Arch Dermatol. 1981 May;117(5):285-9.

The keratitis, ichthyosis, and deafness (KID) syndrome.

Abstract

We describe here a patient with ichthyosis, keratitis, deafness, and recalcitrant cutaneous bacterial and fungal infections, who was previously described as having hereditary hypohidrotic ectodermal dysplasia. Similarly affected patients described in the literature have the following features in common: (1) a distinctive ichthyosis characterized by a fine dry scale, follicular hyperkeratotic spines, and a reticulated pattern of hyperkeratosis on the palms and soles; (2) a vascularizing keratitis that results in notable visual impairment; and (3) neurosensory deafness. One half of the affected patients also display frequent, severe cutaneous infections. We suggest that the name "the KID syndrome" to emphasize the characteristic features of the syndrome-keratitis, ichthyosis, and deafness.

PMID:: 7224657; [PubMed - indexed for MEDLINE]

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Review Keratitis, ichthyosis, and deafness (KID syndrome): review of the literature and proposal of a new terminology. [Pediatr Dermatol. 1996]
Review Keratitis, ichthyosis, and deafness (KID syndrome): review of the literature and proposal of a new terminology.
Caceres-Rios H, Tamayo-Sanchez L, Duran-Mckinster C, de la Luz Orozco M, Ruiz-Maldonado R. Pediatr Dermatol. 1996 Mar-Apr; 13(2):105-13.
[Patient with severe corneal disease in KID syndrome]. [Arch Soc Esp Oftalmol. 2006]
[Patient with severe corneal disease in KID syndrome].
Gómez-Faiña P, Ruiz-Viñals AT, Buil-Calvo JA, España-Albelda A, Pazos-López M, Castilla-Céspedes M. Arch Soc Esp Oftalmol. 2006 Apr; 81(4):225-7.
Review Keratitis, ichthyosis, and deafness (KID) syndrome in half sibs. [Pediatr Dermatol. 1998]
Review Keratitis, ichthyosis, and deafness (KID) syndrome in half sibs.
Koné-Paut I, Hesse S, Palix C, Rey R, Rémédiani K, Garnier JM, Berbis P. Pediatr Dermatol. 1998 May-Jun; 15(3):219-21.
KID syndrome associated with features of ichthyosis hystrix. [Pediatr Dermatol. 2000]
KID syndrome associated with features of ichthyosis hystrix.
Nousari HC, Kimyai-Asadi A, Pinto JL. Pediatr Dermatol. 2000 Mar-Apr; 17(2):115-7.
Keratitis, ichthyosis, deafness (KID) syndrome--the first report from India. [Clin Exp Dermatol. 1993]
Keratitis, ichthyosis, deafness (KID) syndrome--the first report from India.
Kanwar AJ, Ghosh S, Handa S, Thami GP, Kaur S. Clin Exp Dermatol. 1993 Jul; 18(4):386-8.

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