Items per page
Sort by

Send to:

Choose Destination

Results: 1 to 20 of 104

Similar articles for PubMed (Select 22262851)


Substrate specificity of the two mitochondrial ornithine carriers can be swapped by single mutation in substrate binding site.

Monné M, Miniero DV, Daddabbo L, Robinson AJ, Kunji ER, Palmieri F.

J Biol Chem. 2012 Mar 9;287(11):7925-34. doi: 10.1074/jbc.M111.324855. Epub 2012 Jan 19.


Mitochondrial transporters for ornithine and related amino acids: a review.

Monné M, Miniero DV, Daddabbo L, Palmieri L, Porcelli V, Palmieri F.

Amino Acids. 2015 May 23. [Epub ahead of print]


Conformational dynamics in substrate-binding domains influences transport in the ABC importer GlnPQ.

Gouridis G, Schuurman-Wolters GK, Ploetz E, Husada F, Vietrov R, de Boer M, Cordes T, Poolman B.

Nat Struct Mol Biol. 2015 Jan;22(1):57-64. doi: 10.1038/nsmb.2929. Epub 2014 Dec 8.


A novel mutation in the SLC25A15 gene in a Turkish patient with HHH syndrome: functional analysis of the mutant protein.

Ersoy Tunalı N, Marobbio CM, Tiryakioğlu NO, Punzi G, Saygılı SK, Onal H, Palmieri F.

Mol Genet Metab. 2014 May;112(1):25-9. doi: 10.1016/j.ymgme.2014.03.002. Epub 2014 Mar 20.


The human gene SLC25A29, of solute carrier family 25, encodes a mitochondrial transporter of basic amino acids.

Porcelli V, Fiermonte G, Longo A, Palmieri F.

J Biol Chem. 2014 May 9;289(19):13374-84. doi: 10.1074/jbc.M114.547448. Epub 2014 Mar 20.


A L-lysine transporter of high stereoselectivity of the amino acid-polyamine-organocation (APC) superfamily: production, functional characterization, and structure modeling.

Kaur J, Olkhova E, Malviya VN, Grell E, Michel H.

J Biol Chem. 2014 Jan 17;289(3):1377-87. doi: 10.1074/jbc.M113.510743. Epub 2013 Nov 20.


Conformational changes of the bacterial type I ATP-binding cassette importer HisQMP2 at distinct steps of the catalytic cycle.

Heuveling J, Frochaux V, Ziomkowska J, Wawrzinek R, Wessig P, Herrmann A, Schneider E.

Biochim Biophys Acta. 2014 Jan;1838(1 Pt B):106-16. doi: 10.1016/j.bbamem.2013.08.024. Epub 2013 Sep 7.


Mitochondrial glutamate carriers from Drosophila melanogaster: biochemical, evolutionary and modeling studies.

Lunetti P, Cappello AR, Marsano RM, Pierri CL, Carrisi C, Martello E, Caggese C, Dolce V, Capobianco L.

Biochim Biophys Acta. 2013 Oct;1827(10):1245-55. doi: 10.1016/j.bbabio.2013.07.002. Epub 2013 Jul 11.


Single-nucleotide evolution quantifies the importance of each site along the structure of mitochondrial carriers.

Pierri CL, Palmieri F, De Grassi A.

Cell Mol Life Sci. 2014 Jan;71(2):349-64. doi: 10.1007/s00018-013-1389-y. Epub 2013 Jun 26.


Missense mutations linked to friedreich ataxia have different but synergistic effects on mitochondrial frataxin isoforms.

Li H, Gakh O, Smith DY 4th, Ranatunga WK, Isaya G.

J Biol Chem. 2013 Feb 8;288(6):4116-27. doi: 10.1074/jbc.M112.435263. Epub 2012 Dec 26.


Hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome in adulthood: a rare recognizable condition.

Filosto M, Alberici A, Tessa A, Padovani A, Santorelli FM.

Neurol Sci. 2013 Sep;34(9):1699-701. doi: 10.1007/s10072-012-1266-8. Epub 2012 Dec 18. No abstract available.


The substrate specificity of mitochondrial carriers: mutagenesis revisited.

Monné M, Palmieri F, Kunji ER.

Mol Membr Biol. 2013 Mar;30(2):149-59. doi: 10.3109/09687688.2012.737936. Epub 2012 Nov 5.


The mitochondrial oxoglutarate carrier: from identification to mechanism.

Monné M, Miniero DV, Iacobazzi V, Bisaccia F, Fiermonte G.

J Bioenerg Biomembr. 2013 Feb;45(1-2):1-13. doi: 10.1007/s10863-012-9475-7. Review. Erratum in: J Bioenerg Biomembr. 2013 Feb;45(1-2):175. Iacobazzi, Vito [added].


A chimera carrying the functional domain of the orphan protein SLC7A14 in the backbone of SLC7A2 mediates trans-stimulated arginine transport.

Jaenecke I, Boissel JP, Lemke M, Rupp J, Gasnier B, Closs EI.

J Biol Chem. 2012 Aug 31;287(36):30853-60. doi: 10.1074/jbc.M112.350322. Epub 2012 Jul 11.


Insights into the mutation-induced HHH syndrome from modeling human mitochondrial ornithine transporter-1.

Wang JF, Chou KC.

PLoS One. 2012;7(1):e31048. doi: 10.1371/journal.pone.0031048. Epub 2012 Jan 26.


Structural and biochemical analyses reveal how ornithine acetyl transferase binds acidic and basic amino acid substrates.

Iqbal A, Clifton IJ, Chowdhury R, Ivison D, Domene C, Schofield CJ.

Org Biomol Chem. 2011 Sep 21;9(18):6219-25. doi: 10.1039/c1ob05554b. Epub 2011 Jul 28.


Effects of heavy metal cations on the mitochondrial ornithine/citrulline transporter reconstituted in liposomes.

Tonazzi A, Indiveri C.

Biometals. 2011 Dec;24(6):1205-15. doi: 10.1007/s10534-011-9479-5. Epub 2011 Jul 17.


Tetrahydrofolate recognition by the mitochondrial folate transporter.

Lawrence SA, Hackett JC, Moran RG.

J Biol Chem. 2011 Sep 9;286(36):31480-9. doi: 10.1074/jbc.M111.272187. Epub 2011 Jul 15.


Molecular basis for defect in Alix-binding by alternatively spliced isoform of ALG-2 (ALG-2DeltaGF122) and structural roles of F122 in target recognition.

Inuzuka T, Suzuki H, Kawasaki M, Shibata H, Wakatsuki S, Maki M.

BMC Struct Biol. 2010 Aug 6;10:25. doi: 10.1186/1472-6807-10-25.


Role of transmembrane domain 8 in substrate selectivity and translocation of SteT, a member of the L-amino acid transporter (LAT) family.

Bartoccioni P, Del Rio C, Ratera M, Kowalczyk L, Baldwin JM, Zorzano A, Quick M, Baldwin SA, Vázquez-Ibar JL, Palacín M.

J Biol Chem. 2010 Sep 10;285(37):28764-76. doi: 10.1074/jbc.M110.116632. Epub 2010 Jul 7.

Items per page
Sort by

Send to:

Choose Destination

Supplemental Content

Write to the Help Desk