Ann Otol Rhinol Laryngol. 1985 Sep-Oct;94(5 Pt 1):458-61.

Airway obstruction and sleep apnea in Hurler and Hunter syndromes.

Abstract

The Hurler and Hunter syndromes are two forms of mucopolysaccharidosis. Although the diseases are rare, those afflicted commonly require otolaryngologic consultation. Upper airway obstruction is often severe, progressive, and not infrequently the suspected cause of death in these patients. Four patients with these problems are presented. In all of the children, obstructive sleep apnea was a major management problem. This and other upper airway difficulties are detailed with clinical and pathological correlates.

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Airway obstruction and sleep apnea in Hurler and Hunter syndromes.

Abstract

Publication Types, MeSH Terms

Publication Types

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LinkOut - more resources

Medical

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Cited by 1 PubMed Central article

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