A case of DIPNECH presenting as usual interstitial pneumonia

Pneumonol Alergol Pol. 2016;84(3):174-7. doi: 10.5603/PiAP.2016.0020.

Abstract

Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) is a rare disease that is classically described as presenting with cough, dyspnea, and wheezing in non-smoker middle aged females. Pulmonary function tests commonly demonstrate an obstructive pattern and CT of chest usually reveals diffuse air trapping with mosaic pattern. We present a case of patient with DIPNECH manifesting with restrictive pattern and as usual interstitial pneumonia on imaging.

Keywords: DIPNECH; lung diseases/pathology; neuroendocrine cells/pathology.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Biopsy
  • Coronary Artery Disease / complications
  • Cough / etiology
  • Dyspnea / etiology
  • Female
  • Humans
  • Hyperplasia / diagnosis
  • Hyperplasia / diagnostic imaging
  • Hyperplasia / drug therapy
  • Idiopathic Pulmonary Fibrosis / diagnosis*
  • Idiopathic Pulmonary Fibrosis / diagnostic imaging
  • Idiopathic Pulmonary Fibrosis / drug therapy
  • Idiopathic Pulmonary Fibrosis / pathology
  • Lung / diagnostic imaging
  • Lung / pathology*
  • Lung Diseases / diagnosis*
  • Lung Diseases / diagnostic imaging
  • Lung Diseases / drug therapy
  • Lung Diseases / pathology*
  • Multiple Pulmonary Nodules / diagnostic imaging
  • Multiple Pulmonary Nodules / drug therapy
  • Multiple Pulmonary Nodules / pathology
  • Neuroendocrine Cells / pathology*
  • Respiratory Function Tests
  • Tomography, X-Ray Computed