Beta-Catenin Causes Adrenal Hyperplasia by Blocking Zonal Transdifferentiation

Cell Rep. 2020 Apr 21;31(3):107524. doi: 10.1016/j.celrep.2020.107524.

Abstract

Activating mutations in the canonical Wnt/β-catenin pathway are key drivers of hyperplasia, the gateway for tumor development. In a wide range of tissues, this occurs primarily through enhanced effects on cellular proliferation. Whether additional mechanisms contribute to β-catenin-driven hyperplasia remains unknown. The adrenal cortex is an ideal system in which to explore this question, as it undergoes hyperplasia following somatic β-catenin gain-of-function (βcat-GOF) mutations. Targeting βcat-GOF to zona Glomerulosa (zG) cells leads to a progressive hyperplastic expansion in the absence of increased proliferation. Instead, we find that hyperplasia results from a functional block in the ability of zG cells to transdifferentiate into zona Fasciculata (zF) cells. Mechanistically, zG cells demonstrate an upregulation of Pde2a, an inhibitor of zF-specific cAMP/PKA signaling. Hyperplasia is further exacerbated by trophic factor stimulation leading to organomegaly. Together, these data indicate that β-catenin drives adrenal hyperplasia through both proliferation-dependent and -independent mechanisms.

Keywords: Wnt signaling; adrenal cortex; beta-catenin; cell transdifferentiation; hyperplasia.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Adrenal Hyperplasia, Congenital / genetics
  • Adrenal Hyperplasia, Congenital / metabolism*
  • Adrenal Hyperplasia, Congenital / pathology*
  • Animals
  • Cell Transdifferentiation / physiology
  • Female
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • beta Catenin / genetics
  • beta Catenin / metabolism*

Substances

  • CTNNB1 protein, mouse
  • beta Catenin