A combination of double outlet right ventricle(DORV) with Ebstein's anomaly and aortic coarctation (CoA) is vary rare. We report a successful staged surgical repair for DORV with Ebstein's anomaly associated with CoA. The patient had subaortic perimembronous ventricular septal defect (10×7.5 mm) and small atrial septal defect( 3 mm). Two great arteries were side by side position. The posterior leaflet of the tricuspid valve was 10 mm displaced to the right ventricle and tricuspid valve regurgitation was severe. The patients was unsuitable for primary biventricular repair because the size of the mitral valve was considered to be small. First, bilateral pulmonary artery banding was performed after balloon atrio-septostomy in the neonatal period. Three months after the 1st operation, cardiac catheteraization revealed that the left and right heart structure was suitable for biventricular repair. At 4-month-old-age, aortic arch reconstruction, intra-cardiac rerouting and tricuspid valve repair were performed. Post operative tricuspid valve regurgitation was mild. The patient was discharged on the 12th postoperative day with good hemodynamic condition.