We present a patient who had suffered from mild hemoptysis for six years. Abnormal bronchovesicular breath sounds over the left lower lung filed were noted. The chest film also revealed infiltration over the left lower lung field. High-resolution computed tomography (HRCT), aortogram and pulmonary angiography demonstrated anomalous arterial supply to the basilar segments of the left lower lung without coexistence of pulmonary sequestration. Only total nine cases have been reported in English or Chinese literature. The improvement of diagnostic method has enabled an accurate diagnosis before operation with non-invasive examination. Also, this congenital abnormality may not be so rare if meticulously surveyed.