Abstract
Camurati-Engelmann disease is a rare generalized progressive bone affection which causes combined hearing loss, facial palsy and vestibular dysfunction. Differential diagnosis against bone affections is possible because of typical x-ray findings, pseudo mixed hearing loss, myopathy and growth disorders.
Publication types
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Case Reports
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English Abstract
MeSH terms
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Adult
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Audiometry, Pure-Tone
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Audiometry, Speech
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Bone Conduction
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Bone Diseases, Developmental / diagnosis*
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Camurati-Engelmann Syndrome / diagnosis*
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Evoked Potentials, Auditory
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Facial Paralysis / diagnosis*
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Female
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Hearing Loss / diagnosis*
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Hearing Loss, Conductive / diagnosis*
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Hearing Loss, Sensorineural / diagnosis*
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Humans
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Meniere Disease / diagnosis