Currarino syndrome presenting as a cerebrospinal fluid leak from the dermal sinus tract: case report

J Neurosurg Pediatr. 2020 Mar 6:1-5. doi: 10.3171/2020.1.PEDS19692. Online ahead of print.

Abstract

Currarino syndrome is an autosomal dominant condition with variable expressivity and penetrance that is associated with several classic features: sacral dysgenesis, presacral mass, and/or anorectal anomalies. The authors present a unique case in which the patient's initial presentation was a CSF leak from a sinus tract. The sinus tract was identified and disconnected from the thecal sac, obliterating the anterior sacral meningocele. This case represents a unique scenario in which Currarino syndrome manifested as a CSF leak from a dermal sinus tract.

Keywords: Currarino syndrome; cerebrospinal fluid leak; dermal sinus tract; spine.

Publication types

  • Case Reports