Self-limiting recurrent bullous Henoch-Schonlein purpura with lupus anticoagulant

BMJ Case Rep. 2015 Jan 20:2015:bcr2014205436. doi: 10.1136/bcr-2014-205436.

Abstract

Henoch-Schonlein purpura (HSP) is the most common acute systemic vasculitis of childhood with an incidence of approximately 1:10,000. It commonly presents with skin, gastrointestinal tract, joints and renal system signs and symptoms. We present a case of recurrent self-limiting HSP with lupus anticoagulant presenting with haemorrhagic bullous skin lesions and scrotal swelling. The initial presentation resolved within 4 weeks but over the next 6 months, a few self-limiting but milder skin lesions occurred. Some institutions have advocated the use of steroids in these cases but our case showed that the use of steroids may not be required. This atypical presentation of HSP led to unnecessary investigations that this case report aims to prevent in the future by raising its awareness.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Humans
  • IgA Vasculitis / blood
  • IgA Vasculitis / diagnosis*
  • IgA Vasculitis / pathology*
  • Lupus Coagulation Inhibitor / blood
  • Male
  • Remission, Spontaneous
  • Scrotum / pathology*
  • Watchful Waiting

Substances

  • Lupus Coagulation Inhibitor