Studies on human erythrocyte nucleotide metabolism. II. Nonspherocytic hemolytic anemia, high red cell ATP, and ribosephosphate pyrophosphokinase (RPK, E.C.2.7.6.1) deficiency

Blood. 1972 May;39(5):674-84.
No abstract available

MeSH terms

  • Adenosine Diphosphate / blood
  • Adenosine Monophosphate / blood
  • Adenosine Triphosphate / blood
  • Adult
  • Anemia, Hemolytic, Congenital Nonspherocytic / blood*
  • Black People
  • Blood Protein Electrophoresis
  • Erythrocyte Aging
  • Erythrocytes / enzymology
  • Erythrocytes / metabolism*
  • Female
  • Fetal Hemoglobin / analysis
  • Glutathione / blood
  • Glycolysis
  • Hemoglobins / analysis
  • Hemolysis
  • Humans
  • Lactates / biosynthesis
  • Metabolism, Inborn Errors*
  • Nucleotides / metabolism*
  • Phosphotransferases / blood*
  • Pyruvates / biosynthesis
  • Reticulocytes

Substances

  • Hemoglobins
  • Lactates
  • Nucleotides
  • Pyruvates
  • Adenosine Monophosphate
  • Adenosine Diphosphate
  • Adenosine Triphosphate
  • Fetal Hemoglobin
  • Phosphotransferases
  • Glutathione