Eyelid myoclonia with absences (EMA) in two monovular twins

Clin Electroencephalogr. 1989 Jul;20(3):193-5. doi: 10.1177/155005948902000313.

Abstract

EMA (eyelid myoclonia with absences) consists of brief seizures triggered by eyelid closure and characterized by absence and palpebral myoclonia. The EEG shows brief discharges with 3 per second spike and wave complexes. The present report describes the cases of 2 monovular twins who started to have this form of epilepsy at the age of 4 1/2 years. Their seizures, after 2 years of follow-up, are greatly reduced with combined therapy of valproic acid and benzodiazepines (Clobazam).

MeSH terms

  • Child
  • Diseases in Twins*
  • Electroencephalography*
  • Epilepsies, Myoclonic / complications
  • Epilepsies, Myoclonic / physiopathology*
  • Epilepsy, Absence / complications
  • Epilepsy, Absence / physiopathology*
  • Eyelids / physiopathology*
  • Female
  • Follow-Up Studies
  • Humans
  • Twins*
  • Twins, Monozygotic*