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Results: 1 to 20 of 100

Similar articles for PubMed (Select 18611415)

1.

Early deficits in motor coordination and cognitive dysfunction in a mouse model of the neurodegenerative lysosomal storage disorder, Sandhoff disease.

Gulinello M, Chen F, Dobrenis K.

Behav Brain Res. 2008 Nov 21;193(2):315-9. doi: 10.1016/j.bbr.2008.06.016. Epub 2008 Jun 20.

2.

Influence of caloric restriction on motor behavior, longevity, and brain lipid composition in Sandhoff disease mice.

Denny CA, Kasperzyk JL, Gorham KN, Bronson RT, Seyfried TN.

J Neurosci Res. 2006 May 1;83(6):1028-38.

PMID:
16521125
3.

Delayed symptom onset and increased life expectancy in Sandhoff disease mice treated with N-butyldeoxynojirimycin.

Jeyakumar M, Butters TD, Cortina-Borja M, Hunnam V, Proia RL, Perry VH, Dwek RA, Platt FM.

Proc Natl Acad Sci U S A. 1999 May 25;96(11):6388-93.

4.

[Molecular pathogenesis and therapeutic approach of GM2 gangliosidosis].

Tsuji D.

Yakugaku Zasshi. 2013;133(2):269-74. Review. Japanese.

5.

Cognitive dysfunction precedes neuropathology and motor abnormalities in the YAC128 mouse model of Huntington's disease.

Van Raamsdonk JM, Pearson J, Slow EJ, Hossain SM, Leavitt BR, Hayden MR.

J Neurosci. 2005 Apr 20;25(16):4169-80.

6.

The trigeminal retrograde transfer pathway in the treatment of neurodegeneration.

Kyrkanides S, Yang M, Tallents RH, Miller JN, Brouxhon SM, Olschowka JA.

J Neuroimmunol. 2009 Apr 30;209(1-2):139-42. doi: 10.1016/j.jneuroim.2009.02.006. Epub 2009 Mar 10.

PMID:
19278737
7.

Impaired neural differentiation of induced pluripotent stem cells generated from a mouse model of Sandhoff disease.

Ogawa Y, Tanaka M, Tanabe M, Suzuki T, Togawa T, Fukushige T, Kanekura T, Sakuraba H, Oishi K.

PLoS One. 2013;8(1):e55856. doi: 10.1371/journal.pone.0055856. Epub 2013 Jan 31.

8.

Characterization of the mutant β-subunit of β-hexosaminidase for dimer formation responsible for the adult form of Sandhoff disease with the motor neuron disease phenotype.

Yamada K, Takado Y, Kato YS, Yamada Y, Ishiguro H, Wakamatsu N.

J Biochem. 2013 Jan;153(1):111-9. doi: 10.1093/jb/mvs131. Epub 2012 Nov 5.

9.

Peripheral nervous system manifestations in a Sandhoff disease mouse model: nerve conduction, myelin structure, lipid analysis.

McNally MA, Baek RC, Avila RL, Seyfried TN, Strichartz GR, Kirschner DA.

J Negat Results Biomed. 2007 Jul 10;6:8.

10.

Progressive impairment in olfactory working memory in a mouse model of Mild Cognitive Impairment.

Young JW, Sharkey J, Finlayson K.

Neurobiol Aging. 2009 Sep;30(9):1430-43. doi: 10.1016/j.neurobiolaging.2007.11.018. Epub 2008 Feb 1.

PMID:
18242780
11.

Motor, emotional and cognitive deficits in adult BACHD mice: a model for Huntington's disease.

Abada YS, Schreiber R, Ellenbroek B.

Behav Brain Res. 2013 Feb 1;238:243-51. doi: 10.1016/j.bbr.2012.10.039. Epub 2012 Oct 30.

PMID:
23123142
12.

Progression of multiple behavioral deficits with various ages of onset in a murine model of Hurler syndrome.

Pan D, Sciascia A 2nd, Vorhees CV, Williams MT.

Brain Res. 2008 Jan 10;1188:241-53. Epub 2007 Oct 23.

13.

Assessment of motor function, sensory motor gating and recognition memory in a novel BACHD transgenic rat model for huntington disease.

Abada YS, Nguyen HP, Schreiber R, Ellenbroek B.

PLoS One. 2013 Jul 11;8(7):e68584. doi: 10.1371/journal.pone.0068584. Print 2013.

14.

Plasmid-based gene transfer ameliorates visceral storage in a mouse model of Sandhoff disease.

Yamaguchi A, Katsuyama K, Suzuki K, Kosaka K, Aoki I, Yamanaka S.

J Mol Med (Berl). 2003 Mar;81(3):185-93. Epub 2003 Feb 12.

PMID:
12682727
15.

Complexin 1 knockout mice exhibit marked deficits in social behaviours but appear to be cognitively normal.

Drew CJ, Kyd RJ, Morton AJ.

Hum Mol Genet. 2007 Oct 1;16(19):2288-305. Epub 2007 Jul 24.

16.

Miglustat therapy in juvenile Sandhoff disease.

Tallaksen CM, Berg JE.

J Inherit Metab Dis. 2009 Dec;32 Suppl 1:S289-93. doi: 10.1007/s10545-009-1224-7. Epub 2009 Nov 4.

PMID:
19898953
17.

New cases of adult-onset Sandhoff disease with a cerebellar or lower motor neuron phenotype.

Delnooz CC, Lefeber DJ, Langemeijer SM, Hoffjan S, Dekomien G, Zwarts MJ, Van Engelen BG, Wevers RA, Schelhaas HJ, van de Warrenburg BP.

J Neurol Neurosurg Psychiatry. 2010 Sep;81(9):968-72. doi: 10.1136/jnnp.2009.177089.

PMID:
20798201
18.

New blood cells help an overburdened brain.

Mattson MP.

Trends Neurosci. 2001 Jan;24(1):5. No abstract available.

PMID:
11163874
19.

Deletion of macrophage-inflammatory protein 1 alpha retards neurodegeneration in Sandhoff disease mice.

Wu YP, Proia RL.

Proc Natl Acad Sci U S A. 2004 Jun 1;101(22):8425-30. Epub 2004 May 20.

20.

MRS reveals additional hexose N-acetyl resonances in the brain of a mouse model for Sandhoff disease.

Lowe JP, Stuckey DJ, Awan FR, Jeyakumar M, Neville DC, Platt FM, Griffin JL, Styles P, Blamire AM, Sibson NR.

NMR Biomed. 2005 Dec;18(8):517-26.

PMID:
16206131
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