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Pan Afr Med J. 2011;9:33. Epub 2011 Jul 25.

Congenital insensitivity to pain with anhydrosis: report of a family case.

Author information

  • 1Department of anesthesia and intensive care, University Hospital Hassan II, Fez, Morocco.

Abstract

Congenital Insensitivity to pain with anhydrosis (CIPA) is a rare inherited disease. It is classified as hereditary sensory and autonomic neuropathy type IV. Pain insensitivity and autonomic deficits are present, but touch and pressure sensitivity are unimpaired. Mental retardation is usually present. We report a family case of a 5 years old girl and 2 years old boy with congenital insensitivity to pain, while discussing the clinical features and the anesthetic strategy of such patients. Patients with Congenital Insensitivity to Pain with anhydrosis may undergo surgery because of susceptibility to trauma due to absence of pain. The clinical features may intrinsically possess anesthetic challenges.

KEYWORDS:

Congenital insensitivity to pain; anesthesia; family case; hereditary; neuropathy; sensory and autonomic neuropathy

PMID:
22355435
[PubMed - indexed for MEDLINE]
PMCID:
PMC3215555
Free PMC Article
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