Catheter-Based Palliation in an Infant With Obstructed Cor Triatriatum

Can J Cardiol. 2016 Dec;32(12):1575.e13-1575.e15. doi: 10.1016/j.cjca.2016.07.003. Epub 2016 Jul 15.

Abstract

A 33-day-old infant with obstructed cor triatriatum sinister and partial anomalous pulmonary venous drainage presented with respiratory distress and fever. Her suprasystemic pulmonary hypertension was relieved by opening the connection to the right atrium using balloon atrial septoplasty and septostomy, and to the inferior chamber using balloon dilation of a fenestration in the dividing membrane. This enabled extubation and discharge, with elective surgical repair at 2 months. To our knowledge, this is the youngest patient to receive a catheter intervention for obstructed cor triatriatum sinister, providing relief of pulmonary hypertension and postponement of surgical repair.

Publication types

  • Case Reports

MeSH terms

  • Atrial Septum* / pathology
  • Atrial Septum* / physiopathology
  • Atrial Septum* / surgery
  • Cardiac Catheterization / methods*
  • Cardiac Surgical Procedures / methods*
  • Cor Triatriatum* / complications
  • Cor Triatriatum* / diagnosis
  • Cor Triatriatum* / physiopathology
  • Cor Triatriatum* / surgery
  • Female
  • Humans
  • Hypertension, Pulmonary* / etiology
  • Hypertension, Pulmonary* / surgery
  • Infant
  • Palliative Care / methods*
  • Reoperation / methods
  • Respiratory Insufficiency / etiology
  • Respiratory Insufficiency / therapy
  • Treatment Outcome