[Neuro-otologic early symptoms of Camurati-Engelmann disease]

Laryngol Rhinol Otol (Stuttg). 1983 Oct;62(10):463-7.
[Article in German]

Abstract

Camurati-Engelmann disease is a rare generalized progressive bone affection which causes combined hearing loss, facial palsy and vestibular dysfunction. Differential diagnosis against bone affections is possible because of typical x-ray findings, pseudo mixed hearing loss, myopathy and growth disorders.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Audiometry, Pure-Tone
  • Audiometry, Speech
  • Bone Conduction
  • Bone Diseases, Developmental / diagnosis*
  • Camurati-Engelmann Syndrome / diagnosis*
  • Evoked Potentials, Auditory
  • Facial Paralysis / diagnosis*
  • Female
  • Hearing Loss / diagnosis*
  • Hearing Loss, Conductive / diagnosis*
  • Hearing Loss, Sensorineural / diagnosis*
  • Humans
  • Meniere Disease / diagnosis