Arch Dermatol. 1977 Jul;113(7):948-51.

Follicular atrophoderma and basal cell carcinomas: the Bazex syndrome.

Abstract

Seven members of one family had rare, inherited syndrome of follicular atrophoderma, basal cell carcinomas, and localized anhidrosis. Associated findings in some subjectes were generalized hypohidrosis and "eczema" involving the face shortly after birth. This syndrome shows dominant inheritance, possible x-linked. Follicular atrophoderma is an important skin manifestation, as it has been associated in all reported cases with other systemic or cutaneous abnormalities.

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Review [Bazex-Dupré-Christol syndrome. Follicular atrophoderma, multiple basal cell carcinomas and hypotrichosis]. [Hautarzt. 1993]
Review [Bazex-Dupré-Christol syndrome. Follicular atrophoderma, multiple basal cell carcinomas and hypotrichosis].
Herges A, Stieler W, Stadler R. Hautarzt. 1993 Jun; 44(6):385-91.
The Bazex syndrome: follicular atrophoderma with multiple basal cell carcinomas, hypotrichosis and hypohidrosis. [Clin Exp Dermatol. 1981]
The Bazex syndrome: follicular atrophoderma with multiple basal cell carcinomas, hypotrichosis and hypohidrosis.
Plosila M, Kiistala R, Niemi KM. Clin Exp Dermatol. 1981 Jan; 6(1):31-41.
Review [Follicular atrophoderma, basal cell proliferation and hypotrichosis (Bazex-Dupré-Christol syndrome). A study in 2 families]. [Ann Dermatol Venereol. 1994]
Review [Follicular atrophoderma, basal cell proliferation and hypotrichosis (Bazex-Dupré-Christol syndrome). A study in 2 families].
Moreau-Cabarrot A, Bonafé JL, Hachich N, Jalby BC, Aubert G, Rolland M, Bazex J. Ann Dermatol Venereol. 1994; 121(4):297-301.
Follicular atrophoderma with multiple basal cell carcinomas (Bazex). [Br J Dermatol. 1978]
Follicular atrophoderma with multiple basal cell carcinomas (Bazex).
Gould DJ, Barker DJ. Br J Dermatol. 1978 Oct; 99(4):431-5.
Review Sporadic Bazex-Dupré-Christol-like syndrome: early onset basal cell carcinoma, hypohidrosis, hypotrichosis, and prominent milia. [Dermatol Surg. 2000]
Review Sporadic Bazex-Dupré-Christol-like syndrome: early onset basal cell carcinoma, hypohidrosis, hypotrichosis, and prominent milia.
Glaessl A, Hohenlautner U, Landthaler M, Vogt T. Dermatol Surg. 2000 Feb; 26(2):152-4.

See reviews... See all...

Cited by 2 PubMed Central articles

An unusual presentation of anetoderma: a case report. [BMC Dermatol. 2004]
An unusual presentation of anetoderma: a case report.
Aghaei S, Sodaifi M, Aslani FS, Mazharinia N. BMC Dermatol. 2004 Aug 19; 4:9. Epub 2004 Aug 19.
A Scottish family with Bazex-Dupré-Christol syndrome: follicular atrophoderma, congenital hypotrichosis, and basal cell carcinoma. [J Med Genet. 1996]
A Scottish family with Bazex-Dupré-Christol syndrome: follicular atrophoderma, congenital hypotrichosis, and basal cell carcinoma.
Kidd A, Carson L, Gregory DW, de Silva D, Holmes J, Dean JC, Haites N. J Med Genet. 1996 Jun; 33(6):493-7.

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