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BMJ Case Rep. 2012 Nov 14;2012. pii: bcr2012006413. doi: 10.1136/bcr-2012-006413.

Bezafibrate to prevent relapsing pancreatitis in WAGR syndrome.

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  • 1Department of Paediatric Endocrinology, Royal Manchester Children's Hospital, Manchester, UK.

Abstract

Recurrent episodes of acute, severe pancreatitis are a feature of the rare WAGR congenital anomaly syndrome. Although pancreatitis is well recognised as a life-threatening association of WAGR syndrome, treatment to prevent pancreatitis is not recommended. We report the successful prevention of hypertriglyceridaemia-associated relapsing pancreatitis in a child with WAGR syndrome with Bezafibrate. In addition to dietary fat restriction, Bezafibrate may be a useful therapeutic adjunct in WAGR related relapsing pancreatitis.

PMID:
23152176
[PubMed - indexed for MEDLINE]
PMCID:
PMC4543478
Free PMC Article
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