Follicular dendritic cell sarcoma of the porta hepatis

BMJ Case Rep. 2018 Feb 8:2018:bcr2017223232. doi: 10.1136/bcr-2017-223232.

Abstract

Follicular dendritic cell (FDC) sarcoma is a very rare neoplasm which commonly involves the lymph nodes and less commonly involves extranodal organs such as the liver. Most cases of FDC sarcoma are idiopathic, however some cases are associated with other disease states. Management of FDC sarcoma is primarily focused on surgical resection of the mass, and secondarily focused on radiotherapy, chemotherapy and/or biologic pharmacotherapy. We report the case of a patient who was found to have FDC sarcoma presenting as an obstructing mass of the porta hepatis, a manifestation which does not appear to be reported in the literature.

Keywords: general surgery; hepatic cancer; surgical oncology.

Publication types

  • Case Reports

MeSH terms

  • Abdominal Pain / etiology
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Bilirubin / blood
  • Biomarkers, Tumor
  • Cholangiopancreatography, Endoscopic Retrograde
  • Dendritic Cell Sarcoma, Follicular / diagnosis*
  • Dendritic Cell Sarcoma, Follicular / therapy
  • Deoxycytidine / analogs & derivatives
  • Deoxycytidine / therapeutic use
  • Docetaxel
  • Gemcitabine
  • Humans
  • Liver Neoplasms / diagnosis*
  • Liver Neoplasms / therapy
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Neoplasm Recurrence, Local / diagnostic imaging
  • Taxoids / therapeutic use

Substances

  • Biomarkers, Tumor
  • Taxoids
  • Deoxycytidine
  • Docetaxel
  • Bilirubin
  • Gemcitabine