated calcium channel C-terminal fragment (Cav2.1-CTF) aggregate is sufficient to cause cell death.

Takahashi M, Obayashi M, Ishiguro T, Sato N, Niimi Y, Ozaki K, Mogushi K, Mahmut Y, Tanaka H, Tsuruta F, Dolmetsch R, Yamada M, Takahashi H, Kato T, Mori O, Eishi Y, Mizusawa H, Ishikawa K.

PLoS One. 2013;8(3):e50121. doi: 10.1371/journal.pone.0050121. Epub 2013 Mar 7.

PMID:
23505410
[PubMed - indexed for MEDLINE]
Free PMC Article
7.

Mouse models of polyglutamine diseases in therapeutic approaches: review and data table. Part II.

Switonski PM, Szlachcic WJ, Gabka A, Krzyzosiak WJ, Figiel M.

Mol Neurobiol. 2012 Oct;46(2):430-66. doi: 10.1007/s12035-012-8316-3. Epub 2012 Sep 4. Review.

PMID:
22944909
[PubMed - indexed for MEDLINE]
Free PMC Article
8.

Developing treatment for spinal and bulbar muscular atrophy.

Fischbeck KH.

Prog Neurobiol. 2012 Dec;99(3):257-61. doi: 10.1016/j.pneurobio.2012.05.012. Epub 2012 Jun 2. Review.

PMID:
22668795
[PubMed - indexed for MEDLINE]
Free PMC Article
9.

Cell biology of spinocerebellar ataxia.

Orr HT.

J Cell Biol. 2012 Apr 16;197(2):167-77. doi: 10.1083/jcb.201105092. Review.

PMID:
22508507
[PubMed - indexed for MEDLINE]
Free PMC Article
10.

Neurogenic and myogenic contributions to hereditary motor neuron disease.

Bricceno KV, Fischbeck KH, Burnett BG.

Neurodegener Dis. 2012;9(4):199-209. doi: 10.1159/000335311. Epub 2012 Feb 9. Review.

PMID:
22327341
[PubMed - indexed for MEDLINE]
Free PMC Article
11.

The Aggregation Inhibitor Peptide QBP1 as a Therapeutic Molecule for the Polyglutamine Neurodegenerative Diseases.

Popiel HA, Burke JR, Strittmatter WJ, Oishi S, Fujii N, Takeuchi T, Toda T, Wada K, Nagai Y.

J Amino Acids. 2011;2011:265084. doi: 10.4061/2011/265084. Epub 2011 Jun 30.

PMID:
22312459
[PubMed]
Free PMC Article
12.

Effects of aging and sensory loss on glial cells in mouse visual and auditory cortices.

Tremblay MÈ, Zettel ML, Ison JR, Allen PD, Majewska AK.

Glia. 2012 Apr;60(4):541-58. doi: 10.1002/glia.22287. Epub 2012 Jan 5.

PMID:
22223464
[PubMed - indexed for MEDLINE]
Free PMC Article
13.

Mutant huntingtin, abnormal mitochondrial dynamics, defective axonal transport of mitochondria, and selective synaptic degeneration in Huntington's disease.

Reddy PH, Shirendeb UP.

Biochim Biophys Acta. 2012 Feb;1822(2):101-10. doi: 10.1016/j.bbadis.2011.10.016. Epub 2011 Nov 4. Review.

PMID:
22080977
[PubMed - indexed for MEDLINE]
Free PMC Article
14.

Huntington's Disease and Striatal Signaling.

Roze E, Cahill E, Martin E, Bonnet C, Vanhoutte P, Betuing S, Caboche J.

Front Neuroanat. 2011 Aug 23;5:55. doi: 10.3389/fnana.2011.00055. eCollection 2011.

PMID:
22007160
[PubMed]
Free PMC Article
15.
16.

Pathological accumulation of atrophin-1 in dentatorubralpallidoluysian atrophy.

Suzuki Y, Yazawa I.

Int J Clin Exp Pathol. 2011 Apr;4(4):378-84. Epub 2011 Apr 25. Review.

PMID:
21577324
[PubMed - indexed for MEDLINE]
Free PMC Article
17.

Phosphodiesterase 7 inhibition preserves dopaminergic neurons in cellular and rodent models of Parkinson disease.

Morales-Garcia JA, Redondo M, Alonso-Gil S, Gil C, Perez C, Martinez A, Santos A, Perez-Castillo A.

PLoS One. 2011 Feb 24;6(2):e17240. doi: 10.1371/journal.pone.0017240.

PMID:
21390306
[PubMed - indexed for MEDLINE]
Free PMC Article
18.

Does Huntingtin play a role in selective macroautophagy?

Steffan JS.

Cell Cycle. 2010 Sep 1;9(17):3401-13. doi: 10.4161/cc.9.17.12671.

PMID:
20703094
[PubMed - indexed for MEDLINE]
Free PMC Article
19.

The interrelationship between mitochondrial dysfunction and transcriptional dysregulation in Huntington disease.

Jin YN, Johnson GV.

J Bioenerg Biomembr. 2010 Jun;42(3):199-205. doi: 10.1007/s10863-010-9286-7. Review.

PMID:
20556492
[PubMed - indexed for MEDLINE]
Free PMC Article
20.

Valosin-containing protein (VCP) in novel feedback machinery between abnormal protein accumulation and transcriptional suppression.

Koike M, Fukushi J, Ichinohe Y, Higashimae N, Fujishiro M, Sasaki C, Yamaguchi M, Uchihara T, Yagishita S, Ohizumi H, Hori S, Kakizuka A.

J Biol Chem. 2010 Jul 9;285(28):21736-49. doi: 10.1074/jbc.M109.099283. Epub 2010 Apr 21.

PMID:
20410307
[PubMed - indexed for MEDLINE]
Free PMC Article

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