Purpose: To report a case of asymmetric retinopathy of prematurity associated with a peripapillary staphyloma.
Methods: Case report.
Results: A 1,545-g male infant was born at 34 weeks' gestation. He was noted on initial examination to have a peripapillary staphyloma in the left eye and immature retinal vasculature in zone 2 of both eyes. Follow-up examination at 16 weeks of age showed a normal right eye with full vascularization and zone 2, stage 2 retinopathy of prematurity in the left eye.
Conclusion: To our knowledge, this is the first reported case of peripapillary staphyloma in which only the affected eye developed retinopathy of prematurity.