The liver in lipid storage disease: biochemical basis of pathogenesis and clinical features

Prog Liver Dis. 1982:7:331-46.
No abstract available

Publication types

  • Review

MeSH terms

  • Fabry Disease / pathology
  • Gangliosidoses / pathology
  • Gaucher Disease / pathology
  • Humans
  • Leukodystrophy, Globoid Cell / pathology
  • Leukodystrophy, Metachromatic / pathology
  • Lipid Metabolism, Inborn Errors / metabolism
  • Lipid Metabolism, Inborn Errors / pathology*
  • Lipidoses / pathology
  • Liver / pathology*
  • Niemann-Pick Diseases / pathology
  • Sandhoff Disease / pathology
  • Tay-Sachs Disease / pathology
  • alpha-L-Fucosidase / metabolism

Substances

  • alpha-L-Fucosidase