Adult-type ALCAPA syndrome: A rare coronary artery anomaly

Echocardiography. 2018 Jul;35(7):1056-1059. doi: 10.1111/echo.14013. Epub 2018 May 11.

Abstract

Anomalous origin of the left coronary artery arising from the pulmonary artery (ALCAPA or Bland-White-Garland syndrome) is a rare but serious congenital coronary artery anomaly, with a poor prognosis without surgical repair. There are two types of ALCAPA syndrome: infant type and adult type. We present a rare case of a 63-year-old female patient, with isolated left anterior descending artery origin from the pulmonary artery. Coronary computed tomography angiography revealed giant and tortuous coronary arteries with many collaterals between the left and right coronary system. The patient refused any surgical treatment.

Keywords: 2D Echocardiography; anomalous coronary arteries; cardiac imaging; computed tomography; coronary circulation.

Publication types

  • Case Reports
  • Video-Audio Media

MeSH terms

  • Bland White Garland Syndrome / diagnosis*
  • Computed Tomography Angiography / methods*
  • Coronary Angiography / methods*
  • Coronary Vessel Anomalies / diagnosis
  • Coronary Vessels / diagnostic imaging*
  • Echocardiography, Doppler, Color / methods*
  • Female
  • Humans
  • Imaging, Three-Dimensional*
  • Middle Aged
  • Pulmonary Artery / abnormalities
  • Pulmonary Artery / diagnostic imaging*
  • Rare Diseases