Abstract
Stiff-person syndrome or Moersch-Woltmann is a very rare and disabling neurologic disorder characterized by muscle rigidity and episodic spasms involving axial and limb musculature. It is an autoimmune disorder resulting in a malfunction of aminobutyric acid mediated inhibitory networks in the central nervous system. We describe a patient of stiff person syndrome.
© Journal of the Association of Physicians of India 2011.
MeSH terms
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Adult
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Antibodies* / blood
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Antibodies* / cerebrospinal fluid
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Anticonvulsants / administration & dosage
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Autoimmunity
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Baclofen / administration & dosage*
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Clonazepam / administration & dosage*
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Electromyography / methods
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Glutamate Decarboxylase / immunology*
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Humans
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Lordosis / diagnosis
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Lordosis / etiology
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Lumbosacral Region / diagnostic imaging
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Magnetic Resonance Imaging / methods
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Male
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Muscle Relaxants, Central / administration & dosage
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Muscle Rigidity / diagnosis
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Muscle Rigidity / etiology
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Muscle Spasticity / diagnosis
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Muscle Spasticity / etiology
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Muscle, Skeletal* / diagnostic imaging
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Muscle, Skeletal* / physiopathology
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Stiff-Person Syndrome* / diagnosis
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Stiff-Person Syndrome* / immunology
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Stiff-Person Syndrome* / physiopathology
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Treatment Outcome
Substances
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Antibodies
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Anticonvulsants
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Muscle Relaxants, Central
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Clonazepam
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Glutamate Decarboxylase
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Baclofen