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Results: 1 to 20 of 133

1.

A microRNA network regulates expression and biosynthesis of wild-type and DeltaF508 mutant cystic fibrosis transmembrane conductance regulator.

Ramachandran S, Karp PH, Jiang P, Ostedgaard LS, Walz AE, Fisher JT, Keshavjee S, Lennox KA, Jacobi AM, Rose SD, Behlke MA, Welsh MJ, Xing Y, McCray PB Jr.

Proc Natl Acad Sci U S A. 2012 Aug 14;109(33):13362-7. doi: 10.1073/pnas.1210906109. Epub 2012 Aug 1.

PMID:
22853952
[PubMed - indexed for MEDLINE]
Free PMC Article
2.

Regulation of cystic fibrosis transmembrane conductance regulator by microRNA-145, -223, and -494 is altered in ΔF508 cystic fibrosis airway epithelium.

Oglesby IK, Chotirmall SH, McElvaney NG, Greene CM.

J Immunol. 2013 Apr 1;190(7):3354-62. doi: 10.4049/jimmunol.1202960. Epub 2013 Feb 22.

PMID:
23436935
[PubMed - indexed for MEDLINE]
Free Article
3.

A domain mimic increases DeltaF508 CFTR trafficking and restores cAMP-stimulated anion secretion in cystic fibrosis epithelia.

Clarke LL, Gawenis LR, Hwang TC, Walker NM, Gruis DB, Price EM.

Am J Physiol Cell Physiol. 2004 Jul;287(1):C192-9. Epub 2004 Mar 17.

PMID:
15028554
[PubMed - indexed for MEDLINE]
Free Article
4.

Post-transcriptional regulation of cystic fibrosis transmembrane conductance regulator expression and function by microRNAs.

Ramachandran S, Karp PH, Osterhaus SR, Jiang P, Wohlford-Lenane C, Lennox KA, Jacobi AM, Praekh K, Rose SD, Behlke MA, Xing Y, Welsh MJ, McCray PB Jr.

Am J Respir Cell Mol Biol. 2013 Oct;49(4):544-51. doi: 10.1165/rcmb.2012-0430OC.

PMID:
23646886
[PubMed - indexed for MEDLINE]
5.

Comparative processing and function of human and ferret cystic fibrosis transmembrane conductance regulator.

Fisher JT, Liu X, Yan Z, Luo M, Zhang Y, Zhou W, Lee BJ, Song Y, Guo C, Wang Y, Lukacs GL, Engelhardt JF.

J Biol Chem. 2012 Jun 22;287(26):21673-85. doi: 10.1074/jbc.M111.336537. Epub 2012 May 8.

PMID:
22570484
[PubMed - indexed for MEDLINE]
Free PMC Article
6.

Cellular differentiation regulates expression of Cl- transport and cystic fibrosis transmembrane conductance regulator mRNA in human intestinal cells.

Montrose-Rafizadeh C, Guggino WB, Montrose MH.

J Biol Chem. 1991 Mar 5;266(7):4495-9.

PMID:
1705554
[PubMed - indexed for MEDLINE]
Free Article
7.

MiR-101 and miR-144 regulate the expression of the CFTR chloride channel in the lung.

Hassan F, Nuovo GJ, Crawford M, Boyaka PN, Kirkby S, Nana-Sinkam SP, Cormet-Boyaka E.

PLoS One. 2012;7(11):e50837. doi: 10.1371/journal.pone.0050837. Epub 2012 Nov 30.

PMID:
23226399
[PubMed - indexed for MEDLINE]
Free PMC Article
8.

Characterization of wild-type and deltaF508 cystic fibrosis transmembrane regulator in human respiratory epithelia.

Kreda SM, Mall M, Mengos A, Rochelle L, Yankaskas J, Riordan JR, Boucher RC.

Mol Biol Cell. 2005 May;16(5):2154-67. Epub 2005 Feb 16.

PMID:
15716351
[PubMed - indexed for MEDLINE]
Free PMC Article
9.

MicroRNA regulation of expression of the cystic fibrosis transmembrane conductance regulator gene.

Gillen AE, Gosalia N, Leir SH, Harris A.

Biochem J. 2011 Aug 15;438(1):25-32. doi: 10.1042/BJ20110672.

PMID:
21689072
[PubMed - indexed for MEDLINE]
Free Article
10.

Na+/H+ exchanger regulatory factor isoform 1 overexpression modulates cystic fibrosis transmembrane conductance regulator (CFTR) expression and activity in human airway 16HBE14o- cells and rescues DeltaF508 CFTR functional expression in cystic fibrosis cells.

Guerra L, Fanelli T, Favia M, Riccardi SM, Busco G, Cardone RA, Carrabino S, Weinman EJ, Reshkin SJ, Conese M, Casavola V.

J Biol Chem. 2005 Dec 9;280(49):40925-33. Epub 2005 Oct 3.

PMID:
16203733
[PubMed - indexed for MEDLINE]
Free Article
11.

Endogenous surface expression of ΔF508-CFTR mediates cAMP-stimulated Cl(-) current in CFTR(ΔF508/ΔF508) pig thyroid epithelial cells.

Li Y, Ganta S, Fong P.

Exp Physiol. 2012 Jan;97(1):115-24. doi: 10.1113/expphysiol.2011.060756. Epub 2011 Sep 23.

PMID:
21948195
[PubMed - indexed for MEDLINE]
Free PMC Article
12.

SERCA pump inhibitors do not correct biosynthetic arrest of deltaF508 CFTR in cystic fibrosis.

Grubb BR, Gabriel SE, Mengos A, Gentzsch M, Randell SH, Van Heeckeren AM, Knowles MR, Drumm ML, Riordan JR, Boucher RC.

Am J Respir Cell Mol Biol. 2006 Mar;34(3):355-63. Epub 2005 Nov 11.

PMID:
16284361
[PubMed - indexed for MEDLINE]
Free PMC Article
13.

Low temperature and chemical rescue affect molecular proximity of DeltaF508-cystic fibrosis transmembrane conductance regulator (CFTR) and epithelial sodium channel (ENaC).

Qadri YJ, Cormet-Boyaka E, Rooj AK, Lee W, Parpura V, Fuller CM, Berdiev BK.

J Biol Chem. 2012 May 11;287(20):16781-90. doi: 10.1074/jbc.M111.332031. Epub 2012 Mar 22.

PMID:
22442149
[PubMed - indexed for MEDLINE]
Free PMC Article
14.

Human heat shock protein 105/110 kDa (Hsp105/110) regulates biogenesis and quality control of misfolded cystic fibrosis transmembrane conductance regulator at multiple levels.

Saxena A, Banasavadi-Siddegowda YK, Fan Y, Bhattacharya S, Roy G, Giovannucci DR, Frizzell RA, Wang X.

J Biol Chem. 2012 Jun 1;287(23):19158-70. doi: 10.1074/jbc.M111.297580. Epub 2012 Apr 13.

PMID:
22505710
[PubMed - indexed for MEDLINE]
Free PMC Article
15.

Functional cystic fibrosis transmembrane conductance regulator tagged with an epitope of the vesicular stomatis virus glycoprotein can be addressed to the apical domain of polarized cells.

Costa de Beauregard MA, Edelman A, Chesnoy-Marchais D, Tondelier D, Lapillonne A, El Marjou F, Robine S, Louvard D.

Eur J Cell Biol. 2000 Nov;79(11):795-802.

PMID:
11139142
[PubMed - indexed for MEDLINE]
16.

Vector-specific complementation profiles of two independent primary defects in cystic fibrosis airways.

Zhang Y, Jiang Q, Dudus L, Yankaskas JR, Engelhardt JF.

Hum Gene Ther. 1998 Mar 20;9(5):635-48.

PMID:
9551612
[PubMed - indexed for MEDLINE]
17.
18.

Rescue of DeltaF508-CFTR (cystic fibrosis transmembrane conductance regulator) by curcumin: involvement of the keratin 18 network.

Lipecka J, Norez C, Bensalem N, Baudouin-Legros M, Planelles G, Becq F, Edelman A, Davezac N.

J Pharmacol Exp Ther. 2006 May;317(2):500-5. Epub 2006 Jan 19.

PMID:
16424149
[PubMed - indexed for MEDLINE]
Free Article
19.

Chaperone displacement from mutant cystic fibrosis transmembrane conductance regulator restores its function in human airway epithelia.

Sun F, Mi Z, Condliffe SB, Bertrand CA, Gong X, Lu X, Zhang R, Latoche JD, Pilewski JM, Robbins PD, Frizzell RA.

FASEB J. 2008 Sep;22(9):3255-63. doi: 10.1096/fj.07-105338. Epub 2008 Jun 12.

PMID:
18556464
[PubMed - indexed for MEDLINE]
Free PMC Article
20.

Human cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.

Itani OA, Chen JH, Karp PH, Ernst S, Keshavjee S, Parekh K, Klesney-Tait J, Zabner J, Welsh MJ.

Proc Natl Acad Sci U S A. 2011 Jun 21;108(25):10260-5. doi: 10.1073/pnas.1106695108. Epub 2011 Jun 6.

PMID:
21646513
[PubMed - indexed for MEDLINE]
Free PMC Article

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