Stiff Person Syndrome

J Assoc Physicians India. 2015 Aug;63(8):81-2.

Abstract

Stiff-person syndrome or Moersch-Woltmann is a very rare and disabling neurologic disorder characterized by muscle rigidity and episodic spasms involving axial and limb musculature. It is an autoimmune disorder resulting in a malfunction of aminobutyric acid mediated inhibitory networks in the central nervous system. We describe a patient of stiff person syndrome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Antibodies* / blood
  • Antibodies* / cerebrospinal fluid
  • Anticonvulsants / administration & dosage
  • Autoimmunity
  • Baclofen / administration & dosage*
  • Clonazepam / administration & dosage*
  • Electromyography / methods
  • Glutamate Decarboxylase / immunology*
  • Humans
  • Lordosis / diagnosis
  • Lordosis / etiology
  • Lumbosacral Region / diagnostic imaging
  • Magnetic Resonance Imaging / methods
  • Male
  • Muscle Relaxants, Central / administration & dosage
  • Muscle Rigidity / diagnosis
  • Muscle Rigidity / etiology
  • Muscle Spasticity / diagnosis
  • Muscle Spasticity / etiology
  • Muscle, Skeletal* / diagnostic imaging
  • Muscle, Skeletal* / physiopathology
  • Stiff-Person Syndrome* / diagnosis
  • Stiff-Person Syndrome* / immunology
  • Stiff-Person Syndrome* / physiopathology
  • Treatment Outcome

Substances

  • Antibodies
  • Anticonvulsants
  • Muscle Relaxants, Central
  • Clonazepam
  • Glutamate Decarboxylase
  • Baclofen