Rare case of atypical Dejerine syndrome in a child

J Clin Imaging Sci. 2020 Jan 31:10:2. doi: 10.25259/JCIS_172_2019. eCollection 2020.

Abstract

Medial medullary syndrome (aka Dejerine syndrome) is a rare condition that develops following infarction of the medial medulla and is classically defined by the presence of Dejerine's triad of contralateral weakness in upper and lower extremities, contralateral hemisensory loss of vibration and proprioception, and ipsilateral tongue weakness. It is typically caused by occlusion of the vertebral artery or one of its branches. We report the case of a 6-year-old girl who suffered a medial medullary infarction, and she was diagnosed with atypical Dejerine syndrome. Medial medullary infarct leading to atypical Dejerine syndrome has not been reported in this young of a patient in the literature to date.

Keywords: Dejerine syndrome; Medial medullary infarction; Pediatric stroke.

Publication types

  • Case Reports